Note: Categories for "late effects" of infectious and parasitic diseases are to be found at 137-139.
Includes: diseases generally recognized as communicable or transmissible as well as a few diseases of unknown but possibly infectious origin
Excludes: acute respiratory infections (460-466)
carrier or suspected carrier of infectious organism (V02.0-V02.9)
certain localized infections
influenza (487.0-487.8)
INTESTINAL INFECTIOUS DISEASES (001-009)
Excludes: helminthiases (120.0-129)
001.1 Due to Vibrio cholerae el tor
Typhoid (fever) (infection) [any site]
002.9 Paratyphoid fever, unspecified
Includes: infection or food poisoning by Salmonella [any serotype]
003.0 Salmonella gastroenteritis
Salmonellosis
003.2 Localized salmonella infections
003.20 Localized salmonella infection, unspecified
003.24 Salmonella osteomyelitis
003.8 Other specified salmonella infections
003.9 Salmonella infection, unspecified
Includes: bacillary dysentery
Infection by group A Shigella (Schmitz) (Shiga)
Infection by group B Shigella
Infection by group C Shigella
Infection by group D Shigella
004.8 Other specified shigella infections
004.9 Shigellosis, unspecified
Excludes: salmonella infections (003.0-003.9)
toxic effect of:
food contaminants (989.7)
noxious foodstuffs (988.0-988.9)
005.0 Staphylococcal food poisoning
Staphylococcal toxemia specified as due to food
Food poisoning due to Clostridium botulinum
005.2 Food poisoning due to Clostridium perfringens [C. welchii]
Enteritis necroticans
005.3 Food poisoning due to other Clostridia
005.4 Food poisoning due to Vibrio parahaemolyticus
005.8 Other bacterial food poisoning
Excludes: salmonella food poisoning (003.0-003.9)
005.81 Food poisoning due to Vibrio vulnificus
005.89 Other bacterial food poisoning
Food poisoning due to Bacillus cereus
005.9 Food poisoning, unspecified
Includes: infection due to Entamoeba histolytica
Excludes: amebiasis due to organisms other than Entamoeba histolytica (007.8)
006.0 Acute amebic dysentery without mention of abscess
Acute amebiasis
006.1 Chronic intestinal amebiasis without mention of abscess
Chronic:
amebiasis
amebic dysentery
006.2 Amebic nondysenteric colitis
Hepatic amebiasis
Amebic abscess of lung (and liver)
Amebic abscess of brain (and liver) (and lung)
Cutaneous amebiasis
006.8 Amebic infection of other sites
Amebic:
appendicitis
balanitis
Ameboma
Excludes: specific infections by free-living amebae (136.2)
Amebiasis NOS
Includes: protozoal:
colitis
diarrhea
dysentery
Infection by Balantidium coli
Infection by Giardia lamblia
Lambliasis
Infection by Isospora belli and Isospora hominis
Isosporiasis
007.3 Intestinal trichomoniasis
007.8 Other specified protozoal intestinal diseases
Amebiasis due to organisms other than Entamoeba histolytica
007.9 Unspecified protozoal intestinal disease
Flagellate diarrhea
Protozoal dysentery NOS
Includes: any condition classifiable to 009.0-009.3 with mention of the responsible organisms
Excludes: food poisoning by these organisms (005.0-005.9)
008.0 Escherichia coli [E. coli]
E. coli enteritis NOS
008.01 Enteropathogenic E. coli
008.02 Enterotoxigenic E. coli
008.04 Enterohemorrhagic E. coli
008.09 Other intestinal E. coli infections
008.1 Arizona group of paracolon bacilli
Enterobacter aerogenes
008.3 Proteus (mirabilis) (morganii)
008.4 Other specified bacteria
Staphylococcal enterocolitis
008.44 Yersinia enterocolitica
Pseudomembranous colitis
Anaerobic enteritis NOS
Bacteroides (fragilis)
Gram-negative anaerobes
008.47 Other gram-negative bacteria
Gram-negative enteritis NOS
Excludes: gram-negative anaerobes (008.46)
008.5 Bacterial enteritis, unspecified
008.6 Enteritis due to specified virus
Norwalk-like agent
008.64 Other small round viruses [SRV's]
Small round virus NOS
Coxsackie virus
Echovirus
Excludes: poliovirus (045.0-045.9)
Torovirus
008.8 Other organism, not elsewhere classified
Viral:
enteritis NOS
gastroenteritis
Excludes: influenza with involvement of gastrointestinal tract (487.8)
Excludes: diarrheal disease or intestinal infection due to specified organism (001.0-008.8)
diarrhea following gastrointestinal surgery (564.4)
intestinal malabsorption (579.0-579.9)
ischemic enteritis (557.0-557.9)
other noninfectious gastroenteritis and colitis (558.1-558.9)
regional enteritis (555.0-555.9)
ulcerative colitis (556)
009.0 Infectious colitis, enteritis, and gastroenteritis
Colitis (septic)
Dysentery:
NOS
catarrhal
hemorrhagic
Enteritis (septic)
Gastroenteritis (septic)
009.1 Colitis, enteritis, and gastroenteritis of presumed infectious origin
Excludes: colitis NOS (558.9)
enteritis NOS (558.9)
gastroenteritis NOS (558.9)
Diarrhea:
dysenteric
epidemic
Infectious diarrheal disease NOS
009.3 Diarrhea of presumed infectious origin
Excludes: diarrhea NOS (787.91)
TUBERCULOSIS (010-018)
Includes: infection by Mycobacterium tuberculosis (human) (bovine)
Excludes: congenital tuberculosis (771.2)
late effects of tuberculosis (137.0-137.4)
**NOTE** The following fifth-digit subclassification is for use with categories 010-018:
0 unspecified
1 bacteriological or histological examination not done
2 bacteriological or histological examination unknown (at present)
3 tubercle bacilli found (in sputum) by microscopy
4 tubercle bacilli not found (in sputum) by microscopy, but found by bacterial culture
5 tubercle bacilli not found by bacteriological examination, but tuberculosis confirmed histologically
6 tubercle bacilli not found by bacteriological or histological examination, but tuberculosis confirmed by other methods [inoculation of animals]
Requires fifth digit. See beginning of section 010-018 for codes and definitions.
010.0 Primary tuberculous infection
Excludes: nonspecific reaction to tuberculin skin test without active tuberculosis (795.5)
positive PPD (795.5)
positive tuberculin skin test without active tuberculosis (795.5)
010.1 Tuberculous pleurisy in primary progressive tuberculosis
010.8 Other primary progressive tuberculosis
Excludes: tuberculous erythema nodosum (017.1)
010.9 Primary tuberculous infection, unspecified
Requires fifth digit. See beginning of section 010-018 for codes and definitions.
Use additional code to identify any associated silicosis (502)
011.0 Tuberculosis of lung, infiltrative
011.1 Tuberculosis of lung, nodular
011.2 Tuberculosis of lung with cavitation
011.3 Tuberculosis of bronchus
Excludes: isolated bronchial tuberculosis (012.2)
011.4 Tuberculous fibrosis of lung
011.5 Tuberculous bronchiectasis
011.6 Tuberculous pneumonia [any form]
011.7 Tuberculous pneumothorax
011.8 Other specified pulmonary tuberculosis
011.9 Pulmonary tuberculosis, unspecified
Respiratory tuberculosis NOS
Tuberculosis of lung NOS
Requires fifth digit. See beginning of section 010-018 for codes and definitions.
Excludes: respiratory tuberculosis, unspecified (011.9)
Tuberculosis of pleura
Tuberculous empyema
Tuberculous hydrothorax
Excludes: pleurisy with effusion without mention of cause (511.9)
tuberculous pleurisy in primary progressive tuberculosis (010.1)
012.1 Tuberculosis of intrathoracic lymph nodes
Tuberculosis of lymph nodes:
hilar
mediastinal
tracheobronchial
Tuberculous tracheobronchial adenopathy
Excludes: that specified as primary (010.0-010.9)
012.2 Isolated tracheal or bronchial tuberculosis
Tuberculosis of glottis
012.8 Other specified respiratory tuberculosis
Tuberculosis of:
mediastinum
nasopharynx
nose (septum)
sinus [any nasal]
Requires fifth digit. See beginning of section 010-018 for codes and definitions.
Tuberculosis of meninges (cerebral) (spinal)
Tuberculous:
leptomeningitis
meningoencephalitis
Excludes: tuberculoma of meninges (013.1)
Tuberculosis of brain (current disease)
013.3 Tuberculous abscess of brain
013.4 Tuberculoma of spinal cord
013.5 Tuberculous abscess of spinal cord
013.6 Tuberculous encephalitis or myelitis
013.8 Other specified tuberculosis of central nervous system
013.9 Unspecified tuberculosis of central nervous system
Tuberculosis of central nervous system NOS
Requires fifth digit. See beginning of section 010-018 for codes and definitions.
Tuberculous ascites
Tuberculosis (of):
anus
intestine (large) (small)
mesenteric glands
rectum
retroperitoneal (lymph nodes)
Tuberculous enteritis
Requires fifth digit. See beginning of section 010-018 for codes and definitions.
Use additional code to identify manifestation, as:
tuberculous:
arthropathy (711.4)
necrosis of bone (730.8)
osteitis (730.8)
osteomyelitis (730.8)
synovitis (727.01)
tenosynovitis (727.01)
Pott's disease
Use additional code to identify manifestation, as:
curvature of spine [Pott's] (737.4)
kyphosis (737.4)
spondylitis (720.81)
Tuberculous dactylitis
Tuberculous mastoiditis
015.9 Tuberculosis of unspecified bones and joints
Requires fifth digit. See beginning of section 010-018 for codes and definitions.
Renal tuberculosis
Use additional code to identify manifestation, as:
tuberculous:
nephropathy (583.81)
pyelitis (590.81)
pyelonephritis (590.81)
016.5 Other male genital organs
Use additional code to identify manifestation, as:
tuberculosis of:
prostate (601.4)
seminal vesicle (608.81)
testis (608.81)
016.6 Tuberculous oophoritis and salpingitis
016.7 Other female genital organs
Tuberculous:
cervicitis
endometritis
016.9 Genitourinary tuberculosis, unspecified
Requires fifth digit. See beginning of section 010-018 for codes and definitions.
017.0 Skin and subcutaneous cellular tissue
Lupus:
exedens
vulgaris
Scrofuloderma
Tuberculosis:
colliquativa
cutis
lichenoides
papulonecrotica
verrucosa cutis
Excludes: lupus erythematosus (695.4)
disseminated (710.0)
lupus NOS (710.0)
nonspecific reaction to tuberculin skin test without active tuberculosis (795.5)
positive PPD (795.5)
positive tuberculin skin test without active tuberculosis (795.5)
017.1 Erythema nodosum with hypersensitivity reaction in tuberculosis
Bazin's disease
Erythema:
induratum
nodosum, tuberculous
Tuberculosis indurativa
Excludes: erythema nodosum NOS (695.2)
Scrofula
Scrofulous abscess
Tuberculous adenitis
Excludes: tuberculosis of lymph nodes:
bronchial and mediastinal (012.1)
mesenteric and retroperitoneal (014.8)
tuberculous tracheobronchial adenopathy (012.1)
Use additional code to identify manifestation, as:
tuberculous:
episcleritis (379.09)
interstitial keratitis (370.59)
iridocyclitis, chronic (364.11)
keratoconjunctivitis (phlyctenular) (370.31)
Tuberculosis of ear
Tuberculous otitis media
Excludes: tuberculous mastoiditis (015.6)
Addison's disease, tuberculous
Use additional code to identify manifestation, as:
tuberculosis of:
endocardium [any valve] (424.91)
myocardium (422.0)
pericardium (420.0)
Includes: tuberculosis:
disseminated
generalized
miliary, whether of a single specified site, multiple sites, or unspecified site
polyserositis
018.0 Acute miliary tuberculosis
018.8 Other specified miliary tuberculosis
018.9 Miliary tuberculosis, unspecified
ZOONOTIC BACTERIAL DISEASES (020-027)
Includes: infection by Yersinia [Pasteurella] pestis
020.8 Other specified types of plague
Abortive plague
Ambulatory plague
Pestis minor
Includes: deerfly fever
infection by Francisella [Pasteurella] tularensis
rabbit fever
021.0 Ulceroglandular tularemia
Tularemia:
cryptogenic
intestinal
typhoidal
Bronchopneumonic tularemia
021.3 Oculoglandular tularemia
021.8 Other specified tularemia
Tularemia:
generalized or disseminated
glandular
Malignant pustule
Respiratory anthrax
Wool-sorters' disease
022.2 Gastrointestinal anthrax
022.8 Other specified manifestations of anthrax
Includes: fever:
Malta
Mediterranean
undulant
Infection by more than one organism
023.9 Brucellosis, unspecified
Infection by:
Actinobacillus mallei
Malleomyces mallei
Pseudomonas mallei
Farcy
Malleus
Infection by:
Malleomyces pseudomallei
Pseudomonas pseudomallei
Whitmore's bacillus
Pseudoglanders
Rat-bite fever due to Spirillum minor [S. minus]
Sodoku
Epidemic arthritic erythema
Haverhill fever
Rat-bite fever due to Streptobacillus moniliformis
026.9 Unspecified rat-bite fever
Infection by Listeria monocytogenes
Septicemia by Listeria monocytogenes
Use additional code to identify manifestations, as meningitis (320.7)
Excludes: congenital listeriosis (771.2)
027.1 Erysipelothrix infection
Erysipeloid (of Rosenbach)
Infection by Erysipelothrix insidiosa [E. rhusiopathiae]
Septicemia by Erysipelothrix insidiosa [E. rhusiopathiae]
Pasteurella pseudotuberculosis infection by Pasteurella multocida [P. septica]
Mesenteric adenitis by Pasteurella multocida [P. septica]
Septic infection (cat bite) (dog bite) by Pasteurella multocida [P. septica]
Excludes: infection by:
Francisella [Pasteurella] tularensis (021.0-021.9)
Yersinia [Pasteurella] pestis (020.0-020.9)
027.8 Other specified zoonotic bacterial diseases
027.9 Unspecified zoonotic bacterial disease
OTHER BACTERIAL DISEASES (030-041)
Excludes: bacterial venereal diseases (098.0-099.9)
bartonellosis (088.0)
Includes: Hansen's disease
infection by Mycobacterium leprae
Lepromatous leprosy (macular) (diffuse) (infiltrated) (nodular) (neuritic)
Tuberculoid leprosy (macular) (maculoanesthetic) (major) (minor) (neuritic)
Indeterminate [uncharacteristic] leprosy (macular) (neuritic)
Borderline or dimorphous leprosy (infiltrated) (neuritic)
Infection by Mycobacterium:
avium
intracellulare [Battey bacillus]
kansasii
Battey disease
Buruli ulcer
Infection by Mycobacterium:
marinum [M. balnei]
ulcerans
Disseminated mycobacterium avium-intracellulare complex (DMAC)
Mycobacterium avium-intracellulare complex (MAC) bacteremia
031.8 Other specified mycobacterial diseases
031.9 Unspecified diseases due to mycobacteria
Atypical mycobacterium infection NOS
Includes: infection by Corynebacterium diphtheriae
Membranous angina, diphtheritic
032.1 Nasopharyngeal diphtheria
032.2 Anterior nasal diphtheria
Laryngotracheitis, diphtheritic
032.8 Other specified diphtheria
032.81 Conjunctival diphtheria
Pseudomembranous diphtheritic conjunctivitis
032.82 Diphtheritic myocarditis
032.83 Diphtheritic peritonitis
Includes: pertussis
Use additional code to identify any associated pneumonia (484.3)
033.0 Bordetella pertussis [B. pertussis]
033.1 Bordetella parapertussis [B. parapertussis]
033.8 Whooping cough due to other specified organism
Bordetella bronchiseptica [B. bronchiseptica]
033.9 Whooping cough, unspecified organism
034.0 Streptococcal sore throat
Septic:
angina
sore throat
Streptococcal:
angina
laryngitis
pharyngitis
tonsillitis
Scarlatina
Excludes: parascarlatina (057.8)
Excludes: postpartum or puerperal erysipelas (670)
036.0 Meningococcal meningitis
Cerebrospinal fever (meningococcal)
Meningitis:
cerebrospinal
epidemic
036.1 Meningococcal encephalitis
Meningococcal septicemia
036.3 Waterhouse-Friderichsen syndrome, meningococcal
Meningococcal hemorrhagic adrenalitis
Meningococcic adrenal syndrome
Waterhouse-Friderichsen syndrome NOS
036.40 Meningococcal carditis, unspecified
036.41 Meningococcal pericarditis
036.42 Meningococcal endocarditis
036.43 Meningococcal myocarditis
036.8 Other specified meningococcal infections
036.81 Meningococcal optic neuritis
036.82 Meningococcal arthropathy
036.9 Meningococcal infection, unspecified
Meningococcal infection NOS
Excludes: tetanus:
complicating:
abortion (634-638 with .0, 639.0)
ectopic or molar pregnancy (639.0)
neonatorum (771.3)
puerperal (670)
Use additional code for systemic inflammatory response syndrome (SIRS) (995.91-995.92)
Excludes: bacteremia (790.7)
septicemia (sepsis) of newborn (771.81)
038.0 Streptococcal septicemia
038.1 Staphylococcal septicemia
038.10 Staphylococcal septicemia, unspecified
038.11 Staphylococcus aureus septicemia
038.19 Other staphylococcal septicemia
038.2 Pneumococcal septicemia [Streptococcus pneumoniae septicemia]
038.3 Septicemia due to anaerobes
Septicemia due to bacteroides
Excludes: gas gangrene (040.0)
that due to anaerobic streptococci (038.0)
038.4 Septicemia due to other gram-negative organisms
038.40 Gram-negative organism, unspecified
Gram-negative septicemia NOS
038.41 Hemophilus influenzae [H. influenzae]
038.42 Escherichia coli [E. coli]
038.8 Other specified septicemias
Excludes: septicemia (due to):
anthrax (022.3)
gonococcal (098.89)
herpetic (054.5)
meningococcal (036.2)
septicemic plague (020.2)
Septicemia NOS
Excludes: bacteremia NOS (790.7)
Includes: actinomycotic mycetoma
infection by Actinomycetales, such as species of Actinomyces, Actinomadura, Nocardia, Streptomyces
maduromycosis (actinomycotic)
schizomycetoma (actinomycotic)
Erythrasma
Trichomycosis axillaris
Thoracic actinomycosis
Excludes: madura foot due to mycotic infection (117.4)
039.8 Of other specified sites
Actinomycosis NOS
Maduromycosis NOS
Nocardiosis NOS
Excludes: bacteremia NOS (790.7)
bacterial infection NOS (041.9)
Gas bacillus infection or gangrene
Infection by Clostridium:
histolyticum
oedematiens
perfringens [welchii]
septicum
sordellii
Malignant edema
Myonecrosis, clostridial
Myositis, clostridial
Intestinal lipodystrophy
040.8 Other specified bacterial diseases
Use additional code to identify the organism
Note: This category is provided to be used as an additional code to identify the bacterial agent in diseases classified elsewhere. This category will also be used to classify bacterial infections of unspecified nature or site.
Excludes: bacteremia NOS (790.7)
septicemia (038.0-038.9)
041.00 Streptococcus, unspecified
041.10 Staphylococcus, unspecified
Infection by Klebsiella pneumoniae
041.4 Escherichia coli [E.coli]
041.5 Hemophilus influenzae [H. influenzae]
041.6 Proteus (mirabilis) (morganii)
041.8 Other specified bacterial infections
Eaton's agent
Pleuropneumonia-like organisms [PPLO]
041.83 Clostridium perfringens
Gram-negative anaerobes
Excludes: Helicobacter pylori (041.86)
041.85 Other gram-negative organisms
Aerobacter aerogenes
Gram-negative bacteria NOS
Mima polymorpha
Serratia
Excludes: gram-negative anaerobes (041.84)
041.86 Helicobacter pylori (H. pylori)
041.89 Other specified bacteria
041.9 Bacterial infection, unspecified
HUMAN IMMUNODEFICIENCY VIRUS (HIV) INFECTION (042)
Acquired immune deficiency syndrome
Acquired immunodeficiency syndrome
AIDS
AIDS-like syndrome
AIDS-related complex
ARC
HIV infection, symptomatic
Use additional code(s) to identify all manifestations of HIV
Use additional code to identify HIV-2 infection (079.53)
Excludes: asymptomatic HIV infection status (V08)
exposure to HIV virus (V01.79)
nonspecific serologic evidence of HIV (795.71)
POLIOMYELITIS AND OTHER NON-ARTHROPOD-BORNE VIRAL DISEASES OF CENTRAL NERVOUS SYSTEM (045-049)
Excludes: late effects of acute poliomyelitis (138)
**NOTE** The following fifth-digit subclassification is for use with category 045:
0 poliovirus, unspecified type
1 poliovirus type I
2 poliovirus type II
3 poliovirus type III
045.0 Acute paralytic poliomyelitis specified as bulbar
Infantile paralysis (acute) specified as bulbar
Poliomyelitis (acute) (anterior) specified as bulbar
Polioencephalitis (acute) (bulbar)
Polioencephalomyelitis (acute) (anterior) (bulbar)
045.1 Acute poliomyelitis with other paralysis
Paralysis:
acute atrophic, spinal
infantile, paralytic
Poliomyelitis (acute) with paralysis except bulbar
anterior with paralysis except bulbar
epidemic with paralysis except bulbar
045.2 Acute nonparalytic poliomyelitis
Poliomyelitis (acute) specified as nonparalytic
anterior specified as nonparalytic
epidemic specified as nonparalytic
045.9 Acute poliomyelitis, unspecified
Infantile paralysis unspecified whether paralytic or nonparalytic
Poliomyelitis (acute) unspecified whether paralytic or nonparalytic
anterior unspecified whether paralytic or nonparalytic
epidemic unspecified whether paralytic or nonparalytic
046.1 Jakob-Creutzfeldt disease
Subacute spongiform encephalopathy
046.2 Subacute sclerosing panencephalitis
Dawson's inclusion body encephalitis
Van Bogaert's sclerosing leukoencephalitis
046.3 Progressive multifocal leukoencephalopathy
Multifocal leukoencephalopathy NOS
046.8 Other specified slow virus infection of central nervous system
046.9 Unspecified slow virus infection of central nervous system
Includes: meningitis:
abacterial
aseptic
viral
Excludes: meningitis due to:
adenovirus (049.1)
arthropod-borne virus (060.0-066.9)
leptospira (100.81)
virus of:
herpes simplex (054.72)
herpes zoster (053.0)
lymphocytic choriomeningitis (049.0)
mumps (072.1)
poliomyelitis (045.0-045.9)
any other infection specifically classified elsewhere
Meningo-eruptive syndrome
047.8 Other specified viral meningitis
047.9 Unspecified viral meningitis
Viral meningitis NOS
Boston exanthem
Excludes: late effects of viral encephalitis (139.0)
049.0 Lymphocytic choriomeningitis
Lymphocytic:
meningitis (serous) (benign)
meningoencephalitis (serous) (benign)
049.1 Meningitis due to adenovirus
049.8 Other specified non-arthropod-borne viral diseases of central nervous system
Encephalitis:
acute:
inclusion body
necrotizing
epidemic
lethargica
Rio Bravo
von Economo's disease
049.9 Unspecified non-arthropod-borne viral diseases of central nervous system
Viral encephalitis NOS
VIRAL DISEASES ACCOMPANIED BY EXANTHEM (050-057)
Excludes: arthropod-borne viral diseases (060.0-066.9)
Boston exanthem (048)
Hemorrhagic (pustular) smallpox
Malignant smallpox
Purpura variolosa
Variola minor
Varioloid
Vaccinia not from vaccination
Excludes: vaccinia (generalized) (from vaccination) (999.0)
Milkers' node
051.2 Contagious pustular dermatitis
Ecthyma contagiosum
Orf
051.9 Paravaccinia, unspecified
052.0 Postvaricella encephalitis
Postchickenpox encephalitis
052.1 Varicella (hemorrhagic) pneumonitis
052.7 With other specified complications
052.8 With unspecified complication
052.9 Varicella without mention of complication
Chickenpox NOS
Varicella NOS
Includes: shingles
zona
053.1 With other nervous system complications
053.10 With unspecified nervous system complication
053.11 Geniculate herpes zoster
Herpetic geniculate ganglionitis
053.12 Postherpetic trigeminal neuralgia
053.13 Postherpetic polyneuropathy
053.2 With ophthalmic complications
053.20 Herpes zoster dermatitis of eyelid
Herpes zoster ophthalmicus
053.21 Herpes zoster keratoconjunctivitis
053.22 Herpes zoster iridocyclitis
053.7 With other specified complications
053.71 Otitis externa due to herpes zoster
053.8 With unspecified complication
053.9 Herpes zoster without mention of complication
Herpes zoster NOS
Excludes: congenital herpes simplex (771.2)
Kaposi's varicelliform eruption
054.10 Genital herpes, unspecified
Herpes progenitalis
054.11 Herpetic vulvovaginitis
054.12 Herpetic ulceration of vulva
054.13 Herpetic infection of penis
054.2 Herpetic gingivostomatitis
054.3 Herpetic meningoencephalitis
Herpes encephalitis
Simian B disease
054.4 With ophthalmic complications
054.40 With unspecified ophthalmic complication
054.41 Herpes simplex dermatitis of eyelid
054.43 Herpes simplex disciform keratitis
054.44 Herpes simplex iridocyclitis
Herpetic felon
054.7 With other specified complications
054.71 Visceral herpes simplex
054.72 Herpes simplex meningitis
054.73 Herpes simplex otitis externa
054.8 With unspecified complication
054.9 Herpes simplex without mention of complication
Includes: morbilli
rubeola
055.0 Postmeasles encephalitis
055.2 Postmeasles otitis media
055.7 With other specified complications
055.71 Measles keratoconjunctivitis
Measles keratitis
055.8 With unspecified complication
055.9 Measles without mention of complication
Includes: German measles
Excludes: congenital rubella (771.0)
056.0 With neurological complications
056.00 With unspecified neurological complication
056.01 Encephalomyelitis due to rubella
Encephalitis due to rubella
Meningoencephalitis due to rubella
056.7 With other specified complications
056.71 Arthritis due to rubella
056.8 With unspecified complications
056.9 Rubella without mention of complication
057.0 Erythema infectiosum [fifth disease]
057.8 Other specified viral exanthemata
Dukes (-Filatow) disease
Exanthema subitum [sixth disease]
Fourth disease
Parascarlatina
Pseudoscarlatina
Roseola infantum
057.9 Viral exanthem, unspecified
ARTHROPOD-BORNE VIRAL DISEASES (060-066)
Use additional code to identify any associated meningitis (321.2)
Excludes: late effects of viral encephalitis (139.0)
Yellow fever:
jungle
sylvan
060.9 Yellow fever, unspecified
Breakbone fever
Excludes: hemorrhagic fever caused by dengue virus (065.4)
Japanese B encephalitis
062.1 Western equine encephalitis
062.2 Eastern equine encephalitis
Excludes: Venezuelan equine encephalitis (066.2)
Australian arboencephalitis
Australian X disease
Murray Valley encephalitis
062.5 California virus encephalitis
Encephalitis:
California
La Crosse
Tahyna fever
062.8 Other specified mosquito-borne viral encephalitis
Encephalitis by Ilheus virus
Excludes: West Nile virus (066.40-066.49)
062.9 Mosquito-borne viral encephalitis, unspecified
Includes: diphasic meningoencephalitis
063.0 Russian spring-summer [taiga] encephalitis
063.2 Central European encephalitis
063.8 Other specified tick-borne viral encephalitis
Langat encephalitis
Powassan encephalitis
063.9 Tick-borne viral encephalitis, unspecified
Arthropod-borne viral encephalitis, vector unknown
Negishi virus encephalitis
Excludes: viral encephalitis NOS (049.9)
065.0 Crimean hemorrhagic fever [CHF Congo virus]
Central Asian hemorrhagic fever
065.3 Other tick-borne hemorrhagic fever
065.4 Mosquito-borne hemorrhagic fever
Chikungunya hemorrhagic fever
Dengue hemorrhagic fever
Excludes: Chikungunya fever (066.3)
dengue (061)
yellow fever (060.0-060.9)
065.8 Other specified arthropod-borne hemorrhagic fever
Mite-borne hemorrhagic fever
065.9 Arthropod-borne hemorrhagic fever, unspecified
Arbovirus hemorrhagic fever NOS
Changuinola fever
Sandfly fever
Nairobi sheep disease
Tick fever:
American mountain
Colorado
Kemerovo
Quaranfil
Venezuelan equine encephalitis
066.3 Other mosquito-borne fever
Fever (viral):
Bunyamwera
Bwamba
Chikungunya
Guama
Mayaro
Mucambo
O'Nyong-Nyong
Oropouche
Pixuna
Rift valley
Ross river
Wesselsbron
Zika
Excludes: dengue (061)
yellow fever (060.0-060.9)
066.40 West Nile fever, unspecified
West Nile fever NOS
West Nile fever without complications
West Nile virus NOS
066.41 West Nile fever with encephalitis
West Nile encephalitis
West Nile encephalomyelitis
066.42 West Nile fever with other neurologic manifestation
Use additional code to specify the neurologic manifestation
066.49 West Nile fever with other complications
Use additional code to specify the other conditions
066.8 Other specified arthropod-borne viral diseases
Chandipura fever
Piry fever
066.9 Arthropod-borne viral disease, unspecified
Arbovirus infection NOS
OTHER DISEASES DUE TO VIRUSES AND CHLAMYDIAE (070-079)
Includes: viral hepatitis (acute) (chronic)
Excludes: cytomegalic inclusion virus hepatitis (078.5)
**NOTE** The following fifth-digit subclassification is for use with categories 070.2 and 070.3:
0 acute or unspecified, without mention of hepatitis delta
1 acute or unspecified, with hepatitis delta
2 chronic, without mention of hepatitis delta
3 chronic, with hepatitis delta
070.0 Viral hepatitis A with hepatic coma
070.1 Viral hepatitis A without mention of hepatic coma
Infectious hepatitis
070.2 Viral hepatitis B with hepatic coma
070.3 Viral hepatitis B without mention of hepatic coma
Serum hepatitis
070.4 Other specified viral hepatitis with hepatic coma
070.41 Acute hepatitis C with hepatic coma
070.42 Hepatitis delta without mention of active hepatitis B disease with hepatic coma
Hepatitis delta with hepatitis B carrier state
070.43 Hepatitis E with hepatic coma
070.44 Chronic hepatitis C with hepatic coma
070.49 Other specified viral hepatitis with hepatic coma
070.5 Other specified viral hepatitis without mention of hepatic coma
070.51 Acute hepatitis C without mention of hepatic coma
070.52 Hepatitis delta without mention of active hepatitis B disease or hepatic coma
070.53 Hepatitis E without mention of hepatic coma
070.54 Chronic hepatitis C without mention of hepatic coma
070.59 Other specified viral hepatitis without mention of hepatic coma
070.6 Unspecified viral hepatitis with hepatic coma
Excludes: unspecified viral hepatitis C with hepatic coma (070.71)
070.7 Unspecified viral hepatitis C
070.70 Unspecified viral hepatitis C without hepatic coma
Unspecified viral hepatitis C NOS
070.71 Unspecified viral hepatitis C with hepatic coma
070.9 Unspecified viral hepatitis without mention of hepatic coma
Viral hepatitis NOS
Excludes: unspecified viral hepatitis C without hepatic coma (070.70)
Hydrophobia
Lyssa
Mumps meningoencephalitis
072.7 Mumps with other specified complications
072.8 Mumps with unspecified complication
072.9 Mumps without mention of complication
Epidemic parotitis
Infectious parotitis
Includes: parrot fever
psittacosis
Lobular pneumonitis due to ornithosis
073.7 With other specified complications
073.8 With unspecified complication
Excludes: Coxsackie virus:
infection NOS (079.2)
meningitis (047.0)
Vesicular pharyngitis
Bornholm disease
Devil's grip
Epidemic:
myalgia
myositis
074.20 Coxsackie carditis, unspecified
Aseptic myocarditis of newborn
074.3 Hand, foot, and mouth disease
Vesicular stomatitis and exanthem
074.8 Other specified diseases due to Coxsackie virus
Acute lymphonodular pharyngitis
Glandular fever
Monocytic angina
Pfeiffer's disease
Excludes: late effect of trachoma (139.1)
Trachoma dubium
Granular conjunctivitis (trachomatous)
Trachomatous:
follicular conjunctivitis
pannus
Trachoma NOS
Excludes: ophthalmic complications of viral diseases classified elsewhere
077.0 Inclusion conjunctivitis
Paratrachoma
Swimming pool conjunctivitis
Excludes: inclusion blennorrhea (neonatal) (771.6)
077.1 Epidemic keratoconjunctivitis
Shipyard eye
077.2 Pharyngoconjunctival fever
Viral pharyngoconjunctivitis
077.3 Other adenoviral conjunctivitis
Acute adenoviral follicular conjunctivitis
077.4 Epidemic hemorrhagic conjunctivitis
Apollo:
conjunctivitis
disease
Conjunctivitis due to enterovirus type 70
Hemorrhagic conjunctivitis (acute) (epidemic)
077.8 Other viral conjunctivitis
Newcastle conjunctivitis
077.9 Unspecified diseases of conjunctiva due to viruses and Chlamydiae
Viral conjunctivitis NOS
Excludes: viral infection NOS (079.0-079.9)
viremia NOS (790.8)
Viral warts due to human papillomavirus
078.10 Viral warts, unspecified
Condyloma NOS
Verruca NOS:
NOS
Vulgaris
Warts (infectious)
078.19 Other specified viral warts
Genital warts NOS
Verruca
plana
plantaris
Miliary fever
Sweating disease
Benign lymphoreticulosis (of inoculation)
Cat-scratch fever
Aphthous fever
Epizootic:
aphthae
stomatitis
Cytomegalic inclusion disease
Salivary gland virus disease
Use additional code to identify manifestation, as:
cytomegalic inclusion virus:
hepatitis (573.1)
pneumonia (484.1)
Excludes: congenital cytomegalovirus infection (771.1)
078.6 Hemorrhagic nephrosonephritis
Hemorrhagic fever:
epidemic
Korean
Russian with renal syndrome
078.7 Arenaviral hemorrhagic fever
Hemorrhagic fever:
Argentine
Bolivian
Junin virus
Machupo virus
078.8 Other specified diseases due to viruses and Chlamydiae
Excludes: epidemic diarrhea (009.2)
lymphogranuloma venereum (099.1)
078.82 Epidemic vomiting syndrome
Winter vomiting disease
078.88 Other specified diseases due to Chlamydiae
078.89 Other specified diseases due to viruses
Epidemic cervical myalgia
Marburg disease
Tanapox
Note: This category is provided to be used as an additional code to identify the viral agent in diseases classifiable elsewhere. This category will also be used to classify virus infection of unspecified nature or site.
Excludes: human immunodeficiency virus, type 1 [HIV-1] (042)
human T-cell lymphotrophic virus, type III [HTLV-III] (042)
lymphadenopathy-associated virus [LAV] (042)
079.50 Retrovirus, unspecified
079.51 Human T-cell lymphotrophic virus, type I [HTLV-I]
079.52 Human T-cell lymphotrophic virus, type II [HTLV-II]
079.53 Human immunodeficiency virus, type 2 [HIV-2]
079.59 Other specified retrovirus
079.6 Respiratory syncytial virus (RSV)
079.8 Other specified viral and chlamydial infections
079.82 SARS-associated coronavirus
079.88 Other specified chlamydial infection
079.89 Other specified viral infection
079.9 Unspecified viral and chlamydial infections
Excludes: viremia NOS (790.8)
079.98 Unspecified chlamydial infection
Chlamydial infection NOS
079.99 Unspecified viral infection
Viral infection NOS
RICKETTSIOSES AND OTHER ARTHROPOD-BORNE DISEASES (080-088)
Excludes: arthropod-borne viral diseases (060.0-066.9)
Typhus (fever):
classical
epidemic
exanthematic NOS
louse-borne
Typhus (fever):
endemic
flea-borne
Brill-Zinsser disease
Recrudescent typhus (fever)
Japanese river fever
Kedani fever
Mite-borne typhus
Tsutsugamushi
Typhus (fever) NOS
Rocky mountain spotted fever
Sao Paulo fever
African tick typhus
India tick typhus
Kenya tick typhus
Marseilles fever
Mediterranean tick fever
Siberian tick typhus
082.40 Ehrlichiosis, unspecified
082.41 Ehrlichiosis chaffeensis [E. chaffeensis]
082.8 Other specified tick-borne rickettsioses
Lone star fever
082.9 Tick-borne rickettsiosis, unspecified
Tick-borne typhus NOS
Quintan fever
Wolhynian fever
Vesicular rickettsiosis
083.8 Other specified rickettsioses
083.9 Rickettsiosis, unspecified
Note: Subcategories 084.0-084.6 exclude the listed conditions with mention of pernicious complications (084.8-084.9).
Excludes: congenital malaria (771.2)
084.0 Falciparum malaria [malignant tertian]
Malaria (fever):
by Plasmodium falciparum
subtertian
084.1 Vivax malaria [benign tertian]
Malaria (fever) by Plasmodium vivax
Malaria (fever) by Plasmodium malariae
Malariae malaria
Malaria (fever) by Plasmodium ovale
Monkey malaria
Malaria (fever) by more than one parasite
Malaria (fever) NOS
Therapeutically induced malaria
Excludes: accidental infection from syringe, blood transfusion, etc. (084.0-084.6, above, according to parasite species)
transmission from mother to child during delivery (771.2)
Hemoglobinuric:
fever (bilious)
malaria
Malarial hemoglobinuria
084.9 Other pernicious complications of malaria
Algid malaria
Cerebral malaria
Use additional code to identify complication, as:
malarial:
hepatitis (573.2)
nephrosis (581.81)
Dumdum fever
Infection by Leishmania:
donovani
infantum
Leishmaniasis:
dermal, post-kala-azar
Mediterranean
visceral (Indian)
Aleppo boil
Baghdad boil
Delhi boil
Infection by Leishmania tropica (minor)
Leishmaniasis, cutaneous:
dry form
late
recurrent
ulcerating
Oriental sore
Infection by Leishmania tropica major
Leishmaniasis, cutaneous:
acute necrotizing
rural
wet form
zoonotic form
Infection by Leishmania ethiopica
Leishmaniasis, cutaneous:
diffuse
lepromatous
Chiclero ulcer
Infection by Leishmania mexicana
Leishmaniasis tegumentaria diffusa
085.5 Mucocutaneous (American)
Espundia
Infection by Leishmania braziliensis
Uta
085.9 Leishmaniasis, unspecified
Use additional code to identify manifestations, as:
trypanosomiasis:
encephalitis (323.2)
meningitis (321.3)
086.0 Chagas' disease with heart involvement
American trypanosomiasis with heart involvement
Infection by Trypanosoma cruzi with heart involvement
Any condition classifiable to 086.2 with heart involvement
086.1 Chagas' disease with other organ involvement
American trypanosomiasis with involvement of organ other than heart
Infection by Trypanosoma cruzi with involvement of organ other than heart
Any condition classifiable to 086.2 with involvement of organ other than heart
086.2 Chagas' disease without mention of organ involvement
American trypanosomiasis
Infection by Trypanosoma cruzi
Gambian sleeping sickness
Infection by Trypanosoma gambiense
086.4 Rhodesian trypanosomiasis
Infection by Trypanosoma rhodesiense
Rhodesian sleeping sickness
086.5 African trypanosomiasis, unspecified
Sleeping sickness NOS
086.9 Trypanosomiasis, unspecified
Includes: recurrent fever
087.9 Relapsing fever, unspecified
Carrión's disease
Oroya fever
Verruga peruana
088.8 Other specified arthropod-borne diseases
Erythema chronicum migrans
Babesiasis
088.9 Arthropod-borne disease, unspecified
SYPHILIS AND OTHER VENEREAL DISEASES (090-099)
Excludes: nonvenereal endemic syphilis (104.0)
urogenital trichomoniasis (131.0)
090.0 Early congenital syphilis, symptomatic
Congenital syphilitic:
choroiditis
coryza (chronic)
hepatomegaly
mucous patches
periostitis
splenomegaly
Syphilitic (congenital):
epiphysitis
osteochondritis
pemphigus
Any congenital syphilitic condition specified as early or manifest less than two years after birth
090.1 Early congenital syphilis, latent
Congenital syphilis without clinical manifestations, with positive serological reaction and negative spinal fluid test, less than two years after birth
090.2 Early congenital syphilis, unspecified
Congenital syphilis NOS, less than two years after birth
090.3 Syphilitic interstitial keratitis
Syphilitic keratitis:
parenchymatous
punctata profunda
Excludes: interstitial keratitis NOS (370.50)
Use additional code to identify any associated mental disorder
090.40 Juvenile neurosyphilis, unspecified
Congenital neurosyphilis
Dementia paralytica juvenilis
Juvenile:
general paresis
tabes
taboparesis
090.41 Congenital syphilitic encephalitis
090.42 Congenital syphilitic meningitis
090.5 Other late congenital syphilis, symptomatic
Gumma due to congenital syphilis
Hutchinson's teeth
Syphilitic saddle nose
Any congenital syphilitic condition specified as late or manifest two years or more after birth
090.6 Late congenital syphilis, latent
Congenital syphilis without clinical manifestations, with positive serological reaction and negative spinal fluid test, two years or more after birth
090.7 Late congenital syphilis, unspecified
Congenital syphilis NOS, two years or more after birth
090.9 Congenital syphilis, unspecified
Excludes: early cardiovascular syphilis (093.0-093.9)
early neurosyphilis (094.0-094.9)
091.0 Genital syphilis (primary)
Genital chancre
Primary syphilis of:
breast
fingers
lip
tonsils
091.3 Secondary syphilis of skin or mucous membranes
Condyloma latum
Secondary syphilis of:
anus
mouth
pharynx
skin
tonsils
vulva
091.4 Adenopathy due to secondary syphilis
Syphilitic adenopathy (secondary)
Syphilitic lymphadenitis (secondary)
091.5 Uveitis due to secondary syphilis
091.50 Syphilitic uveitis, unspecified
091.51 Syphilitic chorioretinitis (secondary)
091.52 Syphilitic iridocyclitis (secondary)
091.6 Secondary syphilis of viscera and bone
091.61 Secondary syphilitic periostitis
091.62 Secondary syphilitic hepatitis
Secondary syphilis of liver
091.7 Secondary syphilis, relapse
Secondary syphilis, relapse (treated) (untreated)
091.8 Other forms of secondary syphilis
091.81 Acute syphilitic meningitis (secondary)
091.9 Unspecified secondary syphilis
Includes: syphilis (acquired) without clinical manifestations, with positive serological reaction and negative spinal fluid test, less than two years after infection
092.0 Early syphilis, latent, serological relapse after treatment
092.9 Early syphilis, latent, unspecified
093.0 Aneurysm of aorta, specified as syphilitic
Dilatation of aorta, specified as syphilitic
Syphilitic ostial coronary disease
Syphilitic aortic incompetence or stenosis
093.8 Other specified cardiovascular syphilis
093.81 Syphilitic pericarditis
093.9 Cardiovascular syphilis, unspecified
Use additional code to identify any associated mental disorder
Locomotor ataxia (progressive)
Posterior spinal sclerosis (syphilitic)
Tabetic neurosyphilis
Use additional code to identify manifestation, as:
neurogenic arthropathy [Charcot's joint disease] (713.5)
Dementia paralytica
General paralysis (of the insane) (progressive)
Paretic neurosyphilis
Taboparesis
Meningovascular syphilis
Excludes: acute syphilitic meningitis (secondary) (091.81)
094.3 Asymptomatic neurosyphilis
094.8 Other specified neurosyphilis
094.81 Syphilitic encephalitis
094.82 Syphilitic Parkinsonism
094.83 Syphilitic disseminated retinochoroiditis
094.84 Syphilitic optic atrophy
094.85 Syphilitic retrobulbar neuritis
094.86 Syphilitic acoustic neuritis
094.87 Syphilitic ruptured cerebral aneurysm
094.9 Neurosyphilis, unspecified
Gumma (syphilitic) of central nervous system NOS
Syphilis (early) (late) of central nervous system NOS
Syphiloma of central nervous system NOS
Includes: gumma (syphilitic)
tertiary, or unspecified stage
Syphilitic myositis
095.7 Syphilis of synovium, tendon, and bursa
Syphilitic:
bursitis
synovitis
095.8 Other specified forms of late symptomatic syphilis
Excludes: cardiovascular syphilis (093.0-093.9)
neurosyphilis (094.0-094.9)
095.9 Late symptomatic syphilis, unspecified
Syphilis (acquired) without clinical manifestations, with positive serological reaction and negative spinal fluid test, two years or more after infection
097.0 Late syphilis, unspecified
097.1 Latent syphilis, unspecified
Positive serological reaction for syphilis
Syphilis (acquired) NOS
Excludes: syphilis NOS causing death under two years of age (090.9)
098.0 Acute, of lower genitourinary tract
Gonococcal:
Bartholinitis (acute)
urethritis (acute)
vulvovaginitis (acute)
Gonorrhea (acute):
NOS
genitourinary (tract) NOS
098.1 Acute, of upper genitourinary tract
098.10 Gonococcal infection (acute) of upper genitourinary tract, site unspecified
098.11 Gonococcal cystitis (acute)
Gonorrhea (acute) of bladder
098.12 Gonococcal prostatitis (acute)
098.13 Gonococcal epididymo-orchitis (acute)
Gonococcal orchitis (acute)
098.14 Gonococcal seminal vesiculitis (acute)
Gonorrhea (acute) of seminal vesicle
098.15 Gonococcal cervicitis (acute)
Gonorrhea (acute) of cervix
098.16 Gonococcal endometritis (acute)
Gonorrhea (acute) of uterus
098.17 Gonococcal salpingitis, specified as acute
098.2 Chronic, of lower genitourinary tract
Gonococcal specified as chronic or with duration of two months or more:
Bartholinitis specified as chronic or with duration of two months or more
urethritis specified as chronic or with duration of two months or more
vulvovaginitis specified as chronic or with duration of two months or more
Gonorrhea specified as chronic or with duration of two months or more:
NOS specified as chronic or with duration of two months or more
genitourinary (tract) specified as chronic or with duration of two months or more
Any condition classifiable to 098.0 specified as chronic or with duration of two months or more
098.3 Chronic, of upper genitourinary tract
Any condition classifiable to 098.1 stated as chronic or with a duration of two months or more
098.30 Chronic gonococcal infection of upper genitourinary tract, site unspecified
098.31 Gonococcal cystitis, chronic
Any condition classifiable to 098.11, specified as chronic
Gonorrhea of bladder, chronic
098.32 Gonococcal prostatitis, chronic
Any condition classifiable to 098.12, specified as chronic
098.33 Gonococcal epididymo-orchitis, chronic
Any condition classifiable to 098.13, specified as chronic
Chronic gonococcal orchitis
098.34 Gonococcal seminal vesiculitis, chronic
Any condition classifiable to 098.14, specified as chronic
Gonorrhea of seminal vesicle, chronic
098.35 Gonococcal cervicitis, chronic
Any condition classifiable to 098.15, specified as chronic
Gonorrhea of cervix, chronic
098.36 Gonococcal endometritis, chronic
Any condition classifiable to 098.16, specified as chronic
098.37 Gonococcal salpingitis (chronic)
098.4 Gonococcal infection of eye
098.40 Gonococcal conjunctivitis (neonatorum)
Gonococcal ophthalmia (neonatorum)
098.41 Gonococcal iridocyclitis
098.42 Gonococcal endophthalmia
098.5 Gonococcal infection of joint
Gonococcal infection of joint NOS
098.51 Gonococcal synovitis and tenosynovitis
Gonococcal rheumatism
098.6 Gonococcal infection of pharynx
098.7 Gonococcal infection of anus and rectum
Gonococcal proctitis
098.8 Gonococcal infection of other specified sites
098.81 Gonococcal keratosis (blennorrhagica)
098.83 Gonococcal pericarditis
098.84 Gonococcal endocarditis
098.85 Other gonococcal heart disease
Gonococcemia
Bubo (inguinal):
chancroidal
due to Hemophilus ducreyi
Chancre:
Ducrey's simple soft
Ulcus molle (cutis) (skin)
099.1 Lymphogranuloma venereum
Climatic or tropical bubo
(Durand-) Nicolas-Favre disease
Esthiomene
Lymphogranuloma inguinale
Donovanosis
Granuloma pudendi (ulcerating)
Granuloma venereum
Pudendal ulcer
Reiter's syndrome
Use additional code for associated:
arthropathy (711.1)
conjunctivitis (372.33)
099.4 Other nongonococcal urethritis [NGU]
Nonspecific urethritis
099.49 Other specified organism
099.5 Other venereal diseases due to Chlamydia trachomatis
Excludes: Chlamydia trachomatis infection of conjunctiva (076.0-076.9, 077.0, 077.9)
Lymphogranuloma venereum (099.1)
099.53 Lower genitourinary sites
Excludes: urethra (099.41)
Use additional code to specify site of infection, such as:
bladder (595.4)
cervix (616.0)
vagina and vulva (616.11)
099.54 Other genitourinary sites
Use additional code to specify site of infection, such as:
pelvic inflammatory disease NOS (614.9)
testis and epididymis (604.91)
099.55 Unspecified genitourinary site
Perihepatitis
099.8 Other specified venereal diseases
099.9 Venereal disease, unspecified
OTHER SPIROCHETAL DISEASES (100-104)
100.0 Leptospirosis icterohemorrhagica
Leptospiral or spirochetal jaundice (hemorrhagic)
Weil's disease
100.8 Other specified leptospiral infections
100.81 Leptospiral meningitis (aseptic)
Fever:
Fort Bragg
pretibial
swamp
Infection by Leptospira:
australis
bataviae
pyrogenes
100.9 Leptospirosis, unspecified
Acute necrotizing ulcerative:
gingivitis
stomatitis
Fusospirochetal pharyngitis
Spirochetal stomatitis
Trench mouth
Vincent's:
gingivitis
infection [any site]
Includes: frambesia
pian
Chancre of yaws
Frambesia, initial or primary
Initial frambesial ulcer
Mother yaw
102.1 Multiple papillomata and wet crab yaws
Butter yaws
Frambesioma
Pianoma
Plantar or palmar papilloma of yaws
102.2 Other early skin lesions
Early yaws (cutaneous) (macular) (papular) (maculopapular) (micropapular)
Frambeside of early yaws
Cutaneous yaws, less than five years after infection
Ghoul hand
Hyperkeratosis, palmar or plantar (early) (late) due to yaws
Worm-eaten soles
Nodular late yaws (ulcerated)
Gummatous frambeside
Rhinopharyngitis mutilans
Goundou of yaws (late)
Gumma, bone of yaws (late)
Gummatous osteitis or periostitis of yaws (late)
Hydrarthrosis of yaws (early) (late)
Osteitis of yaws (early) (late)
Periostitis (hypertrophic) of yaws (early) (late)
Juxta-articular nodules of yaws
Mucosal yaws
Yaws without clinical manifestations, with positive serology
Chancre (primary) of pinta [carate]
Papule (primary) of pinta [carate]
Pintid of pinta [carate]
Erythematous plaques of pinta [carate]
Hyperchromic lesions of pinta [carate]
Hyperkeratosis of pinta [carate]
Cardiovascular lesions of pinta [carate]
Skin lesions of pinta [carate]:
achromic of pinta [carate]
cicatricial of pinta [carate]
dyschromic of pinta [carate]
Vitiligo of pinta [carate]
Achromic and hyperchromic skin lesions of pinta [carate]
104.0 Nonvenereal endemic syphilis
Bejel
Njovera
104.8 Other specified spirochetal infections
Excludes: relapsing fever (087.0-087.9)
syphilis (090.0-097.9)
104.9 Spirochetal infection, unspecified
MYCOSES (110-118)
Use additional code to identify manifestation, as:
arthropathy (711.6)
meningitis (321.0-321.1)
otitis externa (380.15)
Excludes: infection by Actinomycetales, such as species of Actinomyces, Actinomadura, Nocardia, Streptomyces (039.0-039.9)
Includes: infection by species of Epidermophyton, Microsporum, and Trichophyton
tinea, any type except those in 111
Kerion
Sycosis, mycotic
Trichophytic tinea [black dot tinea], scalp
Dermatophytic onychia
Onychomycosis
Tinea unguium
Tinea manuum
110.3 Of groin and perianal area
Dhobie itch
Eczema marginatum
Tinea cruris
Athlete's foot
Tinea pedis
Herpes circinatus
Tinea imbricata [Tokelau]
110.6 Deep seated dermatophytosis
Granuloma trichophyticum
Majocchi's granuloma
110.8 Of other specified sites
Favus NOS
Microsporic tinea NOS
Ringworm NOS
Infection by Malassezia [Pityrosporum] furfur
Tinea flava
Tinea versicolor
Infection by Cladosporium species
Keratomycosis nigricans
Microsporosis nigra
Pityriasis nigra
Tinea palmaris nigra
Infection by Trichosporon (beigelii) cutaneum
White piedra
Infection by Piedraia hortai
111.8 Other specified dermatomycoses
111.9 Dermatomycosis, unspecified
Includes: infection by Candida species
moniliasis
Excludes: neonatal monilial infection (771.7)
Thrush (oral)
Candidal vulvovaginitis
Monilial vulvovaginitis
112.2 Of other urogenital sites
Candidal balanitis
Candidal intertrigo
Candidal onychia
Candidal perionyxis [paronychia]
Candidal pneumonia
Systemic candidiasis
112.8 Of other specified sites
112.82 Candidal otitis externa
Otomycosis in moniliasis
Includes: infection by Coccidioides (immitis)
Posada-Wernicke disease
114.0 Primary coccidioidomycosis (pulmonary)
Acute pulmonary coccidioidomycosis
Coccidioidomycotic pneumonitis
Desert rheumatism
Pulmonary coccidioidomycosis
San Joaquin Valley fever
114.1 Primary extrapulmonary coccidioidomycosis
Chancriform syndrome
Primary cutaneous coccidioidomycosis
114.3 Other forms of progressive coccidioidomycosis
Coccidioidal granuloma
Disseminated coccidioidomycosis
114.4 Chronic pulmonary coccidioidomycosis
114.5 Pulmonary coccidioidomycosis, unspecified
114.9 Coccidioidomycosis, unspecified
**NOTE** The following fifth-digit subclassification is for use with category 115:
0 without mention of manifestation
1 meningitis
2 retinitis
3 pericarditis
4 endocarditis
5 pneumonia
9 other
115.0 Infection by Histoplasma capsulatum
American histoplasmosis
Darling's disease
Reticuloendothelial cytomycosis
Small form histoplasmosis
115.1 Infection by Histoplasma duboisii
African histoplasmosis
Large form histoplasmosis
115.9 Histoplasmosis, unspecified
Histoplasmosis NOS
Blastomycotic dermatitis
Chicago disease
Cutaneous blastomycosis
Disseminated blastomycosis
Gilchrist's disease
Infection by Blastomyces [Ajellomyces] dermatitidis
North American blastomycosis
Primary pulmonary blastomycosis
Brazilian blastomycosis
Infection by Paracoccidioides [Blastomyces] brasiliensis
Lutz-Splendore-Almeida disease
Mucocutaneous-lymphangitic paracoccidioidomycosis
Pulmonary paracoccidioidomycosis
South American blastomycosis
Visceral paracoccidioidomycosis
Infections by Loboa [Blastomyces] loboi
Keloidal blastomycosis
Lobo's disease
Infection by Rhinosporidium seeberi
Cutaneous sporotrichosis
Disseminated sporotrichosis
Infection by Sporothrix [Sporotrichum] schenckii
Lymphocutaneous sporotrichosis
Pulmonary sporotrichosis
Sporotrichosis of the bones
Chromomycosis
Infection by Cladosporidium carrionii, Fonsecaea compactum, Fonsecaea pedrosoi, Phialophora verrucosa
Infection by Aspergillus species, mainly A. fumigatus, A. flavus group, A. terreus group
Infection by various genera and species of Ascomycetes and Deuteromycetes, such as Acremonium [Cephalosporium] falciforme, Neotestudina rosatii, Madurella grisea, Madurella mycetomii, Pyrenochaeta romeroi, Zopfia [Leptosphaeria] senegalensis
Madura foot, mycotic
Maduromycosis, mycotic
Excludes: actinomycotic mycetomas (039.0-039.9)
Busse-Buschke's disease
European cryptococcosis
Infection by Cryptococcus neoformans
Pulmonary cryptococcosis
Systemic cryptococcosis
Torula
117.6 Allescheriosis [Petriellidosis]
Infections by Allescheria [Petriellidium] boydii [Monosporium apiospermum]
Excludes: mycotic mycetoma (117.4)
117.7 Zygomycosis [Phycomycosis or Mucormycosis]
Infection by species of Absidia, Basidiobolus, Conidiobolus, Cunninghamella, Entomophthora, Mucor, Rhizopus, Saksenaea
117.8 Infection by dematiacious fungi [Phaehyphomycosis]
Infection by dematiacious fungi, such as Cladosporium trichoides [bantianum], Dreschlera hawaiiensis, Phialophora gougerotii, Phialophora jeanselmi
117.9 Other and unspecified mycoses
Infection of skin, subcutaneous tissues, and/or organs by a wide variety of fungi generally considered to be pathogenic to compromised hosts only (e.g., infection by species of Alternaria, Dreschlera, Fusarium)
HELMINTHIASES (120-129)
Vesical schistosomiasis NOS
Intestinal schistosomiasis NOS
Asiatic schistosomiasis NOS
Katayama disease or fever
Cercarial dermatitis
Infection by cercariae of Schistosoma
Schistosome dermatitis
Swimmers' itch
120.8 Other specified schistosomiasis
Infection by Schistosoma:
bovis
intercalatum
mattheii
Infection by Schistosoma spindale
Schistosomiasis chestermani
120.9 Schistosomiasis, unspecified
Blood flukes NOS
Hemic distomiasis
Infection by:
cat liver fluke
Opisthorchis (felineus) (tenuicollis) (viverrini)
Biliary cirrhosis due to clonorchiasis
Chinese liver fluke disease
Hepatic distomiasis due to Clonorchis sinensis
Oriental liver fluke disease
Infection by Paragonimus
Lung fluke disease (oriental)
Pulmonary distomiasis
Infection by Fasciola:
gigantica
hepatica
Liver flukes NOS
Sheep liver fluke infection
Infection by Fasciolopsis (buski)
Intestinal distomiasis
Infection by Metagonimus yokogawai
Infection by:
Heterophyes heterophyes
Stellantchasmus falcatus
121.8 Other specified trematode infections
Infection by:
Dicrocoelium dendriticum
Echinostoma ilocanum
Gastrodiscoides hominis
121.9 Trematode infection, unspecified
Distomiasis NOS
Fluke disease NOS
Includes: echinococciasis
hydatid disease
hydatidosis
122.0 Echinococcus granulosus infection of liver
122.1 Echinococcus granulosus infection of lung
122.2 Echinococcus granulosus infection of thyroid
122.3 Echinococcus granulosus infection, other
122.4 Echinococcus granulosus infection, unspecified
122.5 Echinococcus multilocularis infection of liver
122.6 Echinococcus multilocularis infection, other
122.7 Echinococcus multilocularis infection, unspecified
122.8 Echinococcosis, unspecified, of liver
122.9 Echinococcosis, other and unspecified
123.0 Taenia solium infection, intestinal form
Pork tapeworm (adult) (infection)
Cysticerciasis
Infection by Cysticercus cellulosae [larval form of Taenia solium]
123.2 Taenia saginata infection
Beef tapeworm (infection)
Infection by Taeniarhynchus saginatus
123.4 Diphyllobothriasis, intestinal
Diphyllobothrium (adult) (latum) (pacificum) infection
Fish tapeworm (infection)
123.5 Sparganosis [larval diphyllobothriasis]
Infection by:
Diphyllobothrium larvae
Sparganum (mansoni) (proliferum)
Spirometra larvae
Dwarf tapeworm (infection)
Hymenolepis (diminuta) (nana) infection
Rat tapeworm (infection)
123.8 Other specified cestode infection
Diplogonoporus (grandis) infection
Dipylidium (caninum) infection
Dog tapeworm (infection)
123.9 Cestode infection, unspecified
Tapeworm (infection) NOS
Trichinella spiralis infection
Trichinellosis
Trichiniasis
Chyluria due to Wuchereria bancrofti
Elephantiasis due to Wuchereria bancrofti
Infection due to Wuchereria bancrofti
Lymphadenitis due to Wuchereria bancrofti
Lymphangitis due to Wuchereria bancrofti
Wuchereriasis
Brugia filariasis due to Brugia [Wuchereria] malayi
Chyluria due to Brugia [Wuchereria] malayi
Elephantiasis due to Brugia [Wuchereria] malayi
Infection due to Brugia [Wuchereria] malayi
Lymphadenitis due to Brugia [Wuchereria] malayi
Lymphangitis due to Brugia [Wuchereria] malayi
Eyeworm disease of Africa
Loa loa infection
Onchocerca volvulus infection
Onchocercosis
Infection by:
Acanthocheilonema perstans
Dipetalonema perstans
125.5 Mansonella ozzardi infection
Filariasis ozzardi
125.6 Other specified filariasis
Dirofilaria infection
Infection by:
Acanthocheilonema streptocerca
Dipetalonema streptocerca
Guinea-worm infection
Infection by Dracunculus medinensis
Includes: cutaneous larva migrans due to Ancylostoma
hookworm (disease) (infection)
uncinariasis
126.8 Other specified Ancylostoma
126.9 Ancylostomiasis and necatoriasis, unspecified
Creeping eruption NOS
Cutaneous larva migrans NOS
Ascaridiasis
Infection by Ascaris lumbricoides
Roundworm infection
Infection by Anisakis larva
Infection by Strongyloides stercoralis
Excludes: trichostrongyliasis (127.6)
Infection by Trichuris trichiuria
Trichocephaliasis
Whipworm (disease) (infection)
Infection by Enterobius vermicularis
Oxyuriasis
Oxyuris vermicularis infection
Pinworm (disease) (infection)
Threadworm infection
Infection by Capillaria philippinensis
Excludes: infection by Capillaria hepatica (128.8)
Infection by Trichostrongylus species
127.7 Other specified intestinal helminthiasis
Infection by:
Oesophagostomum apiostomum and related species
Ternidens diminutus
other specified intestinal helminth
Physalopteriasis
127.8 Mixed intestinal helminthiasis
Infection by intestinal helminths classified to more than one of the categories 120.0-127.7
Mixed helminthiasis NOS
127.9 Intestinal helminthiasis, unspecified
Larva migrans visceralis
Toxocara (canis) (cati) infection
Visceral larva migrans syndrome
Infection by Gnathostoma spinigerum and related species
128.8 Other specified helminthiasis
Infection by:
Angiostrongylus cantonensis
Capillaria hepatica
other specified helminth
128.9 Helminth infection, unspecified
Helminthiasis NOS
Worms NOS
OTHER INFECTIOUS AND PARASITIC DISEASES (130-136)
Includes: infection by toxoplasma gondii
toxoplasmosis (acquired)
Excludes: congenital toxoplasmosis (771.2)
130.0 Meningoencephalitis due to toxoplasmosis
Encephalitis due to acquired toxoplasmosis
130.1 Conjunctivitis due to toxoplasmosis
130.2 Chorioretinitis due to toxoplasmosis
Focal retinochoroiditis due to acquired toxoplasmosis
130.3 Myocarditis due to toxoplasmosis
130.4 Pneumonitis due to toxoplasmosis
130.5 Hepatitis due to toxoplasmosis
130.7 Toxoplasmosis of other specified sites
130.8 Multisystemic disseminated toxoplasmosis
Toxoplasmosis of multiple sites
130.9 Toxoplasmosis, unspecified
Includes: infection due to Trichomonas (vaginalis)
131.0 Urogenital trichomoniasis
131.00 Urogenital trichomoniasis, unspecified
Fluor (vaginalis) trichomonal or due to Trichomonas (vaginalis)
Leukorrhea (vaginalis) trichomonal or due to Trichomonas (vaginalis)
131.01 Trichomonal vulvovaginitis
Vaginitis, trichomonal or due to Trichomonas (vaginalis)
131.03 Trichomonal prostatitis
Excludes: intestinal (007.3)
131.9 Trichomoniasis, unspecified
132.0 Pediculus capitis [head louse]
132.1 Pediculus corporis [body louse]
132.2 Phthirus pubis [pubic louse]
Pediculus pubis
Infestation classifiable to more than one of the categories 132.0-132.2
132.9 Pediculosis, unspecified
Infestation by Sarcoptes scabiei
Norwegian scabies
Sarcoptic itch
Chiggers
Infestation by:
Demodex folliculorum
Trombicula
Infestation by mites NOS
Infestation by:
Dermatobia (hominis)
fly larvae
Gasterophilus (intestinalis)
maggots
Oestrus ovis
134.1 Other arthropod infestation
Infestation by:
chigoe
sand flea
Tunga penetrans
Jigger disease
Scarabiasis
Tungiasis
Hirudiniasis (external) (internal)
Leeches (aquatic) (land)
134.8 Other specified infestations
134.9 Infestation, unspecified
Infestation (skin) NOS
Skin parasites NOS
Besnier-Boeck-Schaumann disease
Lupoid (miliary) of Boeck
Lupus pernio (Besnier)
Lymphogranulomatosis, benign (Schaumann's)
Sarcoid (any site):
NOS
Boeck
Darier-Roussy
Uveoparotid fever
Dactylolysis spontanea
136.2 Specific infections by free-living amebae
Meningoencephalitis due to Naegleria
Pneumonia due to Pneumocystis carinii
Infection by Sarcocystis lindemanni
136.8 Other specified infectious and parasitic diseases
Candiru infestation
136.9 Unspecified infectious and parasitic diseases
Infectious disease NOS
Parasitic disease NOS
LATE EFFECTS OF INFECTIOUS AND PARASITIC DISEASES (137-139)
Note: This category is to be used to indicate conditions classifiable to 010-018 as the cause of late effects, which are themselves classified elsewhere. The "late effects" include those specified as such, as sequelae, or as due to old or inactive tuberculosis, without evidence of active disease.
137.0 Late effects of respiratory or unspecified tuberculosis
137.1 Late effects of central nervous system tuberculosis
137.2 Late effects of genitourinary tuberculosis
137.3 Late effects of tuberculosis of bones and joints
137.4 Late effects of tuberculosis of other specified organs
Note: This category is to be used to indicate conditions classifiable to 045 as the cause of late effects, which are themselves classified elsewhere. The "late effects" include conditions specified as such, or as sequelae, or as due to old or inactive poliomyelitis, without evidence of active disease.
Note: This category is to be used to indicate conditions classifiable to categories 001-009, 020-041, 046-136 as the cause of late effects, which are themselves classified elsewhere. The "late effects" include conditions specified as such; they also include sequela of diseases classifiable to the above categories if there is evidence that the disease itself is no longer present.
139.0 Late effects of viral encephalitis
Late effects of conditions classifiable to 049.8-049.9, 062-064
139.1 Late effects of trachoma
Late effects of conditions classifiable to 076
139.8 Late effects of other and unspecified infectious and parasitic diseases
2. NEOPLASMS (140-239)
1. Content:
This chapter contains the following broad groups:
140-195 Malignant neoplasms, stated or presumed to be primary, of specified sites, except of lymphatic and hematopoietic tissue
196-198 Malignant neoplasms, stated or presumed to be secondary, of specified sites
199 Malignant neoplasms, without specification of site
200-208 Malignant neoplasms, stated or presumed to be primary, of lymphatic and hematopoietic tissue
210-229 Benign neoplasms
230-234 Carcinoma in situ
235-238 Neoplasms of uncertain behavior [see Note, at beginning of section 235-238]
239 Neoplasms of unspecified nature
2. Functional activity
All neoplasms are classified in this chapter, whether or not functionally active. An additional code from Chapter 3 may be used to identify such functional activity associated with any neoplasm, e.g.:
catecholamine-producing malignant pheochromocytoma of adrenal:
code 194.0, additional code 255.6
basophil adenoma of pituitary with Cushing's syndrome:
code 227.3, additional code 255.0
3. Morphology [Histology]
For those wishing to identify the histological type of neoplasms, a comprehensive coded nomenclature, which comprises the morphology rubrics of the ICD-Oncology, is given after the E-code chapter.
4. Malignant neoplasms overlapping site boundaries
Categories 140-195 are for the classification of primary malignant neoplasms according to their point of origin. A malignant neoplasm that overlaps two or more subcategories within a three-digit rubric and whose point of origin cannot be determined should be classified to the subcategory .8 "Other." For example, "carcinoma involving tip and ventral surface of tongue" should be assigned to 141.8. On the other hand, "carcinoma of tip of tongue, extending to involve the ventral surface" should be coded to 141.2, as the point of origin, the tip, is known. Three subcategories (149.8, 159.8, 165.8) have been provided for malignant neoplasms that overlap the boundaries of three-digit rubrics within certain systems. Overlapping malignant neoplasms that cannot be classified as indicated above should be assigned to the appropriate subdivision of category 195 (Malignant neoplasm of other and ill-defined sites).
MALIGNANT NEOPLASM OF LIP, ORAL CAVITY, AND PHARYNX (140-149)
Excludes: carcinoma in situ (230.0)
Excludes: skin of lip (173.0)
140.0 Upper lip, vermilion border
Upper lip:
NOS
external
lipstick area
140.1 Lower lip, vermilion border
Lower lip:
NOS
external
lipstick area
Upper lip:
buccal aspect
frenulum
mucosa
oral aspect
Lower lip:
buccal aspect
frenulum
mucosa
oral aspect
140.5 Lip, unspecified, inner aspect
Lip, not specified whether upper or lower:
buccal aspect
frenulum
mucosa
oral aspect
Labial commissure
Malignant neoplasm of contiguous or overlapping sites of lip whose point of origin cannot be determined
140.9 Lip, unspecified, vermilion border
Lip, not specified as upper or lower:
NOS
external
lipstick area
Dorsal surface of base of tongue
Fixed part of tongue NOS
141.1 Dorsal surface of tongue
Anterior two-thirds of tongue, dorsal surface
Dorsal tongue NOS
Midline of tongue
Excludes: dorsal surface of base of tongue (141.0)
141.2 Tip and lateral border of tongue
141.3 Ventral surface of tongue
Anterior two-thirds of tongue, ventral surface
Frenulum linguae
141.4 Anterior two-thirds of tongue, part unspecified
Mobile part of tongue NOS
Border of tongue at junction of fixed and mobile parts at insertion of anterior tonsillar pillar
Malignant neoplasm of contiguous or overlapping sites of tongue whose point of origin cannot be determined
Tongue NOS
Includes: salivary ducts
Excludes: malignant neoplasm of minor salivary glands:
NOS (145.9)
buccal mucosa (145.0)
soft palate (145.3)
tongue (141.0-141.9)
tonsil, palatine (146.0)
Submaxillary gland
142.8 Other major salivary glands
Malignant neoplasm of contiguous or overlapping sites of salivary glands and ducts whose point of origin cannot be determined
142.9 Salivary gland, unspecified
Salivary gland (major) NOS
Includes: alveolar (ridge) mucosa
gingiva (alveolar) (marginal)
interdental papillae
Excludes: malignant odontogenic neoplasms (170.0-170.1)
Malignant neoplasm of contiguous or overlapping sites of gum whose point of origin cannot be determined
Anterior to the premolar-canine junction
144.8 Other sites of floor of mouth
Malignant neoplasm of contiguous or overlapping sites of floor of mouth whose point of origin cannot be determined
144.9 Floor of mouth, part unspecified
Excludes: mucosa of lips (140.0-140.9)
Buccal mucosa
Cheek, inner aspect
Buccal sulcus (upper) (lower)
Labial sulcus (upper) (lower)
Excludes: nasopharyngeal [posterior] [superior] surface of soft palate (147.3)
Junction of hard and soft palate
Roof of mouth
145.8 Other specified parts of mouth
Malignant neoplasm of contiguous or overlapping sites of mouth whose point of origin cannot be determined
Buccal cavity NOS
Minor salivary gland, unspecified site
Oral cavity NOS
Tonsil:
NOS
faucial
palatine
Excludes: lingual tonsil (141.6)
pharyngeal tonsil (147.1)
146.2 Tonsillar pillars (anterior) (posterior)
Faucial pillar
Glossopalatine fold
Palatoglossal arch
Palatopharyngeal arch
Anterior and medial surface of the pharyngoepiglottic fold
146.4 Anterior aspect of epiglottis
Epiglottis, free border [margin]
Glossoepiglottic fold(s)
Excludes: epiglottis:
NOS (161.1)
suprahyoid portion (161.1)
Junction of the free margin of the epiglottis, the aryepiglottic fold, and the pharyngoepiglottic fold
146.6 Lateral wall of oropharynx
146.7 Posterior wall of oropharynx
146.8 Other specified sites of oropharynx
Branchial cleft
Malignant neoplasm of contiguous or overlapping sites of oropharynx whose point of origin cannot be determined
Roof of nasopharynx
Adenoid
Pharyngeal tonsil
Fossa of Rosenmüller
Opening of auditory tube
Pharyngeal recess
Floor of nasopharynx
Nasopharyngeal [posterior] [superior] surface of soft palate
Posterior margin of nasal septum and choanae
147.8 Other specified sites of nasopharynx
Malignant neoplasm of contiguous or overlapping sites of nasopharynx whose point of origin cannot be determined
147.9 Nasopharynx, unspecified
Nasopharyngeal wall NOS
Pyriform fossa
148.2 Aryepiglottic fold, hypopharyngeal aspect
Aryepiglottic fold or interarytenoid fold:
NOS
marginal zone
Excludes: aryepiglottic fold or interarytenoid fold, laryngeal aspect (161.1)
148.3 Posterior hypopharyngeal wall
148.8 Other specified sites of hypopharynx
Malignant neoplasm of contiguous or overlapping sites of hypopharynx whose point of origin cannot be determined
148.9 Hypopharynx, unspecified
Hypopharyngeal wall NOS
Hypopharynx NOS
Malignant neoplasms of lip, oral cavity, and pharynx whose point of origin cannot be assigned to any one of the categories 140-148
Excludes: "book leaf" neoplasm [ventral surface of tongue and floor of mouth] (145.8)
MALIGNANT NEOPLASM OF DIGESTIVE ORGANS AND PERITONEUM (150-159)
Excludes: carcinoma in situ (230.1-230.9)
Excludes: adenocarcinoma (151.0)
cardio-esophageal junction (151.0)
150.3 Upper third of esophagus
Proximal third of esophagus
150.4 Middle third of esophagus
150.5 Lower third of esophagus
Distal third of esophagus
Excludes: adenocarcinoma (151.0)
cardio-esophageal junction (151.0)
Malignant neoplasm of contiguous or overlapping sites of esophagus whose point of origin cannot be determined
Cardiac orifice
Cardio-esophageal junction
Excludes: squamous cell carcinoma (150.2, 150.5)
Prepylorus
Pyloric canal
Antrum of stomach NOS
151.5 Lesser curvature, unspecified
Lesser curvature, not classifiable to 151.1-151.4
151.6 Greater curvature, unspecified
Greater curvature, not classifiable to 151.0-151.4
151.8 Other specified sites of stomach
Anterior wall, not classifiable to 151.0-151.4
Posterior wall, not classifiable to 151.0-151.4
Malignant neoplasm of contiguous or overlapping sites of stomach whose point of origin cannot be determined
Carcinoma ventriculi
Gastric cancer
Excludes: ileocecal valve (153.4)
152.8 Other specified sites of small intestine
Duodenojejunal junction
Malignant neoplasm of contiguous or overlapping sites of small intestine whose point of origin cannot be determined
152.9 Small intestine, unspecified
Left colon
Sigmoid (flexure)
Excludes: rectosigmoid junction (154.0)
Ileocecal valve
Right colon
153.8 Other specified sites of large intestine
Malignant neoplasm of contiguous or overlapping sites of colon whose point of origin cannot be determined
Excludes: ileocecal valve (153.4)
rectosigmoid junction (154.0)
Large intestine NOS
Colon with rectum
Rectosigmoid (colon)
Rectal ampulla
Anal sphincter
Excludes: skin of anus (172.5, 173.5)
Excludes: anus:
margin (172.5, 173.5)
skin (172.5, 173.5)
perianal skin (172.5, 173.5)
Anorectum
Cloacogenic zone
Malignant neoplasm of contiguous or overlapping sites of rectum, rectosigmoid junction, and anus whose point of origin cannot be determined
Carcinoma:
liver, specified as primary
hepatocellular
liver cell
Hepatoblastoma
Canaliculi biliferi
Interlobular:
bile ducts
biliary canals
Intrahepatic:
biliary passages
canaliculi
gall duct
Excludes: hepatic duct (156.1)
155.2 Liver, not specified as primary or secondary
Biliary duct or passage
NOS
Common bile duct
Cystic duct
Hepatic duct
Sphincter of Oddi
156.8 Other specified sites of gallbladder and extrahepatic bile ducts
Malignant neoplasm of contiguous or overlapping sites of gallbladder and extrahepatic bile ducts whose point of origin cannot be determined
156.9 Biliary tract, part unspecified
Malignant neoplasm involving both intrahepatic and extrahepatic bile ducts
Duct of:
Santorini
Wirsung
Islets of Langerhans, any part of pancreas
Use additional code to identify any functional activity
157.8 Other specified sites of pancreas
Ectopic pancreatic tissue
Malignant neoplasm of contiguous or overlapping sites of pancreas whose point of origin cannot be determined
157.9 Pancreas, part unspecified
Periadrenal tissue
Perinephric tissue
Perirenal tissue
Retrocecal tissue
158.8 Specified parts of peritoneum
Cul-de-sac (of Douglas)
Mesentery
Mesocolon
Omentum
Peritoneum:
parietal
pelvic
Rectouterine pouch
Malignant neoplasm of contiguous or overlapping sites of retroperitoneum and peritoneum whose point of origin cannot be determined
159.0 Intestinal tract, part unspecified
Intestine NOS
159.1 Spleen, not elsewhere classified
Angiosarcoma of spleen
Fibrosarcoma of spleen
Excludes: Hodgkin's disease (201.0-201.9)
lymphosarcoma (200.1)
reticulosarcoma (200.0)
159.8 Other sites of digestive system and intra-abdominal organs
Malignant neoplasm of digestive organs and peritoneum whose point of origin cannot be assigned to any one of the categories 150-158
Excludes: anus and rectum (154.8)
cardio-esophageal junction (151.0)
colon and rectum (154.0)
Alimentary canal or tract NOS
Gastrointestinal tract NOS
Excludes: abdominal NOS (195.2)
intra-abdominal NOS (195.2)
MALIGNANT NEOPLASM OF RESPIRATORY AND INTRATHORACIC ORGANS (160-165)
Excludes: carcinoma in situ (231.0-231.9)
Cartilage of nose
Conchae, nasal
Internal nose
Septum of nose
Vestibule of nose
Excludes: nasal bone (170.0)
nose NOS (195.0)
olfactory bulb (192.0)
posterior margin of septum and choanae (147.3)
skin of nose (172.3, 173.3)
turbinates (170.0)
160.1 Auditory tube, middle ear, and mastoid air cells
Antrum tympanicum
Eustachian tube
Tympanic cavity
Excludes: auditory canal (external) (172.2, 173.2)
bone of ear (meatus) (170.0)
cartilage of ear (171.0)
ear (external) (skin) (172.2, 173.2)
Antrum (Highmore) (maxillary)
Malignant neoplasm of contiguous or overlapping sites of nasal cavities, middle ear, and accessory sinuses whose point of origin cannot be determined
160.9 Accessory sinus, unspecified
Intrinsic larynx
Laryngeal commissure (anterior) (posterior)
True vocal cord
Vocal cord NOS
Aryepiglottic fold or interarytenoid fold, laryngeal aspect
Epiglottis (suprahyoid portion) NOS
Extrinsic larynx
False vocal cords
Posterior (laryngeal) surface of epiglottis
Ventricular bands
Excludes: anterior aspect of epiglottis (146.4)
aryepiglottic fold or interarytenoid fold:
NOS (148.2)
hypopharyngeal aspect (148.2)
marginal zone (148.2)
Cartilage:
arytenoid
cricoid
cuneiform
thyroid
161.8 Other specified sites of larynx
Malignant neoplasm of contiguous or overlapping sites of larynx whose point of origin cannot be determined
Cartilage of trachea
Mucosa of trachea
Carina
Hilus of lung
162.3 Upper lobe, bronchus or lung
162.4 Middle lobe, bronchus or lung
162.5 Lower lobe, bronchus or lung
162.8 Other parts of bronchus or lung
Malignant neoplasm of contiguous or overlapping sites of bronchus or lung whose point of origin cannot be determined
162.9 Bronchus and lung, unspecified
163.8 Other specified sites of pleura
Malignant neoplasm of contiguous or overlapping sites of pleura whose point of origin cannot be determined
Endocardium
Epicardium
Myocardium
Pericardium
Excludes: great vessels (171.4)
Malignant neoplasm of contiguous or overlapping sites of thymus, heart, and mediastinum whose point of origin cannot be determined
164.9 Mediastinum, part unspecified
165 Malignant neoplasm of other and ill-defined sites within the respiratory system and intrathoracic organs
165.0 Upper respiratory tract, part unspecified
Malignant neoplasm of respiratory and intrathoracic organs whose point of origin cannot be assigned to any one of the categories 160-164
165.9 Ill-defined sites within the respiratory system
Respiratory tract NOS
Excludes: intrathoracic NOS (195.1)
thoracic NOS (195.1)
MALIGNANT NEOPLASM OF BONE, CONNECTIVE TISSUE, SKIN, AND BREAST (170-176)
Excludes: carcinoma in situ:
breast (233.0)
skin (232.0-232.9)
Includes: cartilage (articular) (joint)
periosteum
Excludes: bone marrow NOS (202.9)
cartilage:
ear (171.0)
eyelid (171.0)
larynx (161.3)
nose (160.0)
synovia (171.0-171.9)
170.0 Bones of skull and face, except mandible
Bone:
ethmoid
frontal
malar
nasal
occipital
orbital
parietal
sphenoid
temporal
zygomatic
Maxilla (superior)
Turbinate
Upper jaw bone
Vomer
Excludes: carcinoma, any type except intraosseous or odontogenic:
maxilla, maxillary (sinus) (160.2)
upper jaw bone (143.0)
jaw bone (lower) (170.1)
Inferior maxilla
Jaw bone NOS
Lower jaw bone
Excludes: carcinoma, any type except intraosseous or odontogenic:
jaw bone NOS (143.9)
lower (143.1)
upper jaw bone (170.0)
170.2 Vertebral column, excluding sacrum and coccyx
Spinal column
Spine
Vertebra
Excludes: sacrum and coccyx (170.6)
170.3 Ribs, sternum, and clavicle
Costal cartilage
Costovertebral joint
Xiphoid process
170.4 Scapula and long bones of upper limb
Acromion
Bones NOS of upper limb
Humerus
Radius
Ulna
170.5 Short bones of upper limb
Carpal
Cuneiform, wrist
Metacarpal
Navicular, of hand
Phalanges of hand
Pisiform
Scaphoid (of hand)
Semilunar or lunate
Trapezium
Trapezoid
Unciform
170.6 Pelvic bones, sacrum, and coccyx
Coccygeal vertebra
Ilium
Ischium
Pubic bone
Sacral vertebra
170.7 Long bones of lower limb
Bones NOS of lower limb
Femur
Fibula
Tibia
170.8 Short bones of lower limb
Astragalus [talus]
Calcaneus
Cuboid
Cuneiform, ankle
Metatarsal
Navicular (of ankle)
Patella
Phalanges of foot
Tarsal
170.9 Bone and articular cartilage, site unspecified
Includes: blood vessel
bursa
fascia
fat
ligament, except uterine
muscle
peripheral, sympathetic, and parasympathetic nerves and ganglia
synovia
tendon (sheath)
Excludes: cartilage (of):
articular (170.0-170.9)
larynx (161.3)
nose (160.0)
connective tissue:
breast (174.0-175.9)
internal organscode to malignant neoplasm of the site [e.g., leiomyosarcoma of stomach, 151.9]
heart (164.1)
uterine ligament (183.4)
Cartilage of:
ear
eyelid
171.2 Upper limb, including shoulder
Arm
Finger
Forearm
Hand
171.3 Lower limb, including hip
Foot
Leg
Popliteal space
Thigh
Toe
Axilla
Diaphragm
Great vessels
Excludes: heart (164.1)
mediastinum (164.2-164.9)
thymus (164.0)
Abdominal wall
Hypochondrium
Excludes: peritoneum (158.8)
retroperitoneum (158.0)
Buttock
Groin
Inguinal region
Perineum
Excludes: pelvic peritoneum (158.8)
retroperitoneum (158.0)
uterine ligament, any (183.3-183.5)
Back NOS
Flank NOS
171.8 Other specified sites of connective and other soft tissue
Malignant neoplasm of contiguous or overlapping sites of connective tissue whose point of origin cannot be determined
171.9 Connective and other soft tissue, site unspecified
Includes: melanocarcinoma
melanoma (skin) NOS
Excludes: skin of genital organs (184.0-184.9, 187.1-187.9)
sites other than skincode to malignant neoplasm of the site
Excludes: vermilion border of lip (140.0-140.1, 140.9)
172.1 Eyelid, including canthus
172.2 Ear and external auditory canal
Auricle (ear)
Auricular canal, external
External [acoustic] meatus
Pinna
172.3 Other and unspecified parts of face
Cheek (external)
Chin
Eyebrow
Forehead
Nose, external
Temple
Axilla
Breast
Buttock
Groin
Perianal skin
Perineum
Umbilicus
Excludes: anal canal (154.2)
anus NOS (154.3)
scrotum (187.7)
172.6 Upper limb, including shoulder
Arm
Finger
Forearm
Hand
172.7 Lower limb, including hip
Ankle
Foot
Heel
Knee
Leg
Popliteal area
Thigh
Toe
172.8 Other specified sites of skin
Malignant melanoma of contiguous or overlapping sites of skin whose point of origin cannot be determined
172.9 Melanoma of skin, site unspecified
Includes: malignant neoplasm of:
sebaceous glands
sudoriferous, sudoriparous glands
sweat glands
Excludes: Kaposi's sarcoma (176.0-176.9)
malignant melanoma of skin (172.0-172.9)
skin of genital organs (184.0-184.9, 187.1-187.9)
Excludes: vermilion border of lip (140.0-140.1, 140.9)
173.1 Eyelid, including canthus
Excludes: cartilage of eyelid (171.0)
173.2 Skin of ear and external auditory canal
Auricle (ear)
Auricular canal, external
External meatus
Pinna
Excludes: cartilage of ear (171.0)
173.3 Skin of other and unspecified parts of face
Cheek, external
Chin
Eyebrow
Forehead
Nose, external
Temple
173.5 Skin of trunk, except scrotum
Axillary fold
Perianal skin
Skin of:
abdominal wall
anus
back
breast
buttock
chest wall
groin
perineum
Umbilicus
Excludes: anal canal (154.2)
anus NOS (154.3)
skin of scrotum (187.7)
173.6 Skin of upper limb, including shoulder
Arm
Finger
Forearm
Hand
173.7 Skin of lower limb, including hip
Ankle
Foot
Heel
Knee
Leg
Popliteal area
Thigh
Toe
173.8 Other specified sites of skin
Malignant neoplasm of contiguous or overlapping sites of skin whose point of origin cannot be determined
Includes: breast (female)
connective tissue
soft parts
Paget's disease of:
breast
nipple
Excludes: skin of breast (172.5, 173.5)
174.8 Other specified sites of female breast
Ectopic sites
Inner breast
Lower breast
Midline of breast
Outer breast
Upper breast
Malignant neoplasm of contiguous or overlapping sites of breast whose point of origin cannot be determined
174.9 Breast (female), unspecified
Excludes: skin of breast (172.5, 173.5)
175.9 Other and unspecified sites of male breast
Ectopic breast tissue, male
Blood vessel
Connective tissue
Fascia
Ligament
Lymphatic(s) NEC
Muscle
Excludes: lymph glands and nodes (176.5)
Oral cavity NEC
Viscera NOS
MALIGNANT NEOPLASM OF GENITOURINARY ORGANS (179-189)
Excludes: carcinoma in situ (233.1-233.9)
Includes: invasive malignancy [carcinoma]
Excludes: carcinoma in situ (233.1)
Cervical canal NOS
Endocervical canal
Endocervical gland
180.8 Other specified sites of cervix
Cervical stump
Squamocolumnar junction of cervix
Malignant neoplasm of contiguous or overlapping sites of cervix uteri whose point of origin cannot be determined
180.9 Cervix uteri, unspecified
Choriocarcinoma NOS
Chorioepithelioma NOS
Excludes: chorioadenoma (destruens) (236.1)
hydatidiform mole (630)
malignant (236.1)
invasive mole (236.1)
male choriocarcinoma NOS (186.0-186.9)
Excludes: carcinoma in situ (233.2)
182.0 Corpus uteri, except isthmus
Cornu
Endometrium
Fundus
Myometrium
Lower uterine segment
182.8 Other specified sites of body of uterus
Malignant neoplasm of contiguous or overlapping sites of body of uterus whose point of origin cannot be determined
Excludes: uterus NOS (179)
Excludes: Douglas' cul-de-sac (158.8)
Use additional code to identify any functional activity
Oviduct
Uterine tube
Mesovarium
Parovarian region
Uterine ligament NOS
Uterosacral ligament
183.8 Other specified sites of uterine adnexa
Tubo-ovarian
Utero-ovarian
Malignant neoplasm of contiguous or overlapping sites of ovary and other uterine adnexa whose point of origin cannot be determined
183.9 Uterine adnexa, unspecified
Excludes: carcinoma in situ (233.3)
Gartner's duct
Vaginal vault
Greater vestibular [Bartholin's] gland
External female genitalia NOS
Pudendum
184.8 Other specified sites of female genital organs
Malignant neoplasm of contiguous or overlapping sites of female genital organs whose point of origin cannot be determined
184.9 Female genital organ, site unspecified
Female genitourinary tract NOS
Excludes: seminal vesicles (187.8)
Use additional code to identify any functional activity
Ectopic testis
Retained testis
186.9 Other and unspecified testis
Testis:
NOS
descended
scrotal
Foreskin
Corpus cavernosum
Skin of penis NOS
Vas deferens
Skin of scrotum
187.8 Other specified sites of male genital organs
Seminal vesicle
Tunica vaginalis
Malignant neoplasm of contiguous or overlapping sites of penis and other male genital organs whose point of origin cannot be determined
187.9 Male genital organ, site unspecified
Male genital organ or tract NOS
Excludes: carcinoma in situ (233.7)
188.0 Trigone of urinary bladder
188.2 Lateral wall of urinary bladder
188.3 Anterior wall of urinary bladder
188.4 Posterior wall of urinary bladder
Internal urethral orifice
188.8 Other specified sites of bladder
Malignant neoplasm of contiguous or overlapping sites of bladder whose point of origin cannot be determined
188.9 Bladder, part unspecified
Bladder wall NOS
Kidney NOS
Kidney parenchyma
Renal calyces
Ureteropelvic junction
Excludes: ureteric orifice of bladder (188.6)
Excludes: urethral orifice of bladder (188.5)
189.8 Other specified sites of urinary organs
Malignant neoplasm of contiguous or overlapping sites of kidney and other urinary organs whose point of origin cannot be determined
189.9 Urinary organ, site unspecified
Urinary system NOS
MALIGNANT NEOPLASM OF OTHER AND UNSPECIFIED SITES (190-199)
Excludes: carcinoma in situ (234.0-234.9)
Excludes: carcinoma in situ (234.0)
eyelid (skin) (172.1, 173.1)
cartilage (171.0)
optic nerve (192.0)
orbital bone (170.0)
190.0 Eyeball, except conjunctiva, cornea, retina, and choroid
Ciliary body
Crystalline lens
Iris
Sclera
Uveal tract
Connective tissue of orbit
Extraocular muscle
Retrobulbar
Excludes: bone of orbit (170.0)
Lacrimal sac
Nasolacrimal duct
190.8 Other specified sites of eye
Malignant neoplasm of contiguous or overlapping sites of eye whose point of origin cannot be determined
Excludes: cranial nerves (192.0)
retrobulbar area (190.1)
191.0 Cerebrum, except lobes and ventricles
Basal ganglia
Cerebral cortex
Corpus striatum
Globus pallidus
Hypothalamus
Thalamus
Hippocampus
Uncus
Choroid plexus
Floor of ventricle
Cerebellopontine angle
Cerebral peduncle
Medulla oblongata
Midbrain
Pons
Corpus callosum
Tapetum
Malignant neoplasm of contiguous or overlapping sites of brain whose point of origin cannot be determined
Cranial fossa NOS
Excludes: peripheral, sympathetic, and parasympathetic nerves and ganglia (171.0-171.9)
Olfactory bulb
Dura (mater)
Falx (cerebelli) (cerebri)
Meninges NOS
Tentorium
Cauda equina
192.8 Other specified sites of nervous system
Malignant neoplasm of contiguous or overlapping sites of other parts of nervous system whose point of origin cannot be determined
192.9 Nervous system, part unspecified
Nervous system (central) NOS
Excludes: meninges NOS (192.1)
Sipple's syndrome
Thyroglossal duct
Use additional code to identify any functional activity
Use additional code to identify any functional activity
Excludes: islets of Langerhans (157.4)
ovary (183.0)
testis (186.0-186.9)
thymus (164.0)
Adrenal cortex
Adrenal medulla
Suprarenal gland
194.3 Pituitary gland and craniopharyngeal duct
Craniobuccal pouch
Hypophysis
Rathke's pouch
Sella turcica
194.6 Aortic body and other paraganglia
Coccygeal body
Glomus jugulare
Para-aortic body
Pluriglandular involvement NOS
Note: If the sites of multiple involvements are known, they should be coded separately.
194.9 Endocrine gland, site unspecified
Includes: malignant neoplasms of contiguous sites, not elsewhere classified, whose point of origin cannot be determined
Excludes: malignant neoplasm:
lymphatic and hematopoietic tissue (200.0-208.9)
secondary sites (196.0-198.8)
unspecified site (199.0-199.1)
Cheek NOS
Jaw NOS
Nose NOS
Supraclavicular region NOS
Axilla
Chest (wall) NOS
Intrathoracic NOS
Intra-abdominal NOS
Groin
Inguinal region NOS
Presacral region
Sacrococcygeal region
Sites overlapping systems within pelvis, as:
rectovaginal (septum)
rectovesical (septum)
Back NOS
Flank NOS
Trunk NOS
Excludes: any malignant neoplasm of lymph nodes, specified as primary (200.0-202.9)
Hodgkin's disease (201.0-201.9)
lymphosarcoma (200.1)
reticulosarcoma (200.0)
other forms of lymphoma (202.0-202.9)
196.0 Lymph nodes of head, face, and neck
Cervical
Cervicofacial
Scalene
Supraclavicular
196.1 Intrathoracic lymph nodes
Bronchopulmonary
Intercostal
Mediastinal
Tracheobronchial
196.2 Intra-abdominal lymph nodes
Intestinal
Mesenteric
Retroperitoneal
196.3 Lymph nodes of axilla and upper limb
Brachial
Epitrochlear
Infraclavicular
Pectoral
196.5 Lymph nodes of inguinal region and lower limb
Femoral
Groin
Popliteal
Tibial
Hypogastric
Iliac
Obturator
Parametrial
196.8 Lymph nodes of multiple sites
Lymph nodes NOS
Excludes: lymph node metastasis (196.0-196.9)
Bronchus
197.3 Other respiratory organs
Trachea
197.4 Small intestine, including duodenum
197.5 Large intestine and rectum
197.6 Retroperitoneum and peritoneum
197.7 Liver, specified as secondary
197.8 Other digestive organs and spleen
Excludes: lymph node metastasis (196.0-196.9)
Skin of breast
198.4 Other parts of nervous system
Meninges (cerebral) (spinal)
Suprarenal gland
Excludes: skin of breast (198.2)
Excludes: retroperitoneal lymph nodes (196.2)
Carcinomatosis unspecified site (primary) (secondary)
Generalized:
cancer unspecified site (primary) (secondary)
malignancy unspecified site (primary) (secondary)
Multiple cancer unspecified site (primary) (secondary)
Cancer unspecified site (primary) (secondary)
Carcinoma unspecified site (primary) (secondary)
Malignancy unspecified site (primary) (secondary)
MALIGNANT NEOPLASM OF LYMPHATIC AND HEMATOPOIETIC TISSUE (200-208)
Excludes: secondary neoplasm of:
bone marrow (198.5)
spleen (197.8)
secondary and unspecified neoplasm of lymph nodes (196.0-196.9)
**NOTE** The following fifth-digit subclassification is for use with categories 200-202:
0 unspecified site, extranodal and solid organ sites
1 lymph nodes of head, face, and neck
2 intrathoracic lymph nodes
3 intra-abdominal lymph nodes
4 lymph nodes of axilla and upper limb
5 lymph nodes of inguinal region and lower limb
6 intrapelvic lymph nodes
7 spleen
8 lymph nodes of multiple sites
Requires fifth digit. See note before section 200 for codes and definitions.
Lymphoma (malignant):
histiocytic (diffuse):
nodular
pleomorphic cell type
reticulum cell type
Reticulum cell sarcoma:
NOS
pleomorphic cell type
Lymphoblastoma (diffuse)
Lymphoma (malignant):
lymphoblastic (diffuse)
lymphocytic (cell type) (diffuse)
lymphosarcoma type
Lymphosarcoma:
NOS
diffuse NOS
lymphoblastic (diffuse)
lymphocytic (diffuse)
prolymphocytic
Excludes: lymphosarcoma:
follicular or nodular (202.0)
mixed cell type (200.8)
lymphosarcoma cell leukemia (207.8)
200.2 Burkitt's tumor or lymphoma
Malignant lymphoma, Burkitt's type
Lymphoma (malignant):
lymphoplasmacytoid type
mixed lymphocytic-histiocytic (diffuse)
Lymphosarcoma, mixed cell type (diffuse)
Reticulolymphosarcoma (diffuse)
Requires fifth digit. See note before section 200 for codes and definitions.
201.4 Lymphocytic-histiocytic predominance
Hodgkin's disease, nodular sclerosis:
NOS
cellular phase
Hodgkin's disease, lymphocytic depletion:
NOS
diffuse fibrosis
reticular type
201.9 Hodgkin's disease, unspecified
Hodgkin's:
disease NOS
lymphoma NOS
Malignant:
lymphogranuloma
lymphogranulomatosis
Requires fifth digit. See note before section 200 for codes and definitions.
Brill-Symmers disease
Lymphoma:
follicular (giant)
lymphocytic, nodular
Lymphosarcoma:
follicular (giant)
nodular
Reticulosarcoma, follicular or nodular
Histiocytic medullary reticulosis
Malignant:
reticuloendotheliosis
reticulosis
202.4 Leukemic reticuloendotheliosis
Hairy-cell leukemia
Acute:
differentiated progressive histiocytosis
histiocytosis X (progressive)
infantile reticuloendotheliosis
reticulosis of infancy
Excludes: Hand-Schüller-Christian disease (277.89)
histiocytosis (acute) (chronic) (277.89)
histiocytosis X (chronic) (277.89)
202.6 Malignant mast cell tumors
Malignant:
mastocytoma
mastocytosis
Mast cell sarcoma
Systemic tissue mast cell disease
Excludes: mast cell leukemia (207.8)
Lymphoma (malignant):
NOS
diffuse
Excludes: benign lymphoma (229.0)
202.9 Other and unspecified malignant neoplasms of lymphoid and histiocytic tissue
Follicular dendritic cell sarcoma
Interdigitating dendritic cell sarcoma
Langerhans cell sarcoma
Malignant neoplasm of bone marrow NOS
**NOTE** The following fifth-digit subclassification is for use with category 203:
0 without mention of remission
1 in remission
Kahler's disease
Myelomatosis
Excludes: solitary myeloma (238.6)
Plasmacytic leukemia
203.8 Other immunoproliferative neoplasms
Includes: leukemia:
lymphatic
lymphoblastic
lymphocytic
lymphogenous
**NOTE** The following fifth-digit subclassification is for use with category 204:
0 without mention of remission
1 in remission
Excludes: acute exacerbation of chronic lymphoid leukemia (204.1)
Aleukemic leukemia:
lymphatic
lymphocytic
lymphoid
204.9 Unspecified lymphoid leukemia
Includes: leukemia:
granulocytic
myeloblastic
myelocytic
myelogenous
myelomonocytic
myelosclerotic
myelosis
**NOTE** The following fifth-digit subclassification is for use with category 205:
0 without mention of remission
1 in remission
Acute promyelocytic leukemia
Excludes: acute exacerbation of chronic myeloid leukemia (205.1)
Eosinophilic leukemia
Neutrophilic leukemia
Chloroma
Granulocytic sarcoma
Aleukemic leukemia:
granulocytic
myelogenous
myeloid
Aleukemic myelosis
205.9 Unspecified myeloid leukemia
Includes: leukemia:
histiocytic
monoblastic
monocytoid
**NOTE** The following fifth-digit subclassification is for use with category 206:
0 without mention of remission
1 in remission
Excludes: acute exacerbation of chronic monocytic leukemia (206.1)
206.8 Other monocytic leukemia
Aleukemic:
monocytic leukemia
monocytoid leukemia
206.9 Unspecified monocytic leukemia
Excludes: leukemic reticuloendotheliosis (202.4)
plasma cell leukemia (203.1)
**NOTE** The following fifth-digit subclassification is for use with category 207:
0 without mention of remission
1 in remission
207.0 Acute erythremia and erythroleukemia
Acute erythremic myelosis
Di Guglielmo's disease
Erythremic myelosis
Heilmeyer-Schöner disease
Megakaryocytic myelosis
Thrombocytic leukemia
207.8 Other specified leukemia
Lymphosarcoma cell leukemia
**NOTE** The following fifth-digit subclassification is for use with category 208:
0 without mention of remission
1 in remission
Acute leukemia NOS
Blast cell leukemia
Stem cell leukemia
Excludes: acute exacerbation of chronic unspecified leukemia (208.1)
Chronic leukemia NOS
Subacute leukemia NOS
208.8 Other leukemia of unspecified cell type
Leukemia NOS
BENIGN NEOPLASMS (210-229)
Excludes: cyst (of):
jaw (526.0-526.2, 526.89)
oral soft tissue (528.4)
radicular (522.8)
Frenulum labii
Lip (inner aspect) (mucosa) (vermilion border)
Excludes: labial commissure (210.4)
skin of lip (216.0)
Lingual tonsil
Gland:
parotid
sublingual
submandibular
Excludes: benign neoplasms of minor salivary glands:
NOS (210.4)
buccal mucosa (210.4)
lips (210.0)
palate (hard) (soft) (210.4)
tongue (210.1)
tonsil, palatine (210.5)
210.4 Other and unspecified parts of mouth
Gingiva
Gum (upper) (lower)
Labial commissure
Oral cavity NOS
Oral mucosa
Palate (hard) (soft)
Uvula
Excludes: benign odontogenic neoplasms of bone (213.0-213.1)
developmental odontogenic cysts (526.0)
mucosa of lips (210.0)
nasopharyngeal [posterior] [superior] surface of soft palate (210.7)
Tonsil (faucial) (palatine)
Excludes: lingual tonsil (210.1)
pharyngeal tonsil (210.7)
tonsillar:
fossa (210.6)
pillars (210.6)
210.6 Other parts of oropharynx
Branchial cleft or vestiges
Epiglottis, anterior aspect
Fauces NOS
Mesopharynx NOS
Tonsillar:
fossa
pillars
Vallecula
Excludes: epiglottis:
NOS (212.1)
suprahyoid portion (212.1)
Adenoid tissue
Lymphadenoid tissue
Pharyngeal tonsil
Posterior nasal septum
Arytenoid fold
Laryngopharynx
Postcricoid region
Pyriform fossa
Throat NOS
Body of stomach
Cardia of stomach
Fundus of stomach
Cardiac orifice
Pylorus
211.2 Duodenum, jejunum, and ileum
Small intestine NOS
Excludes: ampulla of Vater (211.5)
ileocecal valve (211.3)
Appendix
Cecum
Ileocecal valve
Large intestine NOS
Excludes: rectosigmoid junction (211.4)
Anal canal or sphincter
Anus NOS
Rectosigmoid junction
Excludes: anus:
margin (216.5)
skin (216.5)
perianal skin (216.5)
211.5 Liver and biliary passages
Ampulla of Vater
Common bile duct
Cystic duct
Gallbladder
Hepatic duct
Sphincter of Oddi
211.6 Pancreas, except islets of Langerhans
Islet cell tumor
Use additional code to identify any functional activity
211.8 Retroperitoneum and peritoneum
Mesentery
Mesocolon
Omentum
Retroperitoneal tissue
211.9 Other and unspecified site
Alimentary tract NOS
Digestive system NOS
Gastrointestinal tract NOS
Intestinal tract NOS
Intestine NOS
Spleen, not elsewhere classified
212.0 Nasal cavities, middle ear, and accessory sinuses
Cartilage of nose
Eustachian tube
Nares
Septum of nose
Sinus:
ethmoidal
frontal
maxillary
sphenoidal
Excludes: auditory canal (external) (216.2)
bone of:
ear (213.0)
nose [turbinates] (213.0)
cartilage of ear (215.0)
ear (external) (skin) (216.2)
nose NOS (229.8)
skin (216.3)
olfactory bulb (225.1)
polyp of:
accessory sinus (471.8)
ear (385.30-385.35)
nasal cavity (471.0)
posterior margin of septum and choanae (210.7)
Cartilage:
arytenoid
cricoid
cuneiform
thyroid
Epiglottis (suprahyoid portion) NOS
Glottis
Vocal cords (false) (true)
Excludes: epiglottis, anterior aspect (210.6)
polyp of vocal cord or larynx (478.4)
Carina
Hilus of lung
Excludes: great vessels (215.4)
Respiratory organ NOS
Upper respiratory tract NOS
Excludes: intrathoracic NOS (229.8)
thoracic NOS (229.8)
Includes: cartilage (articular) (joint)
periosteum
Excludes: cartilage of:
ear (215.0)
eyelid (215.0)
larynx (212.1)
nose (212.0)
exostosis NOS (726.91)
synovia (215.0-215.9)
Excludes: lower jaw bone (213.1)
213.2 Vertebral column, excluding sacrum and coccyx
213.3 Ribs, sternum, and clavicle
213.4 Scapula and long bones of upper limb
213.5 Short bones of upper limb
213.6 Pelvic bones, sacrum, and coccyx
213.7 Long bones of lower limb
213.8 Short bones of lower limb
213.9 Bone and articular cartilage, site unspecified
Includes: angiolipoma
fibrolipoma
hibernoma
lipoma (fetal) (infiltrating) (intramuscular)
myelolipoma
myxolipoma
214.0 Skin and subcutaneous tissue of face
214.1 Other skin and subcutaneous tissue
214.9 Lipoma, unspecified site
Includes: blood vessel
bursa
fascia
ligament
muscle
peripheral, sympathetic, and parasympathetic nerves and ganglia
synovia
tendon (sheath)
Excludes: cartilage:
articular (213.0-213.9)
larynx (212.1)
nose (212.0)
connective tissue of:
breast (217)
internal organ, except lipoma and hemangiomacode to benign neoplasm of the site
lipoma (214.0-214.9)
215.2 Upper limb, including shoulder
215.3 Lower limb, including hip
Excludes: heart (212.7)
mediastinum (212.5)
thymus (212.6)
Abdominal wall
Hypochondrium
Buttock
Groin
Inguinal region
Perineum
Excludes: uterine:
leiomyoma (218.0-218.9)
ligament, any (221.0)
Back NOS
Flank NOS
Includes: blue nevus
dermatofibroma
hydrocystoma
pigmented nevus
syringoadenoma
syringoma
Excludes: skin of genital organs (221.0-222.9)
Excludes: vermilion border of lip (210.0)
216.1 Eyelid, including canthus
Excludes: cartilage of eyelid (215.0)
216.2 Ear and external auditory canal
Auricle (ear)
Auricular canal, external
External meatus
Pinna
Excludes: cartilage of ear (215.0)
216.3 Skin of other and unspecified parts of face
Cheek, external
Eyebrow
Nose, external
Temple
216.5 Skin of trunk, except scrotum
Axillary fold
Perianal skin
Skin of:
abdominal wall
anus
back
breast
buttock
chest wall
groin
perineum
Umbilicus
Excludes: anal canal (211.4)
anus NOS (211.4)
skin of scrotum (222.4)
216.6 Skin of upper limb, including shoulder
216.7 Skin of lower limb, including hip
216.8 Other specified sites of skin
Breast (male) (female)
connective tissue
glandular tissue
soft parts
Excludes: adenofibrosis (610.2)
benign cyst of breast (610.0)
fibrocystic disease (610.1)
skin of breast (216.5)
Includes: fibroid (bleeding) (uterine)
uterine:
fibromyoma
myoma
218.0 Submucous leiomyoma of uterus
218.1 Intramural leiomyoma of uterus
Interstitial leiomyoma of uterus
218.2 Subserous leiomyoma of uterus
Subperitoneal leiomyoma of uterus
218.9 Leiomyoma of uterus, unspecified
Endometrium
Fundus
Myometrium
219.8 Other specified parts of uterus
219.9 Uterus, part unspecified
Use additional code to identify any functional activity (256.0-256.1)
Excludes: cyst:
corpus albicans (620.2)
corpus luteum (620.1)
endometrial (617.1)
follicular (atretic) (620.0)
graafian follicle (620.0)
ovarian NOS (620.2)
retention (620.2)
Includes: adenomatous polyp
benign teratoma
Excludes: cyst:
epoophoron (752.11)
fimbrial (752.11)
Gartner's duct (752.11)
parovarian (752.11)
221.0 Fallopian tube and uterine ligaments
Oviduct
Parametrium
Uterine ligament (broad) (round) (uterosacral)
Uterine tube
Clitoris
External female genitalia NOS
Greater vestibular [Bartholin's] gland
Labia (majora) (minora)
Pudendum
Excludes: Bartholin's (duct) (gland) cyst (616.2)
221.8 Other specified sites of female genital organs
221.9 Female genital organ, site unspecified
Female genitourinary tract NOS
Use additional code to identify any functional activity
Corpus cavernosum
Glans penis
Prepuce
Excludes: adenomatous hyperplasia of prostate (600.20-600.21)
prostatic:
adenoma (600.20-600.21)
enlargement (600.00-600.01)
hypertrophy (600.00-600.01)
Skin of scrotum
222.8 Other specified sites of male genital organs
Seminal vesicle
Spermatic cord
222.9 Male genital organ, site unspecified
Male genitourinary tract NOS
Kidney NOS
Excludes: renal:
calyces (223.1)
pelvis (223.1)
Excludes: ureteric orifice of bladder (223.3)
223.8 Other specified sites of urinary organs
Excludes: urethral orifice of bladder (223.3)
Paraurethral glands
223.9 Urinary organ, site unspecified
Urinary system NOS
Excludes: cartilage of eyelid (215.0)
eyelid (skin) (216.1)
optic nerve (225.1)
orbital bone (213.0)
224.0 Eyeball, except conjunctiva, cornea, retina, and choroid
Ciliary body
Iris
Sclera
Uveal tract
Excludes: bone of orbit (213.0)
Excludes: hemangioma of retina (228.03)
Lacrimal sac
Nasolacrimal duct
224.8 Other specified parts of eye
Excludes: hemangioma (228.02)
neurofibromatosis (237.7)
peripheral, sympathetic, and parasympathetic nerves and ganglia (215.0-215.9)
retrobulbar (224.1)
Meninges NOS
Meningioma (cerebral)
Cauda equina
Spinal meningioma
225.8 Other specified sites of nervous system
225.9 Nervous system, part unspecified
Nervous system (central) NOS
Excludes: meninges NOS (225.2)
Use additional code to identify any functional activity
Use additional code to identify any functional activity
Excludes: ovary (220)
pancreas (211.6)
testis (222.0)
Suprarenal gland
227.3 Pituitary gland and craniopharyngeal duct (pouch)
Craniobuccal pouch
Hypophysis
Rathke's pouch
Sella turcica
Pineal body
227.6 Aortic body and other paraganglia
Coccygeal body
Glomus jugulare
Para-aortic body
227.9 Endocrine gland, site unspecified
Includes: angioma (benign) (cavernous) (congenital) NOS
cavernous nevus
glomus tumor
hemangioma (benign) (congenital)
Excludes: benign neoplasm of spleen, except hemangioma and lymphangioma (211.9)
glomus jugulare (227.6)
nevus:
NOS (216.0-216.9)
blue or pigmented (216.0-216.9)
vascular (757.32)
228.01 Of skin and subcutaneous tissue
228.02 Of intracranial structures
228.04 Of intra-abdominal structures
Peritoneum
Retroperitoneal tissue
Systemic angiomatosis
Congenital lymphangioma
Lymphatic nevus
Excludes: lymphangioma (228.1)
Intrathoracic NOS
Thoracic NOS
CARCINOMA IN SITU (230-234)
Includes: Bowen's disease
erythroplasia
Queyrat's erythroplasia
Excludes: leukoplakiasee Alphabetic Index
230.0 Lip, oral cavity, and pharynx
Gingiva
Hypopharynx
Mouth [any part]
Nasopharynx
Oropharynx
Salivary gland or duct
Tongue
Excludes: aryepiglottic fold or interarytenoid fold, laryngeal aspect (231.0)
epiglottis:
NOS (231.0)
suprahyoid portion (231.0)
skin of lip (232.0)
Body of stomach
Cardia of stomach
Fundus of stomach
Cardiac orifice
Pylorus
Appendix
Cecum
Ileocecal valve
Large intestine NOS
Excludes: rectosigmoid junction (230.4)
Rectosigmoid junction
Anal sphincter
Excludes: anus:
margin (232.5)
skin (232.5)
perianal skin (232.5)
230.7 Other and unspecified parts of intestine
Duodenum
Ileum
Jejunum
Small intestine NOS
Excludes: ampulla of Vater (230.8)
230.8 Liver and biliary system
Ampulla of Vater
Common bile duct
Cystic duct
Gallbladder
Hepatic duct
Sphincter of Oddi
230.9 Other and unspecified digestive organs
Digestive organ NOS
Gastrointestinal tract NOS
Pancreas
Spleen
Cartilage:
arytenoid
cricoid
cuneiform
thyroid
Epiglottis:
NOS
posterior surface
suprahyoid portion
Vocal cords (false) (true)
Excludes: aryepiglottic fold or interarytenoid fold:
NOS (230.0)
hypopharyngeal aspect (230.0)
marginal zone (230.0)
Carina
Hilus of lung
231.8 Other specified parts of respiratory system
Accessory sinuses
Middle ear
Nasal cavities
Pleura
Excludes: ear (external) (skin) (232.2)
nose NOS (234.8)
skin (232.3)
231.9 Respiratory system, part unspecified
Respiratory organ NOS
Includes: pigment cells
Excludes: vermilion border of lip (230.0)
232.1 Eyelid, including canthus
232.2 Ear and external auditory canal
232.3 Skin of other and unspecified parts of face
232.5 Skin of trunk, except scrotum
Anus, margin
Axillary fold
Perianal skin
Skin of:
abdominal wall
anus
back
breast
buttock
chest wall
groin
perineum
Umbilicus
Excludes: anal canal (230.5)
anus NOS (230.6)
skin of genital organs (233.3, 233.5-233.6)
232.6 Skin of upper limb, including shoulder
232.7 Skin of lower limb, including hip
232.8 Other specified sites of skin
Excludes: Paget's disease (174.0-174.9)
skin of breast (232.5)
Cervical intraepithelial neoplasia III [CIN III]
Severe dysplasia of cervix
Excludes: cervical intraepithelial neoplasia II [CIN II] (622.12)
cytologic evidence of malignancy without histologic confirmation (795.04)
high grade squamous intraepithelial lesion (HGSIL) (795.04)
moderate dysplasia of cervix (622.12)
233.2 Other and unspecified parts of uterus
233.3 Other and unspecified female genital organs
233.6 Other and unspecified male genital organs
233.9 Other and unspecified urinary organs
Excludes: cartilage of eyelid (234.8)
eyelid (skin) (232.1)
optic nerve (234.8)
orbital bone (234.8)
Endocrine gland [any]
Carcinoma in situ NOS
NEOPLASMS OF UNCERTAIN BEHAVIOR (235-238)
Note: Categories 235-238 classify by site certain histo-morphologically well-defined neoplasms, the subsequent behavior of which cannot be predicted from the present appearance.
Gland:
parotid
sublingual
submandibular
Excludes: minor salivary glands (235.1)
235.1 Lip, oral cavity, and pharynx
Gingiva
Hypopharynx
Minor salivary glands
Mouth
Nasopharynx
Oropharynx
Tongue
Excludes: aryepiglottic fold or interarytenoid fold, laryngeal aspect (235.6)
epiglottis:
NOS (235.6)
suprahyoid portion (235.6)
skin of lip (238.2)
235.2 Stomach, intestines, and rectum
235.3 Liver and biliary passages
Ampulla of Vater
Bile ducts [any]
Gallbladder
Liver
235.4 Retroperitoneum and peritoneum
235.5 Other and unspecified digestive organs
Anal:
canal
sphincter
Anus NOS
Esophagus
Pancreas
Spleen
Excludes: anus:
margin (238.2)
skin (238.2)
perianal skin (238.2)
Excludes: aryepiglottic fold or interarytenoid fold:
NOS (235.1)
hypopharyngeal aspect (235.1)
marginal zone (235.1)
235.7 Trachea, bronchus, and lung
235.8 Pleura, thymus, and mediastinum
235.9 Other and unspecified respiratory organs
Accessory sinuses
Middle ear
Nasal cavities
Respiratory organ NOS
Excludes: ear (external) (skin) (238.2)
nose (238.8)
skin (238.2)
Chorioadenoma (destruens)
Invasive mole
Malignant hydatid(iform) mole
Use additional code to identify any functional activity
236.3 Other and unspecified female genital organs
Use additional code to identify any functional activity
236.6 Other and unspecified male genital organs
236.9 Other and unspecified urinary organs
236.90 Urinary organ, unspecified
237.0 Pituitary gland and craniopharyngeal duct
Use additional code to identify any functional activity
Suprarenal gland
Use additional code to identify any functional activity
Aortic body
Carotid body
Coccygeal body
Glomus jugulare
237.4 Other and unspecified endocrine glands
Parathyroid gland
Thyroid gland
Meninges:
NOS
cerebral
spinal
von Recklinghausen's disease
237.70 Neurofibromatosis, unspecified
237.71 Neurofibromatosis, type 1 [von Recklinghausen's disease]
237.72 Neurofibromatosis, type 2 [acoustic neurofibromatosis]
237.9 Other and unspecified parts of nervous system
Cranial nerves
Excludes: peripheral, sympathetic, and parasympathetic nerves and ganglia (238.1)
238.0 Bone and articular cartilage
Excludes: cartilage:
ear (238.1)
eyelid (238.1)
larynx (235.6)
nose (235.9)
synovia (238.1)
238.1 Connective and other soft tissue
Peripheral, sympathetic, and parasympathetic nerves and ganglia
Excludes: cartilage (of):
articular (238.0)
larynx (235.6)
nose (235.9)
connective tissue of breast (238.3)
Excludes: anus NOS (235.5)
skin of genital organs (236.3, 236.6)
vermilion border of lip (235.1)
Excludes: skin of breast (238.2)
238.5 Histiocytic and mast cells
Mast cell tumor NOS
Mastocytoma NOS
Plasmacytoma NOS
Solitary myeloma
238.7 Other lymphatic and hematopoietic tissues
Disease:
lymphoproliferative (chronic) NOS
myeloproliferative (chronic) NOS
Idiopathic thrombocythemia
Megakaryocytic myelosclerosis
Myelodysplastic syndrome
Myelosclerosis with myeloid metaplasia
Panmyelosis (acute)
Refractory anemia
Excludes: myelofibrosis (289.89)
myelosclerosis NOS (289.89)
myelosis:
NOS (205.9)
megakaryocytic (207.2)
Eye
Heart
Excludes: eyelid (skin) (238.2)
cartilage (238.1)
NEOPLASMS OF UNSPECIFIED NATURE (239)
Note: Category 239 classifies by site neoplasms of unspecified morphology and behavior. The term "mass," unless otherwise stated, is not to be regarded as a neoplastic growth.
Includes: "growth" NOS
neoplasm NOS
new growth NOS
tumor NOS
Excludes: anus:
margin (239.2)
skin (239.2)
perianal skin (239.2)
239.2 Bone, soft tissue, and skin
Excludes: anal canal (239.0)
anus NOS (239.0)
bone marrow (202.9)
cartilage:
larynx (239.1)
nose (239.1)
connective tissue of breast (239.3)
skin of genital organs (239.5)
vermilion border of lip (239.0)
Excludes: skin of breast (239.2)
239.5 Other genitourinary organs
Excludes: cerebral meninges (239.7)
cranial nerves (239.7)
239.7 Endocrine glands and other parts of nervous system
Excludes: peripheral, sympathetic, and parasympathetic nerves and ganglia (239.2)
Excludes: eyelid (skin) (239.2)
cartilage (239.2)
great vessels (239.2)
optic nerve (239.7)
3. ENDOCRINE, NUTRITIONAL AND METABOLIC DISEASES, AND IMMUNITY DISORDERS (240-279)
Excludes: endocrine and metabolic disturbances specific
to the fetus and newborn (775.0-775.9)
Note: All neoplasms, whether functionally active or not, are classified in Chapter 2. Codes in Chapter 3 (i.e., 242.8, 246.0, 251-253, 255-259) may be used to identify such functional activity associated with any neoplasm, or by ectopic endocrine tissue.
DISORDERS OF THYROID GLAND (240-246)
240.0 Goiter, specified as simple
Any condition classifiable to 240.9, specified as simple
Enlargement of thyroid
Goiter or struma:
NOS
diffuse colloid
endemic
hyperplastic
nontoxic (diffuse)
parenchymatous
sporadic
Excludes: congenital (dyshormonogenic) goiter (246.1)
Excludes: adenoma of thyroid (226)
cystadenoma of thyroid (226)
241.0 Nontoxic uninodular goiter
Thyroid nodule
Uninodular goiter (nontoxic)
241.1 Nontoxic multinodular goiter
Multinodular goiter (nontoxic)
241.9 Unspecified nontoxic nodular goiter
Adenomatous goiter
Nodular goiter (nontoxic) NOS
Struma nodosa (simplex)
Excludes: neonatal thyrotoxicosis (775.3)
**NOTE** The following fifth-digit subclassification is for use with category 242:
0 without mention of thyrotoxic crisis or storm
1 with mention of thyrotoxic crisis or storm
Basedow's disease
Exophthalmic or toxic goiter NOS
Graves' disease
Primary thyroid hyperplasia
Thyroid nodule, toxic or with hyperthyroidism
Uninodular goiter, toxic or with hyperthyroidism
242.2 Toxic multinodular goiter
Secondary thyroid hyperplasia
242.3 Toxic nodular goiter, unspecified
Adenomatous goiter, toxic or with hyperthyroidism
Nodular goiter, toxic or with hyperthyroidism
Struma nodosa, toxic or with hyperthyroidism
Any condition classifiable to 241.9 specified as toxic or with hyperthyroidism
242.4 Thyrotoxicosis from ectopic thyroid nodule
242.8 Thyrotoxicosis of other specified origin
Overproduction of thyroid-stimulating hormone [TSH]
Thyrotoxicosis:
factitia from ingestion of excessive thyroid material
Use additional E code to identify cause, if drug-induced
242.9 Thyrotoxicosis without mention of goiter or other cause
Hyperthyroidism NOS
Thyrotoxicosis NOS
Congenital thyroid insufficiency
Cretinism (athyrotic) (endemic)
Use additional code to identify associated mental retardation
Excludes: congenital (dyshormonogenic) goiter (246.1)
Includes: athyroidism (acquired)
hypothyroidism (acquired)
myxedema (adult) (juvenile)
thyroid (gland) insufficiency (acquired)
244.0 Postsurgical hypothyroidism
244.1 Other postablative hypothyroidism
Hypothyroidism following therapy, such as irradiation
Hypothyroidism resulting from administration or ingestion of iodide
Use additional E to identify drug
244.3 Other iatrogenic hypothyroidism
Hypothyroidism resulting from:
P-aminosalicylic acid [PAS]
Phenylbutazone
Resorcinol
Iatrogenic hypothyroidism NOS
Use additional E to identify drug
244.8 Other specified acquired hypothyroidism
Secondary hypothyroidism NEC
244.9 Unspecified hypothyroidism
Hypothyroidism, primary or NOS
Myxedema, primary or NOS
Abscess of thyroid
Thyroiditis:
nonsuppurative, acute
pyogenic
suppurative
Use additional code to identify organism
Thyroiditis:
de Quervain's
giant cell
granulomatous
viral
245.2 Chronic lymphocytic thyroiditis
Hashimoto's disease
Struma lymphomatosa
Thyroiditis:
autoimmune
lymphocytic (chronic)
245.3 Chronic fibrous thyroiditis
Struma fibrosa
Thyroiditis:
invasive (fibrous)
ligneous
Riedel's
Use additional E to identify cause
245.8 Other and unspecified chronic thyroiditis
Chronic thyroiditis:
NOS
nonspecific
245.9 Thyroiditis, unspecified
Thyroiditis NOS
246.0 Disorders of thyrocalcitonin secretion
Hypersecretion of calcitonin or thyrocalcitonin
Congenital (dyshormonogenic) goiter
Goiter due to enzyme defect in synthesis of thyroid hormone
Goitrous cretinism (sporadic)
Excludes: cystadenoma of thyroid (226)
246.3 Hemorrhage and infarction of thyroid
246.8 Other specified disorders of thyroid
Abnormality of thyroid-binding globulin
Atrophy of thyroid
Hyper-TBG-nemia
Hypo-TBG-nemia
246.9 Unspecified disorder of thyroid
DISEASES OF OTHER ENDOCRINE GLANDS (250-259)
Excludes: gestational diabetes (648.8)
hyperglycemia NOS (790.6)
neonatal diabetes mellitus (775.1)
nonclinical diabetes (790.29)
**NOTE** The following fifth-digit subclassification is for use with category 250:
0 type II or unspecified type, not stated as uncontrolled
Fifth-digit 0 is for use for type II patients, even if the patient requires insulin
Use additional code, if applicable, for associated long-term (current) insulin use V58.67
1 type I [juvenile type], not stated as uncontrolled
2 type II or unspecified type, uncontrolled
Use additional code, if applicable, for associated long-term (current) insulin use V58.67
Fifth-digit 2 is for use for type II, adult-onset, diabetic patients, even if the patient requires insulin
3 type I [juvenile type], uncontrolled
250.0 Diabetes mellitus without mention of complication
Diabetes mellitus without mention of complication or manifestation classifiable to 250.1-250.9
Diabetes (mellitus) NOS
250.1 Diabetes with ketoacidosis
Diabetic:
acidosis without mention of coma
ketosis without mention of coma
250.2 Diabetes with hyperosmolarity
Hyperosmolar (nonketotic) coma
250.3 Diabetes with other coma
Diabetic coma (with ketoacidosis)
Diabetic hypoglycemic coma
Insulin coma NOS
Excludes: diabetes with hyperosmolar coma (250.2)
250.4 Diabetes with renal manifestations
Use additional code to identify manifestation, as:
chronic kidney disease (585.1-585.9)
diabetic:
nephropathy NOS (583.81)
nephrosis (581.81)
intercapillary glomerulosclerosis (581.81)
Kimmelstiel-Wilson syndrome (581.81)
250.5 Diabetes with ophthalmic manifestations
Use additional code to identify manifestation, as:
diabetic:
blindness (369.00-369.9)
cataract (366.41)
glaucoma (365.44)
macular edema (362.07)
retinal edema (362.07)
retinopathy (362.01-362.07)
250.6 Diabetes with neurological manifestations
Use additional code to identify manifestation, as:
diabetic:
amyotrophy (358.1)
gastroparalysis (536.3)
gastroparesis (536.3)
mononeuropathy (354.0-355.9)
neurogenic arthropathy (713.5)
peripheral autonomic neuropathy (337.1)
polyneuropathy (357.2)
250.7 Diabetes with peripheral circulatory disorders
Use additional code to identify manifestation, as:
diabetic:
gangrene (785.4)
peripheral angiopathy (443.81)
250.8 Diabetes with other specified manifestations
Diabetic hypoglycemia
Hypoglycemic shock
Use additional code to identify manifestation, as:
any associated ulceration (707.10-707.9)
diabetic bone changes (731.8)
Use additional E code to identify cause, if drug-induced
250.9 Diabetes with unspecified complication
Iatrogenic hyperinsulinism
Non-diabetic insulin coma
Use additional E code to identify cause, if drug-induced
Excludes: hypoglycemic coma in diabetes mellitus (250.3)
251.1 Other specified hypoglycemia
Hyperinsulinism:
NOS
ectopic
functional
Hyperplasia of pancreatic islet beta cells NOS
Excludes: hypoglycemia in diabetes mellitus (250.8)
hypoglycemia in infant of diabetic mother (775.0)
hypoglycemic coma (251.0)
neonatal hypoglycemia (775.6)
Use additional E code to identify cause, if drug-induced
251.2 Hypoglycemia, unspecified
Hypoglycemia:
NOS
reactive
spontaneous
Excludes: hypoglycemia:
with coma (251.0)
in diabetes mellitus (250.8)
leucine-induced (270.3)
251.3 Postsurgical hypoinsulinemia
Hypoinsulinemia following complete or partial pancreatectomy
Postpancreatectomy hyperglycemia
251.4 Abnormality of secretion of glucagon
Hyperplasia of pancreatic islet alpha cells with glucagon excess
251.5 Abnormality of secretion of gastrin
Hyperplasia of pancreatic alpha cells with gastrin excess
Zollinger-Ellison syndrome
251.8 Other specified disorders of pancreatic internal secretion
251.9 Unspecified disorder of pancreatic internal secretion
Islet cell hyperplasia NOS
Excludes: ectopic hyperparathyroidism (259.3)
252.00 Hyperparathyroidism, unspecified
252.01 Primary hyperparathyroidism
Hyperplasia of parathyroid
252.02 Secondary hyperparathyroidism, non-renal
Excludes: secondary hyperparathyroidism (of renal origin) (588.81)
252.08 Other hyperparathyroidism
Tertiary hyperparathyroidism
Parathyroiditis (autoimmune)
Tetany:
parathyroid
parathyroprival
Excludes: pseudohypoparathyroidism (275.49)
pseudopseudohypoparathyroidism (275.49)
tetany NOS (781.7)
transitory neonatal hypoparathyroidism (775.4)
252.8 Other specified disorders of parathyroid gland
Cyst of parathyroid gland
Hemorrhage of parathyroid gland
252.9 Unspecified disorder of parathyroid gland
Includes: the listed conditions whether the disorder is in the pituitary or the hypothalamus
Excludes: Cushing's syndrome (255.0)
253.0 Acromegaly and gigantism
Overproduction of growth hormone
253.1 Other and unspecified anterior pituitary hyperfunction
Forbes-Albright syndrome
Excludes: overproduction of:
ACTH (255.3)
thyroid-stimulating hormone [TSH] (242.8)
Cachexia, pituitary
Necrosis of pituitary (postpartum)
Pituitary insufficiency NOS
Sheehan's syndrome
Simmonds' disease
Excludes: iatrogenic hypopituitarism (253.7)
Isolated deficiency of (human) growth hormone [HGH]
Lorain-Levi dwarfism
253.4 Other anterior pituitary disorders
Isolated or partial deficiency of an anterior pituitary hormone, other than growth hormone
Prolactin deficiency
Vasopressin deficiency
Excludes: nephrogenic diabetes insipidus (588.1)
253.6 Other disorders of neurohypophysis
Syndrome of inappropriate secretion of antidiuretic hormone [ADH]
Excludes: ectopic antidiuretic hormone secretion (259.3)
253.7 Iatrogenic pituitary disorders
Hypopituitarism:
hormone-induced
hypophysectomy-induced
postablative
radiotherapy-induced
Use additional E code to identify cause
253.8 Other disorders of the pituitary and other syndromes of diencephalohypophyseal origin
Abscess of pituitary
Adiposogenital dystrophy
Cyst of Rathke's pouch
Fröhlich's syndrome
Excludes: craniopharyngioma (237.0)
Dyspituitarism
Excludes: aplasia or dysplasia with immunodeficiency (279.2)
hypoplasia with immunodeficiency (279.2)
myasthenia gravis (358.00-358.01)
254.0 Persistent hyperplasia of thymus
Hypertrophy of thymus
254.8 Other specified diseases of thymus gland
Atrophy of thymus
Cyst of thymus
Excludes: thymoma (212.6)
254.9 Unspecified disease of thymus gland
Includes: the listed conditions whether the basic disorder is in the adrenals or is pituitary-induced
Adrenal hyperplasia due to excess ACTH
Cushing's syndrome:
NOS
iatrogenic
idiopathic
pituitary-dependent
Ectopic ACTH syndrome
Iatrogenic syndrome of excess cortisol
Overproduction of cortisol
Use additional E code to identify cause, if drug-induced
Excludes: congenital adrenal hyperplasia (255.2)
Aldosteronism NOS
Hyperaldosteronism, unspecified
Excludes: Conn's syndrome (255.12)
255.11 Glucocorticoid-remediable aldosteronism
Familial aldosteronism type I
Excludes: Conn's syndrome (255.12)
255.14 Other secondary aldosteronism
Adrenogenital syndromes, virilizing or feminizing, whether acquired or associated with congenital adrenal hyperplasia consequent on inborn enzyme defects in hormone synthesis
Achard-Thiers syndrome
Congenital adrenal hyperplasia
Female adrenal pseudohermaphroditism
Male:
macrogenitosomia praecox
sexual precocity with adrenal hyperplasia
Virilization (female) (suprarenal)
Excludes: adrenal hyperplasia due to excess ACTH (255.0)
isosexual virilization (256.4)
255.3 Other corticoadrenal overactivity
Acquired benign adrenal androgenic overactivity
Overproduction of ACTH
255.4 Corticoadrenal insufficiency
Addisonian crisis
Addison's disease NOS
Adrenal:
atrophy (autoimmune)
calcification
crisis
hemorrhage
infarction
insufficiency NOS
Excludes: tuberculous Addison's disease (017.6)
255.5 Other adrenal hypofunction
Adrenal medullary insufficiency
Excludes: Waterhouse-Friderichsen syndrome (meningococcal) (036.3)
255.6 Medulloadrenal hyperfunction
Catecholamine secretion by pheochromocytoma
255.8 Other specified disorders of adrenal glands
Abnormality of cortisol-binding globulin
255.9 Unspecified disorder of adrenal glands
256.1 Other ovarian hyperfunction
Hypersecretion of ovarian androgens
256.2 Postablative ovarian failure
Ovarian failure:
iatrogenic
postirradiation
postsurgical
Use additional code for states associated with artificial menopause (627.4)
Excludes: acquired absence of ovary (V45.77)
asymptomatic age-related (natural) postmenopausal status (V49.81)
Use additional code for states associated with natural menopause (627.2)
Excludes: asymptomatic age-related (natural) postmenopausal status (V49.81)
Delayed menarche
Ovarian hypofunction
Primary ovarian failure NOS
Isosexual virilization Stein-Leventhal syndrome
256.8 Other ovarian dysfunction
256.9 Unspecified ovarian dysfunction
257.0 Testicular hyperfunction
Hypersecretion of testicular hormones
257.1 Postablative testicular hypofunction
Testicular hypofunction:
iatrogenic
postirradiation
postsurgical
257.2 Other testicular hypofunction
Defective biosynthesis of testicular androgen
Eunuchoidism:
NOS
hypogonadotropic
Failure:
Leydig's cell, adult
seminiferous tubule, adult
Testicular hypogonadism
Excludes: azoospermia (606.0)
257.8 Other testicular dysfunction
Excludes: androgen insensitivity syndrome (259.5)
257.9 Unspecified testicular dysfunction
258.0 Polyglandular activity in multiple endocrine adenomatosis
Wermer's syndrome
258.1 Other combinations of endocrine dysfunction
Lloyd's syndrome
Schmidt's syndrome
258.8 Other specified polyglandular dysfunction
258.9 Polyglandular dysfunction, unspecified
259.0 Delay in sexual development and puberty, not elsewhere classified
Delayed puberty
259.1 Precocious sexual development and puberty, not elsewhere classified
Sexual precocity:
NOS
constitutional
cryptogenic
idiopathic
Hormone secretion by carcinoid tumors
259.3 Ectopic hormone secretion, not elsewhere classified
Ectopic:
antidiuretic hormone secretion [ADH]
hyperparathyroidism
Excludes: ectopic ACTH syndrome (255.0)
259.4 Dwarfism, not elsewhere classified
Dwarfism:
NOS
constitutional
Excludes: dwarfism:
achondroplastic (756.4)
intrauterine (759.7)
nutritional (263.2)
pituitary (253.3)
renal (588.0)
progeria (259.8)
259.5 Androgen insensitivity syndrome
Partial androgen insensitivity
Reifenstein syndrome
259.8 Other specified endocrine disorders
Pineal gland dysfunction
Progeria
Werner's syndrome
259.9 Unspecified endocrine disorder
Disturbance:
endocrine NOS
hormone NOS
Infantilism NOS
NUTRITIONAL DEFICIENCIES (260-269)
Excludes: deficiency anemias (280.0-281.9)
Nutritional edema with dyspigmentation of skin and hair
Nutritional atrophy
Severe calorie deficiency
Severe malnutrition NOS
Nutritional edema without mention of dyspigmentation of skin and hair
263.0 Malnutrition of moderate degree
263.1 Malnutrition of mild degree
263.2 Arrested development following protein-calorie malnutrition
Nutritional dwarfism
Physical retardation due to malnutrition
263.8 Other protein-calorie malnutrition
263.9 Unspecified protein-calorie malnutrition
Dystrophy due to malnutrition
Malnutrition (calorie) NOS
Excludes: nutritional deficiency NOS (269.9)
264.0 With conjunctival xerosis
264.1 With conjunctival xerosis and Bitot's spot
Bitot's spot in the young child
264.3 With corneal ulceration and xerosis
264.6 With xerophthalmic scars of cornea
264.7 Other ocular manifestations of vitamin A deficiency
Xerophthalmia due to vitamin A deficiency
264.8 Other manifestations of vitamin A deficiency
Follicular keratosis due to vitamin A deficiency
Xeroderma due to vitamin A deficiency
264.9 Unspecified vitamin A deficiency
Hypovitaminosis A NOS
265.1 Other and unspecified manifestations of thiamine deficiency
Other vitamin B1 deficiency states
Deficiency:
niacin (-tryptophan)
nicotinamide
nicotinic acid
vitamin PP
Pellagra (alcoholic)
Riboflavin [vitamin B2] deficiency
Deficiency:
pyridoxal
pyridoxamine
pyridoxine
Vitamin B6 deficiency syndrome
Excludes: vitamin B6-responsive sideroblastic anemia (285.0)
266.2 Other B-complex deficiencies
Deficiency:
cyanocobalamin
folic acid
vitamin B12
Excludes: combined system disease with anemia (281.0-281.1)
deficiency anemias (281.0-281.9)
subacute degeneration of spinal cord with anemia (281.0-281.1)
266.9 Unspecified vitamin B deficiency
Deficiency of vitamin C
Scurvy
Excludes: scorbutic anemia (281.8)
Excludes: vitamin D-resistant:
osteomalacia (275.3)
rickets (275.3)
Excludes: celiac rickets (579.0)
renal rickets (588.0)
Any condition specified as due to rickets and stated to be a late effect or sequela of rickets
Use additional code to identify the nature of late effect
268.2 Osteomalacia, unspecified
268.9 Unspecified vitamin D deficiency
Avitaminosis D
Excludes: deficiency of coagulation factor due to vitamin K deficiency (286.7)
vitamin K deficiency of newborn (776.0)
269.1 Deficiency of other vitamins
Deficiency:
vitamin E
vitamin P
269.2 Unspecified vitamin deficiency
Multiple vitamin deficiency NOS
269.3 Mineral deficiency, not elsewhere classified
Deficiency:
calcium, dietary
iodine
Excludes: deficiency:
calcium NOS (275.40)
potassium (276.8)
sodium (276.1)
269.8 Other nutritional deficiency
Excludes: adult failure to thrive (783.7)
failure to thrive in childhood (783.41)
feeding problems (783.3)
newborn (779.3)
269.9 Unspecified nutritional deficiency
OTHER METABOLIC AND IMMUNITY DISORDERS (270-279)
Use additional code to identify any associated mental retardation
Excludes: abnormal findings without manifest disease (790.0-796.9)
disorders of purine and pyrimidine metabolism (277.1-277.2)
gout (274.0-274.9)
270.0 Disturbances of amino-acid transport
Cystinosis
Cystinuria
Fanconi (-de Toni) (-Debré) syndrome
Glycinuria (renal)
Hartnup disease
Hyperphenylalaninemia
270.2 Other disturbances of aromatic amino-acid metabolism
Albinism
Alkaptonuria
Alkaptonuric ochronosis
Disturbances of metabolism of tyrosine and tryptophan
Homogentisic acid defects
Hydroxykynureninuria
Hypertyrosinemia
Indicanuria
Kynureninase defects
Oasthouse urine disease
Ochronosis
Tyrosinosis
Tyrosinuria
Waardenburg syndrome
Excludes: vitamin B6-deficiency syndrome (266.1)
270.3 Disturbances of branched-chain amino-acid metabolism
Disturbances of metabolism of leucine, isoleucine, and valine
Hypervalinemia
Intermittent branched-chain ketonuria
Leucine-induced hypoglycemia
Leucinosis
Maple syrup urine disease
270.4 Disturbances of sulphur-bearing amino-acid metabolism
Cystathioninemia
Cystathioninuria
Disturbances of metabolism of methionine, homocystine, and cystathionine
Homocystinuria
Hypermethioninemia
Methioninemia
270.5 Disturbances of histidine metabolism
Carnosinemia
Histidinemia
Hyperhistidinemia
Imidazole aminoaciduria
270.6 Disorders of urea cycle metabolism
Argininosuccinic aciduria
Citrullinemia
Disorders of metabolism of ornithine, citrulline, argininosuccinic acid, arginine, and ammonia
Hyperammonemia
Hyperornithinemia
270.7 Other disturbances of straight-chain amino-acid metabolism
Glucoglycinuria
Glycinemia (with methylmalonic acidemia)
Hyperglycinemia
Hyperlysinemia
Pipecolic acidemia
Saccharopinuria
Other disturbances of metabolism of glycine, threonine, serine, glutamine, and lysine
270.8 Other specified disorders of amino-acid metabolism
Alaninemia
Ethanolaminuria
Glycoprolinuria
Hydroxyprolinemia
Hyperprolinemia
Iminoacidopathy
Prolinemia
Prolinuria
Sarcosinemia
270.9 Unspecified disorder of amino-acid metabolism
Excludes: abnormality of secretion of glucagon (251.4)
diabetes mellitus (250.0-250.9)
hypoglycemia NOS (251.2)
mucopolysaccharidosis (277.5)
Amylopectinosis
Glucose-6-phosphatase deficiency
Glycogen storage disease
McArdle's disease
Pompe's disease
von Gierke's disease
Galactose-1-phosphate uridyl transferase deficiency
Galactosuria
271.2 Hereditary fructose intolerance
Essential benign fructosuria
Fructosemia
271.3 Intestinal disaccharidase deficiencies and disaccharide malabsorption
Intolerance or malabsorption (congenital) (of):
glucose-galactose
lactose
sucrose-isomaltose
Renal diabetes
271.8 Other specified disorders of carbohydrate transport and metabolism
Essential benign pentosuria
Fucosidosis
Glycolic aciduria
Hyperoxaluria (primary)
Mannosidosis
Oxalosis
Xylosuria
Xylulosuria
271.9 Unspecified disorder of carbohydrate transport and metabolism
Excludes: localized cerebral lipidoses (330.1)
272.0 Pure hypercholesterolemia
Familial hypercholesterolemia
Fredrickson Type IIa hyperlipoproteinemia
Hyperbetalipoproteinemia
Hyperlipidemia, Group A
Low-density-lipoid-type [LDL] hyperlipoproteinemia
Endogenous hyperglyceridemia
Fredrickson Type IV hyperlipoproteinemia
Hyperlipidemia, Group B
Hyperprebetalipoproteinemia
Hypertriglyceridemia, essential
Very-low-density-lipoid-type [VLDL] hyperlipoproteinemia
Broad- or floating-betalipoproteinemia
Fredrickson Type IIb or III hyperlipoproteinemia
Hypercholesterolemia with endogenous hyperglyceridemia
Hyperbetalipoproteinemia with prebetalipoproteinemia
Tubo-eruptive xanthoma
Xanthoma tuberosum
Bürger-Grütz syndrome
Fredrickson type I or V hyperlipoproteinemia
Hyperlipidemia, Group D
Mixed hyperglyceridemia
272.4 Other and unspecified hyperlipidemia
Alpha-lipoproteinemia
Combined hyperlipidemia
Hyperlipidemia NOS
Hyperlipoproteinemia NOS
272.5 Lipoprotein deficiencies
Abetalipoproteinemia
Bassen-Kornzweig syndrome
High-density lipoid deficiency
Hypoalphalipoproteinemia
Hypobetalipoproteinemia (familial)
Barraquer-Simons disease
Progressive lipodystrophy
Use additional E code to identify cause, if iatrogenic
Excludes: intestinal lipodystrophy (040.2)
Chemically induced lipidosis
Disease:
Anderson's
Fabry's
Gaucher's
I cell [mucolipidosis I]
lipoid storage NOS
Niemann-Pick
pseudo-Hurler's or mucolipidosis III
triglyceride storage, Type I or II
Wolman's or triglyceride storage, Type III
Mucolipidosis II
Primary familial xanthomatosis
Excludes: cerebral lipidoses (330.1)
Tay-Sachs disease (330.1)
272.8 Other disorders of lipoid metabolism
Hoffa's disease or liposynovitis prepatellaris
Launois-Bensaude's lipomatosis
Lipoid dermatoarthritis
272.9 Unspecified disorder of lipoid metabolism
Excludes: agammaglobulinemia and hypogammaglobulinemia (279.0-279.2)
coagulation defects (286.0-286.9)
hereditary hemolytic anemias (282.0-282.9)
273.0 Polyclonal hypergammaglobulinemia
Hypergammaglobulinemic purpura:
benign primary
Waldenström's
273.1 Monoclonal paraproteinemia
Benign monoclonal hypergammaglobulinemia [BMH]
Monoclonal gammopathy:
NOS
associated with lymphoplasmacytic dyscrasias
benign
Paraproteinemia:
benign (familial)
secondary to malignant or inflammatory disease
Cryoglobulinemic:
purpura
vasculitis
Mixed cryoglobulinemia
Macroglobulinemia (idiopathic) (primary)
Waldenström's macroglobulinemia
273.4 Alpha-1-antitrypsin deficiency
AAT deficiency
273.8 Other disorders of plasma protein metabolism
Abnormality of transport protein
Bisalbuminemia
273.9 Unspecified disorder of plasma protein metabolism
Excludes: lead gout (984.0-984.9)
274.10 Gouty nephropathy, unspecified
274.11 Uric acid nephrolithiasis
274.8 Gout with other specified manifestations
274.82 Gouty tophi of other sites
Gouty tophi of heart
Use additional code to identify manifestations, as:
gouty:
iritis (364.11)
neuritis (357.4)
Excludes: abnormal findings without manifest disease (790.0-796.9)
275.0 Disorders of iron metabolism
Bronzed diabetes
Hemochromatosis
Pigmentary cirrhosis (of liver)
Excludes: anemia:
iron deficiency (280.0-280.9)
sideroblastic (285.0)
275.1 Disorders of copper metabolism
Hepatolenticular degeneration
Wilson's disease
275.2 Disorders of magnesium metabolism
Hypermagnesemia
Hypomagnesemia
275.3 Disorders of phosphorus metabolism
Familial hypophosphatemia
Hypophosphatasia
Vitamin D-resistant:
osteomalacia
rickets
275.4 Disorders of calcium metabolism
Excludes: parathyroid disorders (252.00-252.9)
vitamin D deficiency (268.0-268.9)
275.40 Unspecified disorder of calcium metabolism
275.49 Other disorders of calcium metabolism
Nephrocalcinosis
Pseudohypoparathyroidism
Pseudopseudohypoparathyroidism
275.8 Other specified disorders of mineral metabolism
275.9 Unspecified disorder of mineral metabolism
Excludes: diabetes insipidus (253.5)
familial periodic paralysis (359.3)
276.0 Hyperosmolality and/or hypernatremia
Sodium [Na] excess
Sodium [Na] overload
276.1 Hyposmolality and/or hyponatremia
Sodium [Na] deficiency
Acidosis:
NOS
lactic
metabolic
respiratory
Excludes: diabetic acidosis (250.1)
Alkalosis:
NOS
metabolic
respiratory
276.4 Mixed acid-base balance disorder
Hypercapnia with mixed acid-base disorder
Excludes: hypovolemic shock:
postoperative (998.0)
traumatic (958.4)
276.50 Volume depletion, unspecified
Depletion of volume of plasma
Fluid retention
Excludes: ascites (789.5)
localized edema (782.3)
Hyperkalemia
Potassium [K]:
excess
intoxication
overload
Hypokalemia
Potassium [K] deficiency
276.9 Electrolyte and fluid disorders not elsewhere classified
Electrolyte imbalance
Hyperchloremia
Hypochloremia
Excludes: electrolyte imbalance:
associated with hyperemesis gravidarum (643.1)
complicating labor and delivery (669.0)
following abortion and ectopic or molar pregnancy (634-638 with .4, 639.4)
Fibrocystic disease of the pancreas
Mucoviscidosis
277.00 Without mention of meconium ileus
Cystic fibrosis NOS
Meconium:
ileus (of newborn)
obstruction of intestine in mucoviscidosis
277.02 With pulmonary manifestations
Cystic fibrosis with pulmonary exacerbation
Use additional code to identify any infectious organism present, such as:
pseudomonas (041.7)
277.03 With gastrointestinal manifestations
Excludes: with meconium ileus (277.01)
277.09 With other manifestations
277.1 Disorders of porphyrin metabolism
Hematoporphyria
Hematoporphyrinuria
Hereditary coproporphyria
Porphyria
Porphyrinuria
Protocoproporphyria
Protoporphyria
Pyrroloporphyria
277.2 Other disorders of purine and pyrimidine metabolism
Hypoxanthine-guanine-phosphoribosyltransferase deficiency [HG-PRT deficiency]
Lesch-Nyhan syndrome
Xanthinuria
Excludes: gout (274.0-274.9)
orotic aciduric anemia (281.4)
Amyloidosis:
NOS
inherited systemic
nephropathic
neuropathic (Portuguese) (Swiss)
secondary
Benign paroxysmal peritonitis
Familial Mediterranean fever
Hereditary cardiac amyloidosis
277.4 Disorders of bilirubin excretion
Hyperbilirubinemia:
congenital
constitutional
Syndrome:
Crigler-Najjar
Dubin-Johnson
Gilbert's
Rotor's
Excludes: hyperbilirubinemias specific to the perinatal period (774.0-774.7)
Gargoylism
Hunter's syndrome
Hurler's syndrome
Lipochondrodystrophy
Maroteaux-Lamy syndrome
Morquio-Brailsford disease
Osteochondrodystrophy
Sanfilippo's syndrome
Scheie's syndrome
277.6 Other deficiencies of circulating enzymes
Hereditary angioedema
Use additional code for associated manifestation, such as:
cardiovascular disease (414.00-414.07)
obesity (278.00-278.01)
277.8 Other specified disorders of metabolism
277.81 Primary carnitine deficiency
277.82 Carnitine deficiency due to inborn errors of metabolism
277.83 Iatrogenic carnitine deficiency
Carnitine deficiency due to:
Hemodialysis
Valproic acid therapy
277.84 Other secondary carnitine deficiency
277.85 Disorders of fatty acid oxidation
Carnitine palmitoyltransferase deficiencies (CPT1, CPT2)
Glutaric aciduria type II (type IIA, IIB, IIC)
Long chain 3-hydroxyacyl CoA dehydrogenase deficiency (LCHAD)
Long chain/very long chain acyl CoA dehydrogenase deficiency (LCAD, VLCAD)
Medium chain acyl CoA dehydrogenase deficiency (MCAD)
Short chain acyl CoA dehydrogenase deficiency (SCAD)
Excludes: primary carnitine deficiency (277.81)
Adrenomyeloneuropathy
Neonatal adrenoleukodystrophy
Rhizomelic chrondrodysplasia punctata
X-linked adrenoleukodystrophy
Zellweger syndrome
Excludes: infantile Refsum disease (356.3)
277.87 Disorders of mitochondrial metabolism
Kearns-Sayre syndrome
Mitochondrial Encephalopathy, Lactic Acidosis and Stroke-like episodes (MELAS syndrome)
Mitochondrial Neurogastrointestinal Encephalopathy syndrome (MNGIE)
Myoclonus with Epilepsy and with Ragged Red Fibers (MERRF syndrome)
Neuropathy, Ataxia and Retinitis Pigmentosa (NARP syndrome)
Use additional code for associated conditions
Excludes: disorders of pyruvate metabolism (271.8)
Leber's optic atrophy (377.16)
Leigh's subacute necrotizing encephalopathy (330.8)
Reye's syndrome (331.81)
277.89 Other specified disorders of metabolism
Hand-Schüller-Christian disease
Histiocytosis (acute) (chronic)
Histiocytosis X (chronic)
Excludes: histiocytosis:
acute differentiated progressive (202.5)
X, acute (progressive) (202.5)
277.9 Unspecified disorder of metabolism
Enzymopathy NOS
Excludes: hyperalimentation NOS (783.6)
poisoning by vitamins NOS (963.5)
polyphagia (783.6)
Excludes: adiposogenital dystrophy (253.8)
obesity of endocrine origin NOS (259.9)
Use additional code to identify Body Mass Index (BMI) if known (V85.21-V85.4)
Obesity NOS
Severe obesity
Fat pad
279.0 Deficiency of humoral immunity
279.00 Hypogammaglobulinemia, unspecified
Agammaglobulinemia NOS
279.01 Selective IgA immunodeficiency
279.02 Selective IgM immunodeficiency
279.03 Other selective immunoglobulin deficiencies
Selective deficiency of IgG
279.04 Congenital hypogammaglobulinemia
Agammaglobulinemia:
Bruton's type
X-linked
279.05 Immunodeficiency with increased IgM
Immunodeficiency with hyper-IgM:
autosomal recessive
X-linked
279.06 Common variable immunodeficiency
Dysgammaglobulinemia (acquired) (congenital) (primary)
Hypogammaglobulinemia:
acquired primary
congenital non-sex-linked
sporadic
Transient hypogammaglobulinemia of infancy
279.1 Deficiency of cell-mediated immunity
279.10 Immunodeficiency with predominant T-cell defect, unspecified
Pharyngeal pouch syndrome
Thymic hypoplasia
279.12 Wiskott-Aldrich syndrome
Cellular immunodeficiency with abnormal immunoglobulin deficiency
Excludes: ataxia-telangiectasia (334.8)
279.2 Combined immunity deficiency
Agammaglobulinemia:
autosomal recessive
Swiss-type
X-linked recessive
Severe combined immunodeficiency [SCID]
Thymic:
alymphoplasia
aplasia or dysplasia with immunodeficiency
Excludes: thymic hypoplasia (279.11)
279.3 Unspecified immunity deficiency
279.4 Autoimmune disease, not elsewhere classified
Autoimmune disease NOS
Excludes: transplant failure or rejection (996.80-996.89)
279.8 Other specified disorders involving the immune mechanism
Single complement [C1-C9] deficiency or dysfunction
279.9 Unspecified disorder of immune mechanism
4. DISEASES OF THE BLOOD AND BLOOD-FORMING ORGANS (280-289)
Includes: anemia:
asiderotic
hypochromic-microcytic
sideropenic
Excludes: familial microcytic anemia (282.49)
280.0 Secondary to blood loss (chronic)
Normocytic anemia due to blood loss
Excludes: acute posthemorrhagic anemia (285.1)
280.1 Secondary to inadequate dietary iron intake
280.8 Other specified iron deficiency anemias
Paterson-Kelly syndrome
Plummer-Vinson syndrome
Sideropenic dysphagia
280.9 Iron deficiency anemia, unspecified
Anemia:
achlorhydric
chlorotic
idiopathic hypochromic
iron [Fe] deficiency NOS
Anemia:
Addison's
Biermer's
congenital pernicious
Congenital intrinsic factor [Castle's] deficiency
Excludes: combined system disease without mention of anemia (266.2)
subacute degeneration of spinal cord without mention of anemia (266.2)
281.1 Other vitamin B12 deficiency anemia
Anemia:
vegan's
vitamin B12 deficiency (dietary)
due to selective vitamin B12 malabsorption with proteinuria
Syndrome:
Imerslund's
Imerslund-Gräsbeck
Excludes: combined system disease without mention of anemia (266.2)
subacute degeneration of spinal cord without mention of anemia (266.2)
281.2 Folate-deficiency anemia
Congenital folate malabsorption
Folate or folic acid deficiency anemia:
NOS
dietary
drug-induced
Goat's milk anemia
Nutritional megaloblastic anemia (of infancy)
Use additional E code to identify drug
281.3 Other specified megaloblastic anemias, not elsewhere classified
Combined B12 and folate-deficiency anemia
Excludes: refractory megaloblastic anemia (238.7)
281.4 Protein-deficiency anemia
Amino-acid-deficiency anemia
281.8 Anemia associated with other specified nutritional deficiency
Scorbutic anemia
281.9 Unspecified deficiency anemia
Anemia:
dimorphic
macrocytic
megaloblastic NOS
nutritional NOS
simple chronic
282.0 Hereditary spherocytosis
Acholuric (familial) jaundice
Congenital hemolytic anemia (spherocytic)
Congenital spherocytosis
Minkowski-Chauffard syndrome
Spherocytosis (familial)
Excludes: hemolytic anemia of newborn (773.0-773.5)
282.1 Hereditary elliptocytosis
Elliptocytosis (congenital)
Ovalocytosis (congenital) (hereditary)
282.2 Anemias due to disorders of glutathione metabolism
Anemia:
6-phosphogluconic dehydrogenase deficiency
enzyme deficiency, drug-induced
erythrocytic glutathione deficiency
glucose-6-phosphate dehydrogenase [G-6-PD] deficiency
glutathione-reductase deficiency
hemolytic nonspherocytic (hereditary), type I
Disorder of pentose phosphate pathway
Favism
282.3 Other hemolytic anemias due to enzyme deficiency
Anemia:
hemolytic nonspherocytic (hereditary), type II
hexokinase deficiency
pyruvate kinase [PK] deficiency
triosephosphate isomerase deficiency
Excludes: sickle-cell:
disease (282.60-282.69)
trait (282.5)
282.41 Sickle-cell thalassemia without crisis
Sickle-cell thalassemia NOS
Thalassemia Hb-S disease without crisis
282.42 Sickle-cell thalassemia with crisis
Sickle-cell thalassemia with vaso-occlusive pain
Thalassemia Hb-S disease with crisis
Use additional code for type of crisis, such as:
Acute chest syndrome (517.3)
Splenic sequestration (289.52)
Cooley's anemia
Hb-Bart's disease
Hereditary leptocytosis
Mediterranean anemia (with other hemoglobinopathy)
Microdrepanocytosis
Thalassemia (alpha) (beta) (intermedia) (major) (minima) (minor) (mixed) (trait) (with other hemoglobinopathy)
Thalassemia NOS
Hb-AS genotype
Hemoglobin S [Hb-S] trait
Heterozygous:
hemoglobin S
Hb-S
Excludes: that with other hemoglobinopathy (282.60-282.69)
that with thalassemia (282.49)
Sickle-cell anemia
Excludes: sickle-cell thalassemia (282.41-282.42)
sickle-cell trait (282.5)
282.60 Sickle-cell disease, unspecified
Sickle-cell anemia NOS
282.61 Hb-SS disease without crisis
282.62 Hb-SS disease with crisis
Hb-SS disease with vaso-occlusive pain
Sickle-cell crisis NOS
Use additional code for type of crisis, such as:
Acute chest syndrome (517.3)
Splenic sequestration (289.52)
282.63 Sickle-cell/Hb-C disease without crisis
Hb-S/Hb-C disease without crisis
282.64 Sickle-cell/HB-C disease with crisis
Hb-S/Hb-C disease with crisis
Sickle-cell/Hb-C disease with vaso-occlusive pain
Use additional code for types of crisis, such as:
Acute chest syndrome (517.3)
Splenic sequestration (289.52)
282.68 Other sickle-cell disease without crisis
Hb-S/Hb-D disease without crisis
Hb-S/Hb-E disease without crisis
Sickle-cell/Hb-D disease without crisis
Sickle-cell/Hb-E disease without crisis
282.69 Other sickle-cell disease with crisis
Hb-S/Hb-D disease with crisis
Hb-S/Hb-E disease with crisis
Sickle-cell/Hb-D disease with crisis
Sickle-cell/Hb-E disease with crisis
Other sickle-cell disease with vaso-occlusive pain
Use additional code for type of crisis, such as:
Acute chest syndrome (517.3)
Splenic sequestration (289.52)
282.7 Other hemoglobinopathies
Abnormal hemoglobin NOS
Congenital Heinz-body anemia
Disease:
hemoglobin C [Hb-C]
hemoglobin D [Hb-D]
hemoglobin E [Hb-E]
hemoglobin Zurich [Hb-Zurich]
Hemoglobinopathy NOS
Hereditary persistence of fetal hemoglobin [HPFH]
Unstable hemoglobin hemolytic disease
Excludes: familial polycythemia (289.6)
hemoglobin M [Hb-M] disease (289.7)
high-oxygen-affinity hemoglobin (289.0)
282.8 Other specified hereditary hemolytic anemias
Stomatocytosis
282.9 Hereditary hemolytic anemia, unspecified
Hereditary hemolytic anemia NOS
283.0 Autoimmune hemolytic anemias
Autoimmune hemolytic disease (cold type) (warm type)
Chronic cold hemagglutinin disease
Cold agglutinin disease or hemoglobinuria
Hemolytic anemia:
cold type (secondary) (symptomatic)
drug-induced
warm type (secondary) (symptomatic)
Use additional E code to identify cause, if drug-induced
Excludes: Evans' syndrome (287.32)
hemolytic disease of newborn (773.0-773.5)
283.1 Non-autoimmune hemolytic anemias
283.10 Non-autoimmune hemolytic anemia, unspecified
283.11 Hemolytic-uremic syndrome
283.19 Other non-autoimmune hemolytic anemias
Hemolytic anemia:
mechanical
microangiopathic
toxic
Use additional E code to identify cause
283.2 Hemoglobinuria due to hemolysis from external causes
Acute intravascular hemolysis
Hemoglobinuria:
from exertion
march
paroxysmal (cold) (nocturnal)
due to other hemolysis
Marchiafava-Micheli syndrome
Use additional E code to identify cause
283.9 Acquired hemolytic anemia, unspecified
Acquired hemolytic anemia NOS
Chronic idiopathic hemolytic anemia
284.0 Constitutional aplastic anemia
Aplasia, (pure) red cell:
congenital
of infants
primary
Blackfan-Diamond syndrome
Familial hypoplastic anemia
Fanconi's anemia
Pancytopenia with malformations
284.8 Other specified aplastic anemias
Aplastic anemia (due to):
chronic systemic disease
drugs
infection
radiation
toxic (paralytic)
Pancytopenia (acquired)
Red cell aplasia (acquired) (adult) (pure) (with thymoma)
Use additional E code to identify cause
284.9 Aplastic anemia, unspecified
Anemia:
aplastic (idiopathic) NOS
aregenerative
hypoplastic NOS
nonregenerative
Medullary hypoplasia
Excludes: refractory anemia (238.7)
Anemia:
hypochromic with iron loading
sideroachrestic
sideroblastic:
acquired
congenital
hereditary
primary
secondary (drug-induced) (due to disease)
sex-linked hypochromic
vitamin B6-responsive
Pyridoxine-responsive (hypochromic) anemia
Excludes: refractory sideroblastic anemia (238.7)
Use additional E code to identify cause, if drug-induced
285.1 Acute posthemorrhagic anemia
Anemia due to acute blood loss
Excludes: anemia due to chronic blood loss (280.0)
blood loss anemia NOS (280.0)
285.2 Anemia in chronic illness
285.21 Anemia in chronic kidney disease
Anemia in end-stage renal disease
Erythropoietin-resistant anemia (EPO resistant anemia)
285.22 Anemia in neoplastic disease
285.29 Anemia of other chronic illness
Anemia:
dyserythropoietic (congenital)
dyshematopoietic (congenital)
leukoerythroblastic
von Jaksch's
Infantile pseudoleukemia
Anemia:
NOS
essential
normocytic, not due to blood loss
profound
progressive
secondary
Oligocythemia
Excludes: anemia (due to):
blood loss:
acute (285.1)
chronic or unspecified (280.0)
iron deficiency (280.0-280.9)
286.0 Congenital factor VIII disorder
Antihemophilic globulin [AHG] deficiency
Factor VIII (functional) deficiency
Hemophilia:
NOS
A
classical
familial
hereditary
Subhemophilia
Excludes: factor VIII deficiency with vascular defect (286.4)
286.1 Congenital factor IX disorder
Christmas disease
Deficiency:
factor IX (functional)
plasma thromboplastin component [PTC]
Hemophilia B
286.2 Congenital factor XI deficiency
Hemophilia C
Plasma thromboplastin antecedent [PTA] deficiency
Rosenthal's disease
286.3 Congenital deficiency of other clotting factors
Congenital afibrinogenemia
Deficiency:
AC globulin
factor:
I [fibrinogen]
II [prothrombin]
V [labile]
VII [stable]
X [Stuart-Prower]
XII [Hageman]
XIII [fibrin stabilizing]
Laki-Lorand factor
proaccelerin
Disease:
Owren's
Stuart-Prower
Dysfibrinogenemia (congenital)
Dysprothrombinemia (constitutional)
Hypoproconvertinemia
Hypoprothrombinemia (hereditary)
Parahemophilia
286.4 von Willebrand's disease
Angiohemophilia (A) (B)
Constitutional thrombopathy
Factor VIII deficiency with vascular defect
Pseudohemophilia type B
Vascular hemophilia
von Willebrand's (-Jürgens') disease
Excludes: factor VIII deficiency:
NOS (286.0)
with functional defect (286.0)
hereditary capillary fragility (287.8)
286.5 Hemorrhagic disorder due to intrinsic circulating anticoagulants
Antithrombinemia
Antithromboplastinemia
Antithromboplastino-genemia
Hyperheparinemia
Increase in:
anti-VIIIa
anti-IXa
anti-Xa
anti-XIa
antithrombin
Secondary hemophilia
Systemic lupus erythematosus [SLE] inhibitor
Afibrinogenemia, acquired
Consumption coagulopathy
Diffuse or disseminated intravascular coagulation [DIC syndrome]
Fibrinolytic hemorrhage, acquired
Hemorrhagic fibrinogenolysis
Pathologic fibrinolysis
Purpura:
fibrinolytic
fulminans
Excludes: that complicating:
abortion (634-638 with .1, 639.1)
pregnancy or the puerperium (641.3, 666.3)
disseminated intravascular coagulation in newborn (776.2)
286.7 Acquired coagulation factor deficiency
Deficiency of coagulation factor due to:
liver disease
vitamin K deficiency
Hypoprothrombinemia, acquired
Excludes: vitamin K deficiency of newborn (776.0)
Use additional E-code to identify cause, if drug-induced
286.9 Other and unspecified coagulation defects
Defective coagulation NOS
Deficiency, coagulation factor NOS
Delay, coagulation
Disorder:
coagulation
hemostasis
Excludes: abnormal coagulation profile (790.92)
hemorrhagic disease of newborn (776.0)
that complicating:
abortion (634-638 with .1, 639.1)
pregnancy or the puerperium (641.3, 666.3)
Excludes: hemorrhagic thrombocythemia (238.7)
purpura fulminans (286.6)
Peliosis rheumatica
Purpura:
anaphylactoid
autoimmune
Henoch's
nonthrombocytopenic:
hemorrhagic
idiopathic
rheumatica
Schönlein-Henoch
vascular
Vasculitis, allergic
Excludes: hemorrhagic purpura (287.39)
purpura annularis telangiectodes (709.1)
287.1 Qualitative platelet defects
Thrombasthenia (hemorrhagic) (hereditary)
Thrombocytasthenia
Thrombocytopathy (dystrophic)
Thrombopathy (Bernard-Soulier)
Excludes: von Willebrand's disease (286.4)
287.2 Other nonthrombocytopenic purpuras
Purpura:
NOS
senile
simplex
287.3 Primary thrombocytopenia
Excludes: thrombotic thrombocytopenic purpura (446.6)
transient thrombocytopenia of newborn (776.1)
287.30 Primary thrombocytopenia unspecified
Megakaryocytic hypoplasia
287.31 Immune thrombocytopenic purpura
Idiopathic thrombocytopenic purpura
Tidal platelet dysgenesis
287.33 Congenital and hereditary thrombocytopenic purpura
Congenital and hereditary thrombocytopenia
Thrombocytopenia with absent radii (TAR) syndrome
Excludes: Wiskott-Aldrich syndrome (279.12)
287.39 Other primary thrombocytopenia
287.4 Secondary thrombocytopenia
Posttransfusion purpura
Thrombocytopenia (due to):
dilutional
drugs
extracorporeal circulation of blood
massive blood transfusion
platelet alloimmunization
Use additional E code to identify cause
Excludes: transient thrombocytopenia of newborn (776.1)
287.5 Thrombocytopenia, unspecified
287.8 Other specified hemorrhagic conditions
Capillary fragility (hereditary)
Vascular pseudohemophilia
287.9 Unspecified hemorrhagic conditions
Hemorrhagic diathesis (familial)
Excludes: leukemia (204.0-208.9)
Infantile genetic agranulocytosis
Kostmann's syndrome
Neutropenia:
NOS
cyclic
drug-induced
immune
periodic
toxic
Neutropenic splenomegaly
Use additional E code to identify drug or other cause
Excludes: transitory neonatal neutropenia (776.7)
288.1 Functional disorders of polymorphonuclear neutrophils
Chronic (childhood) granulomatous disease
Congenital dysphagocytosis
Job's syndrome
Lipochrome histiocytosis (familial)
Progressive septic granulomatosis
288.2 Genetic anomalies of leukocytes
Anomaly (granulation) (granulocyte) or syndrome:
Alder's (-Reilly)
Chédiak-Steinbrinck (-Higashi)
Jordan's
May-Hegglin
Pelger-Huet
Hereditary:
hypersegmentation
hyposegmentation
leukomelanopathy
Eosinophilia
allergic
hereditary
idiopathic
secondary
Eosinophilic leukocytosis
Excludes: Löffler's syndrome (518.3)
pulmonary eosinophilia (518.3)
288.8 Other specified disease of white blood cells
Leukemoid reaction
lymphocytic
monocytic
myelocytic
Leukocytosis
Lymphocytopenia
Lymphocytosis (symptomatic)
Lymphopenia
Monocytosis (symptomatic)
Plasmacytosis
Excludes: immunity disorders (279.0-279.9)
288.9 Unspecified disease of white blood cells
High-oxygen-affinity hemoglobin
Polycythemia:
acquired
benign
due to:
fall in plasma volume
high altitude
emotional
erythropoietin
hypoxemic
nephrogenous
relative
spurious
stress
Excludes: polycythemia:
neonatal (776.4)
primary (238.4)
vera (238.4)
Chronic:
adenitis any lymph node, except mesenteric
lymphadenitis any lymph node, except mesenteric
Excludes: acute lymphadenitis (683)
mesenteric (289.2)
enlarged glands NOS (785.6)
289.2 Nonspecific mesenteric lymphadenitis
Mesenteric lymphadenitis (acute) (chronic)
289.3 Lymphadenitis, unspecified, except mesenteric
"Big spleen" syndrome
Dyssplenism
Hypersplenia
Excludes: primary splenic neutropenia (288.0)
289.5 Other diseases of spleen
289.50 Disease of spleen, unspecified
289.51 Chronic congestive splenomegaly
Code first sickle-cell disease in crisis (282.42, 282.62, 282.64, 282.69)
Lien migrans
Perisplenitis
Splenic:
abscess
atrophy
cyst
fibrosis
infarction
rupture, nontraumatic
Splenitis
Wandering spleen
Excludes: bilharzial splenic fibrosis (120.0-120.9)
hepatolienal fibrosis (571.5)
splenomegaly NOS (789.2)
Familial:
benign polycythemia
erythrocytosis
Congenital NADH [DPNH]-methemoglobin-reductase deficiency
Hemoglobin M [Hb-M] disease
Methemoglobinemia:
NOS
acquired (with sulfhemoglobinemia)
hereditary
toxic
Stokvis' disease
Sulfhemoglobinemia
Use additional E code to identify cause
289.8 Other specified diseases of blood and blood-forming organs
289.81 Primary hypercoagulable state
Activated protein C resistance
Antithrombin III deficiency
Factor V Leiden mutation
Lupus anticoagulant
Protein C deficiency
Protein S deficiency
Prothrombin gene mutation
289.82 Secondary hypercoagulable state
289.89 Other specified diseases of blood and blood-forming organs
Hypergammaglobulinemia
Myelofibrosis
Pseudocholinesterase deficiency
289.9 Unspecified diseases of blood and blood-forming organs
Blood dyscrasia NOS
Erythroid hyperplasia
5. MENTAL DISORDERS (290-319)
PSYCHOSES (290-299)
Excludes: mental retardation (317-319)
ORGANIC PSYCHOTIC CONDITIONS (290-294)
Includes: psychotic organic brain syndrome
Excludes: nonpsychotic syndromes of organic etiology (310.0-310.9)
psychoses classifiable to 295-298 and without impairment of orientation, comprehension, calculation, learning capacity, and judgement, but associated with physical disease, injury, or condition affecting the brain [e.g., following childbirth] (295.0-298.8)
Code first the associated neurological condition
Excludes: dementia due to alcohol (291.0-291.2)
dementia due to drugs (292.82)
dementia not classified as senile, presenile, or arteriosclerotic (294.10-294.11)
psychoses classifiable to 295-298 occurring in the senium without dementia or delirium (295.0-298.8)
senility with mental changes of nonpsychotic severity (310.1)
transient organic psychotic conditions (293.0-293.9)
290.0 Senile dementia, uncomplicated
Senile dementia:
NOS
simple type
Excludes: mild memory disturbances, not amounting to dementia, associated with senile brain disease (310.1)
senile dementia with:
delirium or confusion (290.3)
delusional [paranoid] features (290.20)
depressive features (290.21)
Brain syndrome with presenile brain disease
Excludes: arteriosclerotic dementia (290.40-290.43)
dementia associated with other cerebral conditions (294.10-294.11)
290.10 Presenile dementia, uncomplicated
Presenile dementia:
NOS
simple type
290.11 Presenile dementia with delirium
Presenile dementia with acute confusional state
290.12 Presenile dementia with delusional features
Presenile dementia, paranoid type
290.13 Presenile dementia with depressive features
Presenile dementia, depressed type
290.2 Senile dementia with delusional or depressive features
Excludes: senile dementia:
NOS (290.0)
with delirium and/or confusion (290.3)
290.20 Senile dementia with delusional features
Senile dementia, paranoid type
Senile psychosis NOS
290.21 Senile dementia with depressive features
290.3 Senile dementia with delirium
Senile dementia with acute confusional state
Excludes: senile:
dementia NOS (290.0)
psychosis NOS (290.20)
Multi-infarct dementia or psychosis
Use additional code to identify cerebral atherosclerosis (437.0)
Excludes: suspected cases with no clear evidence of arteriosclerosis (290.9)
290.40 Vascular dementia, uncomplicated
Arteriosclerotic dementia:
NOS
simple type
290.41 Vascular dementia with delirium
Arteriosclerotic dementia with acute confusional state
290.42 Vascular dementia with delusions
Arteriosclerotic dementia, paranoid type
290.43 Vascular dementia with depressed mood
Arteriosclerotic dementia, depressed type
290.8 Other specified senile psychotic conditions
Presbyophrenic psychosis
290.9 Unspecified senile psychotic condition
Excludes: alcoholism without psychosis (303.0-303.9)
291.0 Alcohol withdrawal delirium
Alcoholic delirium
Delirium tremens
Excludes: alcohol withdrawal (291.81)
291.1 Alcohol-induced persisting amnestic disorder
Alcoholic polyneuritic psychosis
Korsakoff's psychosis, alcoholic
Wernicke-Korsakoff syndrome (alcoholic)
291.2 Alcohol-induced persisting dementia
Alcoholic dementia NOS
Alcoholism associated with dementia NOS
Chronic alcoholic brain syndrome
291.3 Alcohol-induced psychotic disorder with hallucinations
Alcoholic:
hallucinosis (acute)
psychosis with hallucinosis
Excludes: alcohol withdrawal with delirium (291.0)
schizophrenia (295.0-295.9) and paranoid states (297.0-297.9) taking the form of chronic hallucinosis with clear consciousness in an alcoholic
291.4 Idiosyncratic alcohol intoxication
Pathologic:
alcohol intoxication
drunkenness
Excludes: acute alcohol intoxication (305.0)
in alcoholism (303.0)
simple drunkenness (305.0)
291.5 Alcohol-induced psychotic disorder with delusions
Alcoholic:
paranoia
psychosis, paranoid type
Excludes: nonalcoholic paranoid states (297.0-297.9)
schizophrenia, paranoid type (295.3)
291.8 Other specified alcohol-induced mental disorders
Alcohol:
abstinence syndrome or symptoms
withdrawal syndrome or symptoms
Excludes: alcohol withdrawal:
delirium (291.0)
hallucinosis (291.3)
delirium tremens (291.0)
291.82 Alcohol induced sleep disorders
Alcohol induced circadian rhythm sleep disorders
Alcohol induced hypersomnia
Alcohol induced insomnia
Alcohol induced parasomnia
Alcohol-induced anxiety disorder
Alcohol-induced mood disorder
Alcohol-induced sexual dysfunction
291.9 Unspecified alcohol-induced mental disorders
Alcoholic:
mania NOS
psychosis NOS
Alcoholism (chronic) with psychosis
Alcohol-related disorder NOS
Includes: organic brain syndrome associated with consumption of drugs
Use additional code for any associated drug dependence (304.0-304.9)
Use additional E code to identify drug
Drug:
abstinence syndrome or symptoms
withdrawal syndrome or symptoms
292.1 Drug-induced psychotic disorders
292.11 Drug-induced psychotic disorder with delusions
Paranoid state induced by drugs
292.12 Drug-induced psychotic disorder with hallucinations
Hallucinatory state induced by drugs
Excludes: states following LSD or other hallucinogens, lasting only a few days or less ["bad trips"] (305.3)
292.2 Pathological drug intoxication
Drug reaction resulting in brief psychotic states
NOS
idiosyncratic
pathologic
Excludes: expected brief psychotic reactions to hallucinogens ["bad trips"] (305.3)
physiological side-effects of drugs (e.g., dystonias)
292.8 Other specified drug-induced mental disorders
292.82 Drug-induced persisting dementia
292.83 Drug-induced persisting amnestic disorder
292.84 Drug-induced mood disorder
Depressive state induced by drugs
292.85 Drug induced sleep disorders
Drug induced circadian rhythm sleep disorder
Drug induced hypersomnia
Drug induced insomnia
Drug induced parasomnia
Drug-induced anxiety disorder
Drug-induced organic personality syndrome
Drug-induced sexual dysfunction
Drug intoxication
292.9 Unspecified drug-induced mental disorder
Drug-related disorder NOS
Organic psychosis NOS due to or associated with drugs
Includes: transient organic mental disorders not associated with alcohol or drugs
Code first the associated physical or neurological condition
Excludes: confusional state or delirium superimposed on senile dementia (290.3)
dementia due to:
alcohol (291.0-291.9)
arteriosclerosis (290.40-290.43)
drugs (292.82)
senility (290.0)
293.0 Delirium due to conditions classified elsewhere
Acute:
confusional state
infective psychosis
organic reaction
posttraumatic organic psychosis
psycho-organic syndrome
Acute psychosis associated with endocrine, metabolic, or cerebrovascular disorder
Epileptic:
confusional state
twilight state
Subacute:
confusional state
infective psychosis
organic reaction
posttraumatic organic psychosis
psycho-organic syndrome
psychosis associated with endocrine or metabolic disorder
293.8 Other specified transient mental disorders due to conditions classified elsewhere
293.81 Psychotic disorder with delusions in conditions classified elsewhere
Transient organic psychotic condition, paranoid type
293.82 Psychotic disorder with hallucinations in conditions classified elsewhere
Transient organic psychotic condition, hallucinatory type
293.83 Mood disorder in conditions classified elsewhere
Transient organic psychotic condition, depressive type
293.84 Anxiety disorder in conditions classified elsewhere
Catatonic disorder in conditions classified elsewhere
293.9 Unspecified transient mental disorder in conditions classified elsewhere
Organic psychosis:
infective NOS
posttraumatic NOS
transient NOS
Psycho-organic syndrome
Includes: organic psychotic brain syndromes (chronic), not elsewhere classified
294.0 Amnestic disorder in conditions classified elsewhere
Korsakoff's psychosis or syndrome (nonalcoholic)
Code first underlying condition
Excludes: alcoholic:
amnestic syndrome (291.1)
Korsakoff's psychosis (291.1)
294.1 Dementia in conditions classified elsewhere
Dementia of the Alzheimer's type
Code first any underlying physical condition as:
dementia in:
Alzheimer's disease (331.0)
cerebral lipidoses (330.1)
dementia with Lewy bodies (331.82)
dementia with Parkinsonism (331.82)
epilepsy (345.0-345.9)
frontal dementia (331.19)
frontotemporal dementia (331.19)
general paresis [syphilis] (094.1)
hepatolenticular degeneration (275.1)
Huntington's chorea (333.4)
Jakob-Creutzfeldt disease (046.1)
multiple sclerosis (340)
Pick's disease of the brain (331.11)
polyarteritis nodosa (446.0)
syphilis (094.1)
Excludes: dementia:
arteriosclerotic (290.40-290.43)
presenile (290.10-290.13)
senile (290.0)
epileptic psychosis NOS (294.8)
294.10 Dementia in conditions classified elsewhere without behavioral disturbance
Dementia in conditions classified elsewhere NOS
294.11 Dementia in conditions classified elsewhere with behavioral disturbance
Aggressive behavior
Combative behavior
Violent behavior
Wandering off
294.8 Other persistent mental disorders due to conditions classified elsewhere
Amnestic disorder NOS
Dementia NOS
Epileptic psychosis NOS
Mixed paranoid and affective organic psychotic states
Use additional code for associated epilepsy (345.0-345.9)
Excludes: mild memory disturbances, not amounting to dementia (310.1)
294.9 Unspecified persistent mental disorders due to conditions classified elsewhere
Cognitive disorder NOS
Organic psychosis (chronic)
OTHER PSYCHOSES (295-299)
Use additional code to identify any associated physical disease, injury, or condition affecting the brain with psychoses classifiable to 295-298
Includes: schizophrenia of the types described in 295.0-295.9 occurring in children
Excludes: childhood type schizophrenia (299.9)
infantile autism (299.0)
**NOTE** The following fifth-digit subclassification is for use with category 295:
0 unspecified
1 subchronic
2 chronic
3 subchronic with acute exacerbation
4 chronic with acute exacerbation
5 in remission
Schizophrenia simplex
Excludes: latent schizophrenia (295.5)
Hebephrenia
Hebephrenic type schizophrenia
Catatonic (schizophrenia):
agitation
excitation
excited type
stupor
withdrawn type
Schizophrenic:
catalepsy
catatonia
flexibilitas cerea
Paraphrenic schizophrenia
Excludes: involutional paranoid state (297.2)
paranoia (297.1)
paraphrenia (297.2)
295.4 Schizophreniform disorder
Oneirophrenia
Schizophreniform:
attack
psychosis, confusional type
Excludes: acute forms of schizophrenia of:
catatonic type (295.2)
hebephrenic type (295.1)
paranoid type (295.3)
simple type (295.0)
undifferentiated type (295.8)
Latent schizophrenic reaction
Schizophrenia:
borderline
incipient
prepsychotic
prodromal
pseudoneurotic
pseudopsychopathic
Excludes: schizoid personality (301.20-301.22)
Chronic undifferentiated schizophrenia
Restzustand (schizophrenic)
Schizophrenic residual state
295.7 Schizoaffective disorder
Cyclic schizophrenia
Mixed schizophrenic and affective psychosis
Schizo-affective psychosis
Schizophreniform psychosis, affective type
295.8 Other specified types of schizophrenia
Acute (undifferentiated) schizophrenia
Atypical schizophrenia
Cenesthopathic schizophrenia
Excludes: infantile autism (299.0)
295.9 Unspecified schizophrenia
Schizophrenia:
NOS
mixed NOS
undifferentiated NOS
undifferentiated type
Schizophrenic reaction NOS
Schizophreniform psychosis NOS
Includes: episodic affective disorders
Excludes: neurotic depression (300.4)
reactive depressive psychosis (298.0)
reactive excitation (298.1)
**NOTE** The following fifth-digit subclassification is for use with categories 296.0-296.6:
0 unspecified
1 mild
2 moderate
3 severe, without mention of psychotic behavior
4 severe, specified as with psychotic behavior
5 in partial or unspecified remission
6 in full remission
296.0 Bipolar I disorder, single manic episode
Hypomania (mild) NOS single episode or unspecified
Hypomanic psychosis single episode or unspecified
Mania (monopolar) NOS single episode or unspecified
Manic-depressive psychosis or reaction, single episode or unspecified:
hypomanic, single episode or unspecified
manic, single episode or unspecified
Excludes: circular type, if there was a previous attack of depression (296.4)
296.1 Manic disorder, recurrent episode
Any condition classifiable to 296.0, stated to be recurrent
Excludes: circular type, if there was a previous attack of depression (296.4)
296.2 Major depressive disorder, single episode
Depressive psychosis, single episode or unspecified
Endogenous depression, single episode or unspecified
Involutional melancholia, single episode or unspecified
Manic-depressive psychosis or reaction, depressed type, single episode or unspecified
Monopolar depression, single episode or unspecified
Psychotic depression, single episode or unspecified
Excludes: circular type, if previous attack was of manic type (296.5)
depression NOS (311)
reactive depression (neurotic) (300.4)
psychotic (298.0)
296.3 Major depressive disorder, recurrent episode
Any condition classifiable to 296.2, stated to be recurrent
Excludes: circular type, if previous attack was of manic type (296.5)
depression NOS (311)
reactive depression (neurotic) (300.4)
psychotic (298.0)
296.4 Bipolar I disorder, most recent episode (or current) manic
Bipolar disorder, now manic
Manic-depressive psychosis, circular type but currently manic
Excludes: brief compensatory or rebound mood swings (296.99)
296.5 Bipolar I disorder, most recent episode (or current) depressed
Bipolar disorder, now depressed
Manic-depressive psychosis, circular type but currently depressed
Excludes: brief compensatory or rebound mood swings (296.99)
296.6 Bipolar I disorder, most recent episode (or current) mixed
Manic-depressive psychosis, circular type, mixed
296.7 Bipolar I disorder, most recent episode (or current) unspecified
Atypical bipolar affective disorder NOS
Manic-depressive psychosis, circular type, current condition not specified as either manic or depressive
296.8 Other and unspecified bipolar disorders
296.80 Bipolar disorder, unspecified
Bipolar disorder NOS
Manic-depressive:
reaction NOS
syndrome NOS
296.81 Atypical manic disorder
296.82 Atypical depressive disorder
Bipolar II disorder
Manic-depressive psychosis, mixed type
296.9 Other and unspecified episodic mood disorder
Excludes: psychogenic affective psychoses (298.0-298.8)
296.90 Unspecified episodic mood disorder
Affective psychosis NOS
Melancholia NOS
Mood disorder NOS
296.99 Other specified episodic mood disorder
Mood swings:
brief compensatory
rebound
Includes: paranoid disorders
Excludes: acute paranoid reaction (298.3)
alcoholic jealousy or paranoid state (291.5)
paranoid schizophrenia (295.3)
Chronic paranoid psychosis
Sander's disease
Systematized delusions
Excludes: paranoid personality disorder (301.0)
Involutional paranoid state
Late paraphrenia
Paraphrenia (involutional)
297.3 Shared psychotic disorder
Folie à deux
Induced psychosis or paranoid disorder
297.8 Other specified paranoid states
Paranoia querulans
Sensitiver Beziehungswahn
Excludes: acute paranoid reaction or state (298.3)
senile paranoid state (290.20)
297.9 Unspecified paranoid state
Paranoid:
disorder NOS
psychosis NOS
reaction NOS
state NOS
Includes: psychotic conditions due to or provoked by:
emotional stress
environmental factors as major part of etiology
298.0 Depressive type psychosis
Psychogenic depressive psychosis
Psychotic reactive depression
Reactive depressive psychosis
Excludes: manic-depressive psychosis, depressed type (296.2-296.3)
neurotic depression (300.4)
reactive depression NOS (300.4)
298.1 Excitative type psychosis
Acute hysterical psychosis
Psychogenic excitation
Reactive excitation
Excludes: manic-depressive psychosis, manic type (296.0-296.1)
Psychogenic confusion
Psychogenic twilight state
Excludes: acute confusional state (293.0)
Acute psychogenic paranoid psychosis
Bouffée délirante
Excludes: paranoid states (297.0-297.9)
298.4 Psychogenic paranoid psychosis
Protracted reactive paranoid psychosis
298.8 Other and unspecified reactive psychosis
Brief psychotic disorder
Brief reactive psychosis NOS
Hysterical psychosis
Psychogenic psychosis NOS
Psychogenic stupor
Excludes: acute hysterical psychosis (298.1)
Atypical psychosis
Psychosis NOS
Psychotic disorder NOS
Excludes: adult type psychoses occurring in childhood, as:
affective disorders (296.0-296.9)
manic-depressive disorders (296.0-296.9)
schizophrenia (295.0-295.9)
**NOTE** The following fifth-digit subclassification is for use with category 299:
0 current or active state
1 residual state
Childhood autism
Infantile psychosis
Kanner's syndrome
Excludes: disintegrative psychosis (299.1)
Heller's syndrome (299.1)
schizophrenic syndrome of childhood (299.9)
299.1 Childhood disintegrative disorder
Heller's syndrome
Use additional code to identify any associated neurological disorder
Excludes: infantile autism (299.0)
schizophrenic syndrome of childhood (299.9)
299.8 Other specified pervasive developmental disorders
Asperger's disorder
Atypical childhood psychosis
Borderline psychosis of childhood
Excludes: simple stereotypes without psychotic disturbance (307.3)
299.9 Unspecified pervasive developmental disorder
Child psychosis NOS
Pervasive developmental disorder NOS
Schizophrenia, childhood type NOS
Schizophrenic syndrome of childhood NOS
Excludes: schizophrenia of adult type occurring in childhood (295.0-295.9)
NEUROTIC DISORDERS, PERSONALITY DISORDERS, AND OTHER NONPSYCHOTIC MENTAL DISORDERS (300-316)
Excludes: anxiety in:
acute stress reaction (308.0)
transient adjustment reaction (309.24)
neurasthenia (300.5)
psychophysiological disorders (306.0-306.9)
separation anxiety (309.21)
300.00 Anxiety state, unspecified
Anxiety:
neurosis
reaction
state (neurotic)
Atypical anxiety disorder
300.01 Panic disorder without agoraphobia
Panic:
attack
state
Excludes: panic disorder with agoraphobia (300.21)
300.02 Generalized anxiety disorder
300.1 Dissociative, conversion and factitious disorders
Excludes: adjustment reaction (309.0-309.9)
anorexia nervosa (307.1)
gross stress reaction (308.0-308.9)
hysterical personality (301.50-301.59)
psychophysiologic disorders (306.0-306.9)
Astasia-abasia, hysterical
Conversion hysteria or reaction
Hysterical:
blindness
deafness
paralysis
Hysterical amnesia
Hysterical fugue
300.14 Dissociative identity disorder
300.15 Dissociative disorder or reaction, unspecified
300.16 Factitious disorder with predominantly psychological signs and symptoms
Compensation neurosis
Ganser's syndrome, hysterical
300.19 Other and unspecified factitious illness
Factitious disorder (with combined psychological and physical signs and symptoms) (with predominantly physical signs and symptoms) NOS
Excludes: multiple operations or hospital addiction syndrome (301.51)
Excludes: anxiety state not associated with a specific situation or object (300.00-300.09)
obsessional phobias (300.3)
Anxiety-hysteria NOS
Phobia NOS
300.21 Agoraphobia with panic disorder
Fear of:
open spaces with panic attacks
streets with panic attacks
travel with panic attacks
Panic disorder with agoraphobia
Excludes: agoraphobia without panic disorder (300.22)
panic disorder without agoraphobia (300.01)
300.22 Agoraphobia without mention of panic attacks
Any condition classifiable to 300.21 without mention of panic attacks
Fear of:
eating in public
public speaking
washing in public
300.29 Other isolated or specific phobias
Acrophobia
Animal phobias
Claustrophobia
Fear of crowds
300.3 Obsessive-compulsive disorders
Anancastic neurosis
Compulsive neurosis
Obsessional phobia [any]
Excludes: obsessive-compulsive symptoms occurring in:
endogenous depression (296.2-296.3)
organic states (e.g., encephalitis) schizophrenia (295.0-295.9)
Anxiety depression
Depression with anxiety
Depressive reaction
Neurotic depressive state
Reactive depression
Excludes: adjustment reaction with depressive symptoms (309.0-309.1)
depression NOS (311)
manic-depressive psychosis, depressed type (296.2-296.3)
reactive depressive psychosis (298.0)
Fatigue neurosis
Nervous debility
Psychogenic:
asthenia
general fatigue
Use additional code to identify any associated physical disorder
Excludes: anxiety state (300.00-300.09)
neurotic depression (300.4)
psychophysiological disorders (306.0-306.9)
specific nonpsychotic mental disorders following organic brain damage (310.0-310.9)
300.6 Depersonalization disorder
Derealization (neurotic)
Neurotic state with depersonalization episode
Excludes: depersonalization associated with:
anxiety (300.00-300.09)
depression (300.4)
manic-depressive disorder or psychosis (296.0-296.9)
schizophrenia (295.0-295.9)
Body dysmorphic disorder
Excludes: hypochondriasis in:
hysteria (300.10-300.19)
manic-depressive psychosis, depressed type (296.2-296.3)
neurasthenia (300.5)
obsessional disorder (300.3)
schizophrenia (295.0-295.9)
Briquet's disorder
Severe somatoform disorder
300.82 Undifferentiated somatoform disorder
Atypical somatoform disorder
Somatoform disorder NOS
300.89 Other somatoform disorders
Occupational neurosis, including writers' cramp
Psychasthenia
Psychasthenic neurosis
300.9 Unspecified nonpsychotic mental disorder
Psychoneurosis NOS
Includes: character neurosis
Use additional code to identify any associated neurosis or psychosis, or physical condition
Excludes: nonpsychotic personality disorder associated with organic brain syndromes (310.0-310.9)
301.0 Paranoid personality disorder
Fanatic personality
Paranoid personality (disorder)
Paranoid traits
Excludes: acute paranoid reaction (298.3)
alcoholic paranoia (291.5)
paranoid schizophrenia (295.3)
paranoid states (297.0-297.9)
301.1 Affective personality disorder
Excludes: affective psychotic disorders (296.0-296.9)
neurasthenia (300.5)
neurotic depression (300.4)
301.10 Affective personality disorder, unspecified
301.11 Chronic hypomanic personality disorder
Chronic hypomanic disorder
Hypomanic personality
301.12 Chronic depressive personality disorder
Chronic depressive disorder
Depressive character or personality
Cycloid personality
Cyclothymia
Cyclothymic personality
301.2 Schizoid personality disorder
Excludes: schizophrenia (295.0-295.9)
301.20 Schizoid personality disorder, unspecified
301.21 Introverted personality
301.22 Schizotypal personality disorder
301.3 Explosive personality disorder
Aggressive:
personality
reaction
Aggressiveness
Emotional instability (excessive)
Pathological emotionality
Quarrelsomeness
Excludes: dyssocial personality (301.7)
hysterical neurosis (300.10-300.19)
301.4 Obsessive-compulsive personality disorder
Anancastic personality
Obsessional personality
Excludes: obsessive-compulsive disorder (300.3)
phobic state (300.20-300.29)
301.5 Histrionic personality disorder
Excludes: hysterical neurosis (300.10-300.19)
301.50 Histrionic personality disorder, unspecified
Hysterical personality NOS
301.51 Chronic factitious illness with physical symptoms
Hospital addiction syndrome
Multiple operations syndrome
Munchausen syndrome
301.59 Other histrionic personality disorder
Personality:
emotionally unstable
labile
psychoinfantile
301.6 Dependent personality disorder
Asthenic personality
Inadequate personality
Passive personality
Excludes: neurasthenia (300.5)
passive-aggressive personality (301.84)
301.7 Antisocial personality disorder
Amoral personality
Asocial personality
Dyssocial personality
Personality disorder with predominantly sociopathic or asocial manifestation
Excludes: disturbance of conduct without specifiable personality disorder (312.0-312.9)
explosive personality (301.3)
301.8 Other personality disorders
301.81 Narcissistic personality disorder
301.82 Avoidant personality disorder
301.83 Borderline personality disorder
301.84 Passive-aggressive personality
Personality:
eccentric
"haltlose" type
immature
masochistic
psychoneurotic
Excludes: psychoinfantile personality (301.59)
301.9 Unspecified personality disorder
Pathological personality NOS
Personality disorder NOS
Psychopathic:
constitutional state
personality (disorder)
Excludes: sexual disorder manifest in:
organic brain syndrome (290.0-294.9, 310.0-310.9)
psychosis (295.0-298.9)
302.0 Ego-dystonic sexual orientation
Ego-dystonic lesbianism
Sexual orientation conflict disorder
Excludes: homosexual pedophilia (302.2)
Bestiality
Excludes: trans-sexualism (302.5)
Excludes: transvestism (302.3)
302.50 With unspecified sexual history
302.52 With homosexual history
302.53 With heterosexual history
302.6 Gender identity disorder in children
Feminism in boys
Gender identity disorder NOS
Excludes: gender identity disorder in adult (302.85)
trans-sexualism (302.50-302.53)
transvestism (302.3)
302.7 Psychosexual dysfunction
Excludes: decreased sexual desire NOS (799.81)
impotence of organic origin (607.84)
normal transient symptoms from ruptured hymen
transient or occasional failures of erection due to fatigue, anxiety, alcohol, or drugs
302.70 Psychosexual dysfunction, unspecified
Sexual dysfunction NOS
302.71 Hypoactive sexual desire disorder
Excludes: decreased sexual desire NOS (799.81)
302.72 With inhibited sexual excitement
Female sexual arousal disorder
Frigidity
Impotence
Male erectile disorder
302.73 Female orgasmic disorder
302.76 Dyspareunia, psychogenic
302.79 With other specified psychosexual dysfunctions
Sexual aversion disorder
302.8 Other specified psychosexual disorders
302.85 Gender identity disorder in adolescents or adults
Excludes: gender identity disorder NOS (302.6)
gender identity disorder in children (302.6)
Frotteurism
Nymphomania
Satyriasis
302.9 Unspecified psychosexual disorder
Paraphilia NOS
Pathologic sexuality NOS
Sexual deviation NOS
Sexual disorder NOS
Use additional code to identify any associated condition, as:
alcoholic psychoses (291.0-291.9)
drug dependence (304.0-304.9)
physical complications of alcohol, such as:
cerebral degeneration (331.7)
cirrhosis of liver (571.2)
epilepsy (345.0-345.9)
gastritis (535.3)
hepatitis (571.1)
liver damage NOS (571.3)
Excludes: drunkenness NOS (305.0)
**NOTE** The following fifth-digit subclassification is for use with category 303:
0 unspecified
1 continuous
2 episodic
3 in remission
303.0 Acute alcoholic intoxication
Acute drunkenness in alcoholism
303.9 Other and unspecified alcohol dependence
Chronic alcoholism
Dipsomania
Excludes: nondependent abuse of drugs (305.1-305.9)
**NOTE** The following fifth-digit subclassification is for use with category 304:
0 unspecified
1 continuous
2 episodic
3 in remission
Heroin
Meperidine
Methadone
Morphine
Opium
Opium alkaloids and their derivatives
Synthetics with morphine-like effects
304.1 Sedative, hypnotic or anxiolytic dependence
Barbiturates
Nonbarbiturate sedatives and tranquilizers with a similar effect:
chlordiazepoxide
diazepam
glutethimide
meprobamate
methaqualone
Coca leaves and derivatives
Hashish
Hemp
Marihuana
304.4 Amphetamine and other psychostimulant dependence
Methylphenidate
Phenmetrazine
Dimethyltryptamine [DMT]
Lysergic acid diethylamide [LSD] and derivatives
Mescaline
Psilocybin
304.6 Other specified drug dependence
Absinthe addiction
Glue sniffing
Inhalant dependence
Phencyclidine dependence
Excludes: tobacco dependence (305.1)
304.7 Combinations of opioid type drug with any other
304.8 Combinations of drug dependence excluding opioid type drug
304.9 Unspecified drug dependence
Drug addiction NOS
Drug dependence NOS
Note: Includes cases where a person, for whom no other diagnosis is possible, has come under medical care because of the maladaptive effect of a drug on which he is not dependent and that he has taken on his own initiative to the detriment of his health or social functioning.
Excludes: alcohol dependence syndrome (303.0-303.9)
drug dependence (304.0-304.9)
drug withdrawal syndrome (292.0)
poisoning by drugs or medicinal substances (960.0-979.9)
**NOTE** The following fifth-digit subclassification is for use with codes 305.0, 305.2-305.9
0 unspecified
1 continuous
2 episodic
3 in remission
Drunkenness NOS
Excessive drinking of alcohol NOS
"Hangover" (alcohol)
Inebriety NOS
Excludes: acute alcohol intoxication in alcoholism (303.0)
alcoholic psychoses (291.0-291.9)
Tobacco dependence
Excludes: history of tobacco use (V15.82)
Acute intoxication from hallucinogens ["bad trips"]
LSD reaction
305.4 Sedative, hypnotic or anxiolytic abuse
305.7 Amphetamine or related acting sympathomimetic abuse
305.8 Antidepressant type abuse
305.9 Other, mixed, or unspecified drug abuse
Caffeine intoxication
Inhalant abuse
"Laxative habit"
Misuse of drugs NOS
Nonprescribed use of drugs or patent medicinals
Phencyclidine abuse
Includes: psychogenic:
physical symptoms not involving tissue damage
physiological manifestations not involving tissue damage
Excludes: hysteria (300.11-300.19)
physical symptoms secondary to a psychiatric disorder classified elsewhere
psychic factors associated with physical conditions involving tissue damage classified elsewhere (316)
specific nonpsychotic mental disorders following organic brain damage (310.0-310.9)
Psychogenic paralysis
Psychogenic torticollis
Excludes: Gilles de la Tourette's syndrome (307.23)
paralysis as hysterical or conversion reaction (300.11)
tics (307.20-307.22)
Psychogenic:
air hunger
cough
hiccough
hyperventilation
yawning
Excludes: psychogenic asthma (316 and 493.9)
Cardiac neurosis
Cardiovascular neurosis
Neurocirculatory asthenia
Psychogenic cardiovascular disorder
Excludes: psychogenic paroxysmal tachycardia (316 and 427.2)
Psychogenic pruritus
Excludes: psychogenic:
alopecia (316 and 704.00)
dermatitis (316 and 692.9)
eczema (316 and 691.8 or 692.9)
urticaria (316 and 708.0-708.9)
Aerophagy
Cyclical vomiting, psychogenic
Diarrhea, psychogenic
Nervous gastritis
Psychogenic dyspepsia
Excludes: cyclical vomiting NOS (536.2)
globus hystericus (300.11)
mucous colitis (316 and 564.9)
psychogenic:
cardiospasm (316 and 530.0)
duodenal ulcer (316 and 532.0-532.9)
gastric ulcer (316 and 531.0-531.9)
peptic ulcer NOS (316 and 533.0-533.9)
vomiting NOS (307.54)
Excludes: enuresis, psychogenic (307.6)
frigidity (302.72)
impotence (302.72)
psychogenic dyspareunia (302.76)
306.50 Psychogenic genitourinary malfunction, unspecified
Functional vaginismus
306.52 Psychogenic dysmenorrhea
Excludes: hysterical blindness or deafness (300.11)
psychophysical visual disturbances (368.16)
306.8 Other specified psychophysiological malfunction
Bruxism
Teeth grinding
306.9 Unspecified psychophysiological malfunction
Psychophysiologic disorder NOS
Psychosomatic disorder NOS
Note: This category is intended for use if the psychopathology is manifested by a single specific symptom or group of symptoms which is not part of an organic illness or other mental disorder classifiable elsewhere.
Excludes: those due to mental disorders classified elsewhere
those of organic origin
Excludes: dysphasia (784.5)
lisping or lalling (307.9)
retarded development of speech (315.31-315.39)
Excludes: eating disturbance NOS (307.50)
feeding problem (783.3)
of nonorganic origin (307.59)
loss of appetite (783.0)
of nonorganic origin (307.59)
Excludes: nail-biting or thumb-sucking (307.9)
stereotypes occurring in isolation (307.3)
tics of organic origin (333.3)
307.20 Tic disorder, unspecified
Tic disorder NOS
307.22 Chronic motor or vocal tic disorder
Motor-verbal tic disorder
307.3 Stereotypic movement disorder
Body-rocking
Head banging
Spasmus nutans
Stereotypes NOS
Excludes: tics (307.20-307.23)
of organic origin (333.3)
307.4 Specific disorders of sleep of nonorganic origin
Excludes: narcolepsy (347.00-347.11)
organic hypersomnia (327.10-327.19)
organic insomnia (327.00-327.09)
those of unspecified cause (780.50-780.59)
307.40 Nonorganic sleep disorder, unspecified
307.41 Transient disorder of initiating or maintaining sleep
Adjustment insomnia
Hyposomnia associated with acute or intermittent emotional reactions or conflicts
Insomnia associated with acute or intermittent emotional reactions or conflicts
Sleeplessness associated with acute or intermittent emotional reactions or conflicts
307.42 Persistent disorder of initiating or maintaining sleep
Hyposomnia, insomnia, or sleeplessness associated with:
anxiety
conditioned arousal
depression (major) (minor)
psychosis
Idiopathic insomnia
Paradoxical insomnia
Primary insomnia
Psychophysiological insomnia
307.43 Transient disorder of initiating or maintaining wakefulness
Hypersomnia associated with acute or intermittent emotional reactions or conflicts
307.44 Persistent disorder of initiating or maintaining wakefulness
Hypersomnia associated with depression (major) (minor)
Insufficient sleep syndrome
Primary hypersomnia
Excludes: sleep deprivation (V69.4)
307.45 Circadian rhythm sleep disorder of nonorganic origin
Night terror disorder
Night terrors
Sleep terror disorder
Sleepwalking
Somnambulism
307.47 Other dysfunctions of sleep stages or arousal from sleep
Nightmare disorder
Nightmares:
NOS
REM-sleep type
Sleep drunkenness
307.48 Repetitive intrusions of sleep
Repetitive intrusion of sleep with:
atypical polysomnographic features
environmental disturbances
repeated REM-sleep interruptions
"Short-sleeper"
Subjective insomnia complaint
307.5 Other and unspecified disorders of eating
Excludes: anorexia:
nervosa (307.1)
of unspecified cause (783.0)
overeating, of unspecified cause (783.6)
vomiting:
NOS (787.0)
cyclical (536.2)
psychogenic (306.4)
307.50 Eating disorder, unspecified
Eating disorder NOS
Overeating of nonorganic origin
Perverted appetite of nonorganic origin
Regurgitation, of nonorganic origin, of food with reswallowing
Excludes: obsessional rumination (300.3)
Feeding disorder of infancy or early childhood of nonorganic origin
Infantile feeding disturbances of nonorganic origin
Loss of appetite of nonorganic origin
Enuresis (primary) (secondary) of nonorganic origin
Excludes: enuresis of unspecified cause (788.3)
Encopresis (continuous) (discontinuous) of nonorganic origin
Excludes: encopresis of unspecified cause (787.6)
307.8 Pain disorders related to psychological factors
307.80 Psychogenic pain, site unspecified
Excludes: headache:
NOS (784.0)
migraine (346.0-346.9)
Code first to site of pain
Excludes: pain disorder exclusively attributed to psychological factors (307.80)
psychogenic pain (307.80)
307.9 Other and unspecified special symptoms or syndromes, not elsewhere classified
Communication disorder NOS
Hair plucking
Lalling
Lisping
Masturbation
Nail-biting
Thumb-sucking
Includes: catastrophic stress
combat fatigue
gross stress reaction (acute)
transient disorders in response to exceptional physical or mental stress which usually subside within hours or days
Excludes: adjustment reaction or disorder (309.0-309.9)
chronic stress reaction (309.1-309.9)
308.0 Predominant disturbance of emotions
Anxiety as acute reaction to exceptional [gross] stress
Emotional crisis as acute reaction to exceptional [gross] stress
Panic state as acute reaction to exceptional [gross] stress
308.1 Predominant disturbance of consciousness
Fugues as acute reaction to exceptional [gross] stress
308.2 Predominant psychomotor disturbance
Agitation states as acute reaction to exceptional [gross] stress
Stupor as acute reaction to exceptional [gross] stress
308.3 Other acute reactions to stress
Acute situational disturbance
Acute stress disorder
Excludes: prolonged posttraumatic emotional disturbance (309.81)
308.4 Mixed disorders as reaction to stress
308.9 Unspecified acute reaction to stress
Includes: adjustment disorders
reaction (adjustment) to chronic stress
Excludes: acute reaction to major stress (308.0-308.9)
neurotic disorders (300.0-300.9)
309.0 Adjustment disorder with depressed mood
Grief reaction
Excludes: affective psychoses (296.0-296.9)
neurotic depression (300.4)
prolonged depressive reaction (309.1)
psychogenic depressive psychosis (298.0)
309.1 Prolonged depressive reaction
Excludes: affective psychoses (296.0-296.9)
brief depressive reaction (309.0)
neurotic depression (300.4)
psychogenic depressive psychosis (298.0)
309.2 With predominant disturbance of other emotions
309.21 Separation anxiety disorder
309.22 Emancipation disorder of adolescence and early adult life
309.23 Specific academic or work inhibition
309.24 Adjustment disorder with anxiety
309.28 Adjustment disorder with mixed anxiety and depressed mood
Adjustment reaction with anxiety and depression
Culture shock
309.3 Adjustment disorder with disturbance of conduct
Conduct disturbance as adjustment reaction
Destructiveness as adjustment reaction
Excludes: destructiveness in child (312.9)
disturbance of conduct NOS (312.9)
dyssocial behavior without manifest psychiatric disorder (V71.01-V71.02)
personality disorder with predominantly sociopathic or asocial manifestations (301.7)
309.4 Adjustment disorder with mixed disturbance of emotions and conduct
309.8 Other specified adjustment reactions
309.81 Posttraumatic stress disorder
Chronic posttraumatic stress disorder
Concentration camp syndrome
Posttraumatic stress disorder NOS
Excludes: acute stress disorder (308.3)
posttraumatic brain syndrome:
nonpsychotic (310.2)
psychotic (293.0-293.9)
309.82 Adjustment reaction with physical symptoms
309.83 Adjustment reaction with withdrawal
Elective mutism as adjustment reaction
Hospitalism (in children) NOS
309.9 Unspecified adjustment reaction
Adaptation reaction NOS
Adjustment reaction NOS
Excludes: neuroses, personality disorders, or other
nonpsychotic conditions occurring in a form similar to that seen with
functional disorders but in association with a physical condition (300.0-300.9,
301.0-301.9)
Lobotomy syndrome
Postleucotomy syndrome [state]
Excludes: postcontusion syndrome (310.2)
310.1 Personality change due to conditions classified elsewhere
Cognitive or personality change of other type, of nonpsychotic severity
Organic psychosyndrome of nonpsychotic severity
Presbyophrenia NOS
Senility with mental changes of nonpsychotic severity
Excludes: memory loss of unknown cause (780.93)
Postcontusion syndrome or encephalopathy
Posttraumatic brain syndrome, nonpsychotic
Status postcommotio cerebri
Excludes: any organic psychotic conditions following head injury (293.0-294.0)
frontal lobe syndrome (310.0)
postencephalitic syndrome (310.8)
310.8 Other specified nonpsychotic mental disorders following organic brain damage
Mild memory disturbance
Postencephalitic syndrome
Other focal (partial) organic psychosyndromes
310.9 Unspecified nonpsychotic mental disorder following organic brain damage
Depressive disorder NOS
Depressive state NOS
Depression NOS
Excludes: acute reaction to major stress with depressive symptoms (308.0)
affective personality disorder (301.10-301.13)
affective psychoses (296.0-296.9)
brief depressive reaction (309.0)
depressive states associated with stressful events (309.0-309.1)
disturbance of emotions specific to childhood and adolescence, with misery and unhappiness (313.1)
mixed adjustment reaction with depressive symptoms (309.4)
neurotic depression (300.4)
prolonged depressive adjustment reaction (309.1)
psychogenic depressive psychosis (298.0)
Excludes: adjustment reaction with disturbance of conduct (309.3)
drug dependence (304.0-304.9)
dyssocial behavior without manifest psychiatric disorder (V71.01-V71.02)
personality disorder with predominantly sociopathic or asocial manifestations (301.7)
sexual deviations (302.0-302.9)
**NOTE** The following fifth-digit subclassification is for use with categories 312.0-312.2:
0 unspecified
1 mild
2 moderate
3 severe
312.0 Undersocialized conduct disorder, aggressive type
Aggressive outburst
Anger reaction
Unsocialized aggressive disorder
312.1 Undersocialized conduct disorder, unaggressive type
Childhood truancy, unsocialized
Solitary stealing
Tantrums
312.2 Socialized conduct disorder
Childhood truancy, socialized
Group delinquency
Excludes: gang activity without manifest psychiatric disorder (V71.01)
312.3 Disorders of impulse control, not elsewhere classified
312.30 Impulse control disorder, unspecified
312.34 Intermittent explosive disorder
312.35 Isolated explosive disorder
Trichotillomania
312.4 Mixed disturbance of conduct and emotions
Neurotic delinquency
Excludes: compulsive conduct disorder (312.3)
312.8 Other specified disturbances of conduct, not elsewhere classified
312.81 Conduct disorder, childhood onset type
312.82 Conduct disorder, adolescent onset type
Conduct disorder of unspecified onset
312.9 Unspecified disturbance of conduct
Delinquency (juvenile)
Disruptive behavior disorder NOS
Excludes: adjustment reaction (309.0-309.9)
emotional disorder of neurotic type (300.0-300.9)
masturbation, nail-biting, thumb-sucking, and other isolated symptoms (307.0-307.9)
Anxiety and fearfulness of childhood and adolescence
Overanxious disorder of childhood and adolescence
Excludes: abnormal separation anxiety (309.21)
anxiety states (300.00-300.09)
hospitalism in children (309.83)
phobic state (300.20-300.29)
313.1 Misery and unhappiness disorder
Excludes: depressive neurosis (300.4)
313.2 Sensitivity, shyness, and social withdrawal disorder
Excludes: infantile autism (299.0)
schizoid personality (301.20-301.22)
schizophrenia (295.0-295.9)
313.21 Shyness disorder of childhood
Sensitivity reaction of childhood or adolescence
313.22 Introverted disorder of childhood
Social withdrawal of childhood or adolescence
Withdrawal reaction of childhood or adolescence
Excludes: elective mutism as adjustment reaction (309.83)
Sibling jealousy
Excludes: relationship problems associated with aggression, destruction, or other forms of conduct disturbance (312.0-312.9)
313.8 Other or mixed emotional disturbances of childhood or adolescence
313.81 Oppositional defiant disorder
Identity problem
313.83 Academic underachievement disorder
Reactive attachment disorder of infancy or early childhood
313.9 Unspecified emotional disturbance of childhood or adolescence
Mental disorder of infancy, childhood or adolescence NOS
Excludes: hyperkinesis as symptom of underlying disordercode the underlying disorder
314.0 Attention deficit disorder
Adult
Child
314.00 Without mention of hyperactivity
Predominantly inattentive type
Combined type
Overactivity NOS
Predominantly hyperactive/impulsive type
Simple disturbance of attention with overactivity
314.1 Hyperkinesis with developmental delay
Developmental disorder of hyperkinesis
Use additional code to identify any associated neurological disorder
314.2 Hyperkinetic conduct disorder
Hyperkinetic conduct disorder without developmental delay
Excludes: hyperkinesis with significant delays in specific skills (314.1)
314.8 Other specified manifestations of hyperkinetic syndrome
314.9 Unspecified hyperkinetic syndrome
Hyperkinetic reaction of childhood or adolescence NOS
Hyperkinetic syndrome NOS
Excludes: that due to a neurological disorder (320.0-389.9)
315.0 Specific reading disorder
315.00 Reading disorder, unspecified
Specific spelling difficulty
Dyscalculia
315.2 Other specific learning difficulties
Disorder of written expression
Excludes: specific arithmetical disorder (315.1)
specific reading disorder (315.00-315.09)
315.3 Developmental speech or language disorder
315.31 Expressive language disorder
Developmental aphasia
Word deafness
Excludes: acquired aphasia (784.3)
elective mutism (309.83, 313.0, 313.23)
315.32 Mixed receptive-expressive language disorder
Developmental articulation disorder
Dyslalia
Phonological disorder
Excludes: lisping and lalling (307.9)
stammering and stuttering (307.0)
315.4 Developmental coordination disorder
Clumsiness syndrome
Dyspraxia syndrome
Specific motor development disorder
315.5 Mixed development disorder
315.8 Other specified delays in development
315.9 Unspecified delay in development
Developmental disorder NOS
Learning disorder NOS
Psychologic factors in physical conditions classified elsewhere
Use additional code to identify the associated physical condition, as:
psychogenic:
asthma (493.9)
dermatitis (692.9)
duodenal ulcer (532.0-532.9)
eczema (691.8, 692.9)
gastric ulcer (531.0-531.9)
mucous colitis (564.9)
paroxysmal tachycardia (427.2)
ulcerative colitis (556)